{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,19]],"date-time":"2026-02-19T14:53:22Z","timestamp":1771512802319,"version":"3.50.1"},"reference-count":59,"publisher":"MDPI AG","issue":"4","license":[{"start":{"date-parts":[[2026,2,19]],"date-time":"2026-02-19T00:00:00Z","timestamp":1771459200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JCM"],"abstract":"<jats:p>Background: The aim of this prospective longitudinal observational study was to assess respiratory muscle function after surgical correction of scoliosis in individuals with spinal muscular atrophy (SMA). Material: The study included 20 patients (aged 7\u201319) with scoliosis in the course of neuromuscular disease, eligible for surgical treatment with diagnosed SMA Type 2 or 3. Methods: Measurements were taken of the maximal inspiratory pressure (MIP) [cmH2O] and the maximal expiratory pressure (MEP) [cmH2O] in all patients immediately before surgical correction of scoliosis (measurement I), 7 days after surgery (measurement II) and 3 months after surgery (measurement III). Results: The mean Cobb angle of spinal curvature measured before surgery in the entire group was 102.57 \u00b1 17.96. The mean MEP values in the entire group of patients were 40.48 \u00b1 11.76 cmH2O before surgery, 36.74 \u00b1 17.17 cmH2O after 7 days, and 39.17 \u00b1 16.18 cmH2O 3 months after surgery. The MIP values for the entire group were 64.35 \u00b1 28.40 cmH2O before surgery, 53.96 \u00b1 28.66 cmH2O after 7 days, and 67.00 \u00b1 31.27 cmH2O after 3 months. Conclusions: Surgical correction of spinal curvature creates conditions for maintaining respiratory muscle strength in patients with SMA over a period of several months of observation. As a result of the surgical intervention, respiratory muscle strength did not deteriorate, but even slightly increased.<\/jats:p>","DOI":"10.3390\/jcm15041615","type":"journal-article","created":{"date-parts":[[2026,2,19]],"date-time":"2026-02-19T13:47:02Z","timestamp":1771508822000},"page":"1615","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["The Impact of Surgical Correction of Neuromuscular Scoliosis on Respiratory Muscle Function in Individuals with Spinal Muscular Atrophy\u2014Preliminary Report"],"prefix":"10.3390","volume":"15","author":[{"given":"Edyta","family":"Daszkiewicz","sequence":"first","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation, University Hospital of Orthopaedics Rehabilitation in Zakopane, Jagiellonian University Collegium Medicum, 31-008 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7152-2012","authenticated-orcid":false,"given":"Barbara","family":"Jasiewicz","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation, University Hospital of Orthopaedics Rehabilitation in Zakopane, Jagiellonian University Collegium Medicum, 31-008 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Karina","family":"Ro\u017cek","sequence":"additional","affiliation":[{"name":"Institute of Social Sciences and Public Health, Pedagogical University of Krakow, 30-084 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2162-3915","authenticated-orcid":false,"given":"Piotr","family":"Kurzeja","sequence":"additional","affiliation":[{"name":"Institute of Health Sciences, University of Applied Sciences in Nowy Targ, 34-400 Nowy Targ, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Micha\u0142","family":"Zarzycki","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation, University Hospital of Orthopaedics Rehabilitation in Zakopane, Jagiellonian University Collegium Medicum, 31-008 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Zbigniew","family":"Figura","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation, University Hospital of Orthopaedics Rehabilitation in Zakopane, Jagiellonian University Collegium Medicum, 31-008 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0009-8156-4185","authenticated-orcid":false,"given":"Aleksandra","family":"Adamik","sequence":"additional","affiliation":[{"name":"Institute of Applied Sciences, Faculty of Motor Rehabilitation, University of Physical Culture, 31-571 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3714-3676","authenticated-orcid":false,"given":"Katarzyna","family":"Ogrodzka-Ciechanowicz","sequence":"additional","affiliation":[{"name":"Institute of Clinical Rehabilitation, Faculty of Motor Rehabilitation, University of Physical Culture, 31-571 Krakow, Poland"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2026,2,19]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"1164","DOI":"10.1007\/s12325-019-00923-8","article-title":"Survival, motor function, and motor milestones: Comparison of AVXS-101 relative to nusinersen for the treatment of infants with spinal muscular atrophy type 1","volume":"36","author":"Dabbous","year":"2019","journal-title":"Adv Ther."},{"key":"ref_2","doi-asserted-by":"crossref","unstructured":"Verhaart, I.E.C., Robertson, A., Wilson, I.J., Aartsma-Rus, A., Cameron, S., Jones, C.C., Cook, S.F., and Lochm\u00fcller, H. 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