{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T09:10:05Z","timestamp":1772356205390,"version":"3.50.1"},"reference-count":10,"publisher":"Maad Rayan Publishing Company","issue":"4","content-domain":{"domain":["mejdd.org"],"crossmark-restriction":false},"short-container-title":["Middle East J Dig Dis"],"published-print":{"date-parts":[[2023,10,30]]},"abstract":"<jats:p>A rare congenital hepatobiliary disorder called Caroli\u2019s disease is characterized by multifocal segmental dilatation of intrahepatic bile ducts that can affect the entire liver or only specific areas of it. Coexisting conditions with Caroli\u2019s disease include autosomal dominant polycystic kidney disease (ADPKD) and autosomal recessive polycystic kidney disease (ARPKD). ADPKD results in the development of cysts, which are tiny fluid-filled sacs, in the kidneys. Caroli\u2019s disease is considered a rare disorder, affecting a small number of individuals worldwide. The symptoms of Caroli\u2019s disease can vary from person to person and it also may overlap with other liver and biliary disorders. As a result, it may be challenging to diagnose and manage the condition due to limited awareness and expertise. Increased awareness, research, and specialized medical care are crucial in improving outcomes for individuals affected by this rare disorder. This study involves the case of a 60- year-old woman presented with abdominal pain, fever, weight loss, and jaundice. Her imaging test endoscopic retrograde cholangiopancreatography (ERCP) signifies Caroli\u2019s disease with pancreatic duct (PD) calculi and management involves supportive care with antibiotics. Antibiotics were prescribed to prevent or treat infections such as cholangitis and nutritional supplement was recommended in managing Caroli\u2019s disease. The patient underwent pancreatic stent placement and was discharged with regular follow-up. So, this case highlights the clinical and diagnostic aspects to improve disease understanding and the progression of Caroli\u2019s illness along with ADPKD.<\/jats:p>","DOI":"10.34172\/mejdd.2023.360","type":"journal-article","created":{"date-parts":[[2024,1,27]],"date-time":"2024-01-27T07:47:35Z","timestamp":1706341655000},"page":"289-292","update-policy":"https:\/\/doi.org\/10.34172\/crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Caroli\u2019s Disease Associated with Autosomal Dominant Polycystic Kidney Disease with Acute Pancreatitis: A Case Report"],"prefix":"10.34172","volume":"15","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-6407-6739","authenticated-orcid":true,"given":"Karishma M","family":"Rathi","sequence":"first","affiliation":[{"name":"Department of Pharmacy Practice at Dr. D.Y. Patil Institute of Pharmaceutical Sciences and Research Pimpri, Pune, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6766-5670","authenticated-orcid":true,"given":"Priyanka","family":"Pingat","sequence":"additional","affiliation":[{"name":"Department of Pharmacy Practice at Dr. D.Y. Patil Institute of Pharmaceutical Sciences and Research Pimpri, Pune, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4737-7449","authenticated-orcid":true,"given":"Prachi","family":"Bansode","sequence":"additional","affiliation":[{"name":"Department of Pharmacy Practice at Dr. D.Y. Patil Institute of Pharmaceutical Sciences and Research Pimpri, Pune, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0838-5254","authenticated-orcid":true,"given":"Shaili","family":"Dongare","sequence":"additional","affiliation":[{"name":"Department of Pharmacy Practice at Dr. D.Y. Patil Institute of Pharmaceutical Sciences and Research Pimpri, Pune, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"20123","published-online":{"date-parts":[[2023,10,30]]},"reference":[{"key":"R1","doi-asserted-by":"publisher","DOI":"10.1007\/s12664-013-0403-5"},{"key":"R2","unstructured":"Sweeney WE, Avner ED. Polycystic kidney disease, autosomal recessive. In: Adam MP, Feldman J, Mirzaa GM, Pagon RA, Wallace SE, Bean LJH, et al, eds. GeneReviews\u00ae. Seattle, WA: University of Washington; 2001. https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK1326\/."},{"key":"R3","doi-asserted-by":"publisher","DOI":"10.32677\/IJCR.2019.v05.i01.026"},{"key":"R4","first-page":"2185","article-title":"Monolobar Caroli\u2019s disease in an adult Case report","volume":"50","author":"Giovanardi RO","year":"2003","journal-title":"Hepatogastroenterology"},{"key":"R5","doi-asserted-by":"publisher","DOI":"10.1007\/s11894-007-0010-7"},{"key":"R6","doi-asserted-by":"publisher","DOI":"10.5958\/2454-2652.2017.00075.0"},{"key":"R7","first-page":"23","article-title":"Monolobar Caroli\u2019s disease: report of three cases","volume":"2","author":"Seddik H","year":"2017","journal-title":"Int J Gastroenterol Hepatol TransplNutr"},{"key":"R8","doi-asserted-by":"publisher","DOI":"10.3748\/wjg.v13.i13.1930"},{"key":"R9","doi-asserted-by":"publisher","DOI":"10.1186\/s12884-021-03768-8"},{"key":"R10","doi-asserted-by":"publisher","DOI":"10.18502\/crcp.v4i3.1716"}],"container-title":["Middle East Journal of Digestive Diseases"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/mejdd.org\/index.php\/mejdd\/article\/view\/2859\/2340","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/mejdd.org\/index.php\/mejdd\/article\/view\/2859\/2340","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,1,27]],"date-time":"2024-01-27T07:47:44Z","timestamp":1706341664000},"score":1,"resource":{"primary":{"URL":"http:\/\/mejdd.org\/index.php\/mejdd\/article\/view\/2859"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,10,30]]},"references-count":10,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2023,10,30]]}},"URL":"https:\/\/doi.org\/10.34172\/mejdd.2023.360","relation":{},"ISSN":["2008-5249"],"issn-type":[{"value":"2008-5249","type":"print"}],"subject":[],"published":{"date-parts":[[2023,10,30]]},"assertion":[{"value":"Iranian Association of Gastroerterology and Hepatology","name":"journal_owner","label":"Journal Owner"},{"value":"Iranian Association of Gastroerterology and Hepatology","name":"journal_publisher","label":"Journal Publisher"},{"value":"2023-03-09","order":1,"name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2023-08-07","order":2,"name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}},{"value":"2023-10-30","order":3,"name":"published","label":"Published","group":{"name":"publication_history","label":"Publication History"}}]}}