{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,6]],"date-time":"2026-05-06T05:03:50Z","timestamp":1778043830267,"version":"3.51.4"},"reference-count":24,"publisher":"MDPI AG","issue":"24","license":[{"start":{"date-parts":[[2024,12,16]],"date-time":"2024-12-16T00:00:00Z","timestamp":1734307200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JCM"],"abstract":"<jats:p>Objectives: Congenital hearing loss is a significant health concern, with diverse etiologies encompassing cochlear and cochleovestibular pathologies. Preoperative radiological evaluation in cochlear implant candidates is pivotal for treatment planning. We aim to elucidate the spectrum of radiological findings in patients with congenital hearing loss undergoing cochlear implant assessment. Methods: An analysis included 389 sensorineural hearing loss (SNHL) patients who underwent cochlear implantation at a tertiary university hospital, of which 177 were congenital SNHL. Computed tomography (CT) and magnetic resonance imaging (MRI) data were meticulously assessed for diverse congenital pathologies, focusing on congenital malformations. Results: In the congenital SNHL group, comprising 177 patients (80 females and 97 males), congenital cochleovestibular malformations were evident in 56 ears of 29 cases. Different congenital cochleovestibular malformations, ranging from labyrinthine aplasia to isolated large vestibular aqueducts, were detected. Among the various anomalies, incomplete partitions and cochlear hypoplasia emerged as more frequent patterns. Conclusions: This study offers a comprehensive radiological analysis of congenital SNHL patients undergoing cochlear implantation, revealing a spectrum of anomalies. It demonstrates the diverse nature of anomalies affecting the external auditory canal, middle ear structures, and cochleovestibular system. These insights provide a deeper understanding of congenital SNHL and contribute to developing informed treatment strategies.<\/jats:p>","DOI":"10.3390\/jcm13247664","type":"journal-article","created":{"date-parts":[[2024,12,17]],"date-time":"2024-12-17T03:46:02Z","timestamp":1734407162000},"page":"7664","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Radiological Perspectives in Congenital Sensorineural Hearing Loss: Insights from Cochlear Implant Candidates"],"prefix":"10.3390","volume":"13","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-8443-0838","authenticated-orcid":false,"given":"Sabri","family":"\u015eirolu","sequence":"first","affiliation":[{"name":"Sisli Hamidiye Etfal Training and Research Hospital, Radiology Clinic, University of Health Sciences, 34418 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7688-367X","authenticated-orcid":false,"given":"Rauf","family":"Hamid","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4288-7861","authenticated-orcid":false,"given":"Seyfullah Halit","family":"Karag\u00f6z","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7766-5866","authenticated-orcid":false,"given":"Osman Aykan","family":"Karg\u0131n","sequence":"additional","affiliation":[{"name":"Istanbul Physical Therapy and Rehabilitation Training and Research Hospital, Radiology Clinic, University of Health Sciences, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3236-6659","authenticated-orcid":false,"given":"Vefa","family":"Salt","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3876-7285","authenticated-orcid":false,"given":"Sevda","family":"Yener","sequence":"additional","affiliation":[{"name":"Department of Radiation Oncology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6747-7212","authenticated-orcid":false,"given":"Halide \u00c7etin","family":"Kara","sequence":"additional","affiliation":[{"name":"Department of Otorhinolaryngology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emine Deniz","family":"G\u00f6zen","sequence":"additional","affiliation":[{"name":"Department of Otorhinolaryngology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Serdar","family":"Arslan","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bora","family":"Korkmazer","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Onur","family":"Tutar","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Osman","family":"K\u0131z\u0131lk\u0131l\u0131\u00e7","sequence":"additional","affiliation":[{"name":"Department of Radiology, Cerrahpa\u015fa Medical Faculty, \u0130stanbul University-Cerrahpa\u015fa, 34147 Istanbul, T\u00fcrkiye"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2024,12,16]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"884","DOI":"10.1002\/ohn.326","article-title":"Prevalence of Subclinical Hearing Loss in the United States","volume":"169","author":"Dragon","year":"2023","journal-title":"Otolaryngol. 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