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Abbreviations: AIP\u2014Autoimmune pancreatitis; AIP-1\u2014Type 1 autoimmune pancreatitis, also known as lymphoplasmacytic sclerosing pancreatitis (LPSP); AIP-2\u2014Type 2 autoimmune pancreatitis, also referred to as idiopathic duct-centric pancreatitis (IDCP); AIP-3\u2014Type 3 autoimmune pancreatitis, also known as immune checkpoint inhibitor (ICI)-induced autoimmune pancreatitis; IgG4-RD\u2014Immunoglobulin G4-related disease.<\/jats:p>","DOI":"10.3390\/jcm14093076","type":"journal-article","created":{"date-parts":[[2025,4,29]],"date-time":"2025-04-29T09:00:39Z","timestamp":1745917239000},"page":"3076","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":19,"title":["Autoimmune Pancreatitis: A Review"],"prefix":"10.3390","volume":"14","author":[{"ORCID":"https:\/\/orcid.org\/0009-0009-9148-1543","authenticated-orcid":false,"given":"Varun","family":"Vemulapalli","sequence":"first","affiliation":[{"name":"Department of Internal Medicine, UT Houston Health Science Center, Houston, TX 77030, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3448-4421","authenticated-orcid":false,"given":"Cristina","family":"Natha","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, UT Houston Health Science Center, Houston, TX 77030, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1878-4678","authenticated-orcid":false,"given":"Anusha","family":"Shirwaikar Thomas","sequence":"additional","affiliation":[{"name":"Department of Gastroenterology, Hepatology, and Nutrition, The University of Texas MD Anderson Cancer Center, Houston, TX 77030, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1968","published-online":{"date-parts":[[2025,4,29]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"403","DOI":"10.1016\/j.advms.2020.07.002","article-title":"Autoimmune pancreatitis\u2014An ongoing challenge","volume":"65","author":"Blaho","year":"2020","journal-title":"Adv. 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