{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,5]],"date-time":"2026-10-05T11:34:00Z","timestamp":1791200040846,"version":"4.2.0"},"reference-count":35,"publisher":"MDPI AG","issue":"4","license":[{"start":{"date-parts":[[2020,3,27]],"date-time":"2020-03-27T00:00:00Z","timestamp":1585267200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JCM"],"abstract":"<jats:p>Cardiomyopathies are responsible for heart failure and sudden cardiac death, but epidemiological data are scarce and the public health burden may be underestimated. We studied aggregating data from all public or private hospitals in France. Patients were categorized from relevant ICD-10 codes into dilated, hypertrophic, restrictive, or other cardiomyopathies (DCM, HCM, RCM, or OCM, respectively). Between 2008 and 2015, a total of 326,461 distinct patients had cardiomyopathy-related hospitalizations. The hospital-based prevalence of cardiomyopathy was 809 per million inhabitants (PMI) per year, including 428 PMI for DCM, 101 PMI for HCM, 26 PMI for RCM, and 253 PMI for OCM. Patients with cardiomyopathies accounted for 51% of all heart transplants, 33% of defibrillator implantations, 38% of mechanical circulatory supports, and 11.3% of hospitalizations for heart failure. In patients less than 40 years of age, these figures were 71%, 51%, 63%, and 23%, respectively. Over 2008\u20132015 and considering all cardiomyopathies, there was a significant increase for heart transplant (average annual percentage change, AAPC: +3.86%, p = 0.0015) and for defibrillator implantation (AAPC: +6.98%, p &lt; 0.0001), and a significant decrease of in-hospital mortality (AAPC: \u22124.7%, p = 0.0002). This nationwide study shows that cardiomyopathies constitute an important cause of hospitalization, with increasing invasive therapeutic procedures and decreasing mortality.<\/jats:p>","DOI":"10.3390\/jcm9040920","type":"journal-article","created":{"date-parts":[[2020,4,2]],"date-time":"2020-04-02T13:39:34Z","timestamp":1585834774000},"page":"920","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":30,"title":["The Public Health Burden of Cardiomyopathies: Insights from a Nationwide Inpatient Study"],"prefix":"10.3390","volume":"9","author":[{"given":"Simon","family":"Lannou","sequence":"first","affiliation":[{"name":"APHP, Service de Cardiologie, Centre de r\u00e9f\u00e9rence des maladies cardiaques h\u00e9r\u00e9ditaires ou rares, H\u00f4pital Ambroise Par\u00e9, 92100 Boulogne Billancourt, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5500-1535","authenticated-orcid":false,"given":"Nicolas","family":"Mansencal","sequence":"additional","affiliation":[{"name":"APHP, Service de Cardiologie, Centre de r\u00e9f\u00e9rence des maladies cardiaques h\u00e9r\u00e9ditaires ou rares, H\u00f4pital Ambroise Par\u00e9, 92100 Boulogne Billancourt, France"},{"name":"Univ Paris-Saclay, Univ Versailles-Saint Quentin, Univ Paris-Sud, Inserm, Clinical Epidemiology Team, CESP Centre for Research in Epidemiology and Population Health, 94807 Villejuif, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"C\u00e9cile","family":"Couchoud","sequence":"additional","affiliation":[{"name":"Agence de la Biom\u00e9decine, 93212 Saint-Denis la Plaine, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mathilde","family":"Lassalle","sequence":"additional","affiliation":[{"name":"Agence de la Biom\u00e9decine, 93212 Saint-Denis la Plaine, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Olivier","family":"Dubourg","sequence":"additional","affiliation":[{"name":"APHP, Service de Cardiologie, Centre de r\u00e9f\u00e9rence des maladies cardiaques h\u00e9r\u00e9ditaires ou rares, H\u00f4pital Ambroise Par\u00e9, 92100 Boulogne Billancourt, France"},{"name":"Univ Paris-Saclay, Univ Versailles-Saint Quentin, Univ Paris-Sud, Inserm, Clinical Epidemiology Team, CESP Centre for Research in Epidemiology and Population Health, 94807 Villejuif, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"B\u00e9n\u00e9dicte","family":"Stengel","sequence":"additional","affiliation":[{"name":"Univ Paris-Saclay, Univ Versailles-Saint Quentin, Univ Paris-Sud, Inserm, Clinical Epidemiology Team, CESP Centre for Research in Epidemiology and Population Health, 94807 Villejuif, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5904-7570","authenticated-orcid":false,"given":"Christian","family":"Jacquelinet","sequence":"additional","affiliation":[{"name":"Univ Paris-Saclay, Univ Versailles-Saint Quentin, Univ Paris-Sud, Inserm, Clinical Epidemiology Team, CESP Centre for Research in Epidemiology and Population Health, 94807 Villejuif, France"},{"name":"Agence de la Biom\u00e9decine, 93212 Saint-Denis la Plaine, France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1782-1118","authenticated-orcid":false,"given":"Philippe","family":"Charron","sequence":"additional","affiliation":[{"name":"APHP, Service de Cardiologie, Centre de r\u00e9f\u00e9rence des maladies cardiaques h\u00e9r\u00e9ditaires ou rares, H\u00f4pital Ambroise Par\u00e9, 92100 Boulogne Billancourt, France"},{"name":"APHP, D\u00e9partement de G\u00e9n\u00e9tique, Centre de r\u00e9f\u00e9rence des maladies cardiaques h\u00e9r\u00e9ditaires ou rares, H\u00f4pital Piti\u00e9-Salp\u00eatri\u00e8re, 75013 Paris, France"},{"name":"Sorbonne Universit\u00e9, INSERM, UMR_S 1166 and ICAN Institute for Cardiometabolism and Nutrition, 75013 Paris, France"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1968","published-online":{"date-parts":[[2020,3,27]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"270","DOI":"10.1093\/eurheartj\/ehm342","article-title":"Classification of the cardiomyopathies: A position statement from the European Society of Cardiology Working Group on myocardial and pericardial diseases","volume":"29","author":"Elliott","year":"2008","journal-title":"Eur. Heart J."},{"key":"ref_2","doi-asserted-by":"crossref","first-page":"1807","DOI":"10.1161\/CIRCULATIONAHA.106.174287","article-title":"Contemporary definitions and classification of the cardiomyopathies: An American Heart Association Scientific Statement from the Council on Clinical Cardiology, Heart Failure and Transplantation Committee","volume":"113","author":"Maron","year":"2006","journal-title":"Circulation"},{"key":"ref_3","doi-asserted-by":"crossref","first-page":"1850","DOI":"10.1093\/eurheartj\/ehv727","article-title":"Proposal for a revised definition of dilated cardiomyopathy, hypokinetic non-dilated cardiomyopathy, and its implications for clinical practice: A position statement of the ESC working group on myocardial and pericardial diseases","volume":"37","author":"Pinto","year":"2016","journal-title":"Eur. Heart J."},{"key":"ref_4","doi-asserted-by":"crossref","unstructured":"Miles, C., Fanton, Z., Tome, M., and Behr, E.R. (2019). Inherited cardiomyopathies. BMJ, 365.","DOI":"10.1136\/bmj.l1570"},{"key":"ref_5","doi-asserted-by":"crossref","first-page":"400","DOI":"10.1016\/S0140-6736(16)31713-5","article-title":"Dilated cardiomyopathy","volume":"390","author":"Weintraub","year":"2017","journal-title":"Lancet"},{"key":"ref_6","doi-asserted-by":"crossref","first-page":"214","DOI":"10.1097\/HCO.0b013e32832a1d2e","article-title":"Restrictive cardiomyopathy","volume":"24","author":"Mogensen","year":"2009","journal-title":"Curr. Opin. Cardiol."},{"key":"ref_7","doi-asserted-by":"crossref","first-page":"1253","DOI":"10.1016\/S0140-6736(16)31321-6","article-title":"Hypertrophic obstructive cardiomyopathy","volume":"389","author":"Veselka","year":"2017","journal-title":"Lancet"},{"key":"ref_8","doi-asserted-by":"crossref","first-page":"61","DOI":"10.1056\/NEJMra1509267","article-title":"Arrhythmogenic right ventricular cardiomyopathy","volume":"376","author":"Corrado","year":"2017","journal-title":"Jarcho JA. N. Engl. J. Med."},{"key":"ref_9","doi-asserted-by":"crossref","first-page":"722","DOI":"10.1161\/CIRCRESAHA.117.309711","article-title":"Classification, epidemiology, and global burden of cardiomyopathies","volume":"121","author":"McKenna","year":"2017","journal-title":"Circ. Res."},{"key":"ref_10","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.jacc.2017.04.052","article-title":"Global, Regional, and National Burden of Cardiovascular Diseases for 10 Causes, 1990 to 2015","volume":"70","author":"Roth","year":"2017","journal-title":"J. Am. Coll. Cardiol."},{"key":"ref_11","doi-asserted-by":"crossref","first-page":"785","DOI":"10.1161\/01.CIR.92.4.785","article-title":"Prevalence of hypertrophic cardiomyopathy in a general population of young adults: Echocardiographic analysis of 4111 subjects in the CARDIA Study","volume":"92","author":"Maron","year":"1995","journal-title":"Circulation"},{"key":"ref_12","doi-asserted-by":"crossref","first-page":"564","DOI":"10.1161\/01.CIR.80.3.564","article-title":"Epidemiology of idiopathic dilated and hypertrophic cardiomyopathy. A population-based study in Olmsted County, Minnesota, 1975\u20131984","volume":"80","author":"Codd","year":"1989","journal-title":"Circulation"},{"key":"ref_13","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1001\/jamacardio.2019.4534","article-title":"Mortality among Referral Patients With Hypertrophic Cardiomyopathy vs. the General European Population","volume":"5","author":"Lorenzini","year":"2020","journal-title":"JAMA Cardiol."},{"key":"ref_14","doi-asserted-by":"crossref","first-page":"2441","DOI":"10.1056\/NEJMoa1510687","article-title":"A Prospective study of sudden cardiac death among children and young adults","volume":"374","author":"Bagnall","year":"2016","journal-title":"N. Engl. J. Med."},{"key":"ref_15","doi-asserted-by":"crossref","first-page":"1085","DOI":"10.1161\/CIRCULATIONAHA.108.804617","article-title":"Sudden deaths in young competitive athletes: Analysis of 1866 deaths in the United States, 1980\u20132006","volume":"119","author":"Maron","year":"2009","journal-title":"Circulation"},{"key":"ref_16","doi-asserted-by":"crossref","first-page":"1784","DOI":"10.1093\/eurheartj\/ehx819","article-title":"The Cardiomyopathy Registry of the EURObservational Research Programme of the European Society of Cardiology: Baseline data and contemporary management of adult patients with cardiomyopathies","volume":"39","author":"Charron","year":"2018","journal-title":"Eur. Heart J."},{"key":"ref_17","doi-asserted-by":"crossref","first-page":"1166","DOI":"10.1016\/j.jval.2011.07.001","article-title":"DRG-Based Hospital Payment Systems and Technological Innovation in 12 European Countries","volume":"14","author":"Quentin","year":"2011","journal-title":"Value Health"},{"key":"ref_18","first-page":"77","article-title":"The French organ transplant data system","volume":"116","author":"Strang","year":"2005","journal-title":"Stud. Health Technol. Inform."},{"key":"ref_19","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1002\/(SICI)1097-0258(20000215)19:3<335::AID-SIM336>3.0.CO;2-Z","article-title":"Permutation tests for joinpoint regression with applications to cancer rates","volume":"19","author":"Kim","year":"2000","journal-title":"Stat. Med."},{"key":"ref_20","doi-asserted-by":"crossref","unstructured":"Cantrelle, C., Legeai, C., Latouche, A., Tuppin, P., Jasseron, C., Sebbag, L., Bastien, O., and Dorent, R. (2017). Access to Heart Transplantation: A proper analysis of the competing risks of death and transplantation is required to optimize graft allocation. Transplant. Direct, 3.","DOI":"10.1097\/TXD.0000000000000711"},{"key":"ref_21","doi-asserted-by":"crossref","first-page":"80","DOI":"10.1016\/j.ejcts.2009.06.054","article-title":"Trends in adult heart transplantation: A national survey from the United Kingdom Cardiothoracic Transplant Audit 1995\u20132007","volume":"37","author":"Thekkudan","year":"2010","journal-title":"Eur. J. Cardiothorac. Surg."},{"key":"ref_22","first-page":"27","article-title":"An update on cardiac transplantation in the United States based on an analysis of the UNOS Registry","volume":"31","author":"Khatiwala","year":"2015","journal-title":"Clin. Transpl."},{"key":"ref_23","doi-asserted-by":"crossref","first-page":"906","DOI":"10.1016\/j.jchf.2015.06.012","article-title":"Characteristics, treatments, and outcomes of hospitalized heart failure patients stratified by etiologies of cardiomyopathy","volume":"3","author":"Shore","year":"2015","journal-title":"JACC Heart Failure"},{"key":"ref_24","doi-asserted-by":"crossref","first-page":"1763","DOI":"10.1185\/03007995.2011.604310","article-title":"Prevalence of pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension in the United States","volume":"27","author":"Kirson","year":"2011","journal-title":"Curr. Med. Res. Opin."},{"key":"ref_25","doi-asserted-by":"crossref","first-page":"2793","DOI":"10.1093\/eurheartj\/ehv316","article-title":"2015 ESC Guidelines for the management of patients with ventricular arrhythmias and the prevention of sudden cardiac death: The Task Force for the Management of Patients with Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death of the European Society of Cardiology","volume":"36","author":"Priori","year":"2015","journal-title":"Eur. Heart J."},{"key":"ref_26","doi-asserted-by":"crossref","first-page":"531","DOI":"10.1038\/nrcardio.2013.105","article-title":"Dilated cardiomyopathy: The complexity of a diverse genetic architecture","volume":"10","author":"Hershberger","year":"2013","journal-title":"Nat. Rev. Cardiol."},{"key":"ref_27","doi-asserted-by":"crossref","first-page":"2585","DOI":"10.1093\/eurheartj\/ehv338","article-title":"Wild-type transthyretin amyloidosis as a cause of heart failure with preserved ejection fraction","volume":"36","author":"Robles","year":"2015","journal-title":"Eur. Heart J."},{"key":"ref_28","doi-asserted-by":"crossref","first-page":"2010","DOI":"10.1093\/eurheartj\/eht439","article-title":"A novel clinical risk prediction model for sudden cardiac death in hypertrophic cardiomyopathy (HCM Risk-SCD)","volume":"35","author":"Jichi","year":"2014","journal-title":"Eur. Heart J."},{"key":"ref_29","doi-asserted-by":"crossref","first-page":"1850","DOI":"10.1093\/eurheartj\/ehz103","article-title":"A new prediction model for ventricular arrhythmias in arrhythmogenic right ventricular cardiomyopathy","volume":"40","author":"Bosman","year":"2019","journal-title":"Eur. Heart J."},{"key":"ref_30","doi-asserted-by":"crossref","unstructured":"Norrish, G., Ding, T., Field, E., Zi\u00f3\u0142kowska, L., Olivotto, I., Limongelli, G., Anastasakis, A., Weintraub, R., Biagini, E., and Ragni, L. (2019). Development of a Novel Risk Prediction Model for Sudden Cardiac Death in Childhood Hypertrophic Cardiomyopathy (HCM Risk-Kids). JAMA Cardiol., 14.","DOI":"10.1093\/eurheartj\/ehz747.0062"},{"key":"ref_31","doi-asserted-by":"crossref","first-page":"1536","DOI":"10.1161\/CIRCRESAHA.119.313569","article-title":"Novel therapies for prevention and early treatment of cardiomyopathies","volume":"124","author":"Repetti","year":"2019","journal-title":"Circ. Res."},{"key":"ref_32","doi-asserted-by":"crossref","first-page":"403","DOI":"10.2147\/CLEP.S139300","article-title":"Misclassification of hypertrophic cardiomyopathy: Validation of diagnostic codes","volume":"9","author":"Magnusson","year":"2017","journal-title":"Clin. Epidemiol."},{"key":"ref_33","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1186\/s13023-015-0251-8","article-title":"Rare diseases in ICD11: Making rare diseases visible in health information systems through appropriate coding","volume":"10","author":"Bellet","year":"2015","journal-title":"Orphanet. J. Rare Dis."},{"key":"ref_34","doi-asserted-by":"crossref","first-page":"S149","DOI":"10.1016\/j.respe.2017.05.004","article-title":"Value of a national administrative database to guide public decisions: From the Syst\u00e8me national d\u2019information inter-r\u00e9gimes de l\u2019Assurance Maladie (SNIIRAM) to the Syst\u00e8me national des donn\u00e9es de sant\u00e9 (SNDS) in France","volume":"65","author":"Tuppin","year":"2017","journal-title":"Rev. Epidemiol. Sante Publique"},{"key":"ref_35","doi-asserted-by":"crossref","unstructured":"McCormick, N., Lacaille, D., Bhole, V., and Avina-Zubieta, J.A. (2014). Validity of Heart Failure Diagnoses in Administrative Databases: A Systematic Review and Meta-Analysis. PLoS ONE, 9.","DOI":"10.1371\/journal.pone.0104519"}],"container-title":["Journal of Clinical Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.mdpi.com\/2077-0383\/9\/4\/920\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,10,11]],"date-time":"2025-10-11T09:12:24Z","timestamp":1760173944000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.mdpi.com\/2077-0383\/9\/4\/920"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,3,27]]},"references-count":35,"journal-issue":{"issue":"4","published-online":{"date-parts":[[2020,4]]}},"alternative-id":["jcm9040920"],"URL":"https:\/\/doi.org\/10.3390\/jcm9040920","relation":{},"ISSN":["2077-0383"],"issn-type":[{"value":"2077-0383","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,3,27]]}}}