{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,8]],"date-time":"2025-10-08T22:04:24Z","timestamp":1759961064101,"version":"3.37.0"},"reference-count":0,"publisher":"American Academy of Audiology","issue":"10","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["j am acad audiol"],"published-print":{"date-parts":[[2005,11,1]]},"abstract":"<jats:p>A 23-month-old female was referred for hearing aid fitting after failing newborn hearing screening and being diagnosed with significant hearing loss through subsequent diagnostic testing. Auditory brainstem response (ABR) and behavioral testing revealed a moderate-to-severe bilateral\n mixed hearing loss. Prior to the hearing aid evaluation, tympanostomy tubes had been placed bilaterally with little or no apparent change in hearing sensitivity. Initial testing during the hearing aid fitting confirmed earlier findings, but abnormal middle ear results were observed, requiring\n referral for additional otologic management. Following medical clearance, binaural digital programmable hearing aids were fit using Desired Sensation Level parameters. Behavioral testing and probe microphone measures showed significant improvements in audibility. Decrease in hearing sensitivity\n was observed six months following hearing aid fitting. Radiological studies, ordered due to the mixed component and decreased hearing sensitivity, revealed large vestibular aqueduct syndrome (LVAS). Based on the diagnosis of LVAS, a cochlear implant was placed on the right ear; almost immediate\n speech-language gains were observed. Una ni\u00f1a de 23 meses de edad fue referida para adaptaci\u00f3n de aud\u00edfonos luego de fallar una prueba de tamizaje auditivo para reci\u00e9n nacidos, y de establecerse que era portadora de una hipoacusia significativa con el uso de pruebas\n diagn\u00f3sticas subsecuentes. Las respuestas evocadas de tallo cerebral (ABR) y las pruebas audiom\u00e9tricas conductuales demostraron una hipoacusia mixta bilateral de grado moderado a severo. Previo a la evaluaci\u00f3n para adaptar auxiliares auditivos se le colocaron tubos timp\u00e1nicos\n sin cambio aparente su sensibilidad auditiva. Las pruebas iniciales durante la adaptaci\u00f3n de los auxiliares auditivos confirmaron los hallazgos iniciales, pero se observaron resultados anormales en la funci\u00f3n del o\u00eddo medio que requirieron una referencia para manejo otol\u00f3gico.\n Cu\u00e1ndo fue dada de alta m\u00e9dicamente, se le adaptaron auxiliares auditivos digitalmente programables en forma binaural utilizando par\u00e1metros de Nivel Deseado de Sensaci\u00f3n. Las pruebas conductuales y las medidas de micr\u00f3fono de sonda mostraron un incremento\n significativo en la audibilidad. Una disminuci\u00f3n en la sensibilidad auditiva se observ\u00f3 seis meses despu\u00e9s de la adaptaci\u00f3n de los aud\u00edfonos. Los estudios radiol\u00f3gicos, ordenados debido al componente mixto y a la disminuci\u00f3n en la sensibilidad\n auditiva, revelaron un s\u00edndrome de acueducto vestibular grande (LVAS). Basados en el diagn\u00f3stico de LVAS se coloc\u00f3 un implante coclear en el o\u00eddo derecho, y casi de inmediato, se observ\u00f3 una mejor\u00eda en el habla-lenguaje.<\/jats:p>","DOI":"10.3766\/jaaa.16.10.6","type":"journal-article","created":{"date-parts":[[2008,4,22]],"date-time":"2008-04-22T23:54:28Z","timestamp":1208908468000},"page":"822-828","source":"Crossref","is-referenced-by-count":4,"title":["Large Vestibular Aqueduct Syndrome: A Case Study"],"prefix":"10.3766","volume":"16","author":[{"given":"Jackie L.","family":"Clark","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ross J.","family":"Roeser","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"2087","container-title":["Journal of the American Academy of Audiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ingentaconnect.com\/content\/aaa\/jaaa\/2005\/00000016\/00000010\/art00006","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,2,5]],"date-time":"2025-02-05T23:12:22Z","timestamp":1738797142000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ingentaconnect.com\/content\/10.3766\/jaaa.16.10.6"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2005,11,1]]},"references-count":0,"journal-issue":{"issue":"10","published-print":{"date-parts":[[2005,11,1]]}},"alternative-id":["1050-0545(20051101)16:10L.822;1-"],"URL":"https:\/\/doi.org\/10.3766\/jaaa.16.10.6","relation":{},"ISSN":["1050-0545"],"issn-type":[{"type":"print","value":"1050-0545"}],"subject":[],"published":{"date-parts":[[2005,11,1]]}}}