{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,20]],"date-time":"2026-09-20T18:24:46Z","timestamp":1789928686385,"version":"4.0.1"},"reference-count":0,"publisher":"MyJove Corporation","issue":"130","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JoVE"],"DOI":"10.3791\/56550","type":"journal-article","created":{"date-parts":[[2017,12,20]],"date-time":"2017-12-20T19:01:08Z","timestamp":1513796468000},"source":"Crossref","is-referenced-by-count":3,"title":["&lt;em&gt;In Vitro&lt;\/em&gt; Enzyme Measurement to Test Pharmacological Chaperone Responsiveness in Fabry and Pompe Disease"],"prefix":"10.3791","author":[{"given":"Jan","family":"Lukas","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anne-Marie","family":"Knospe","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Susanne","family":"Seemann","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Valentina","family":"Citro","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Maria V.","family":"Cubellis","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Arndt","family":"Rolfs","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"2098","published-online":{"date-parts":[[2017,12,20]]},"container-title":["Journal of Visualized Experiments"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.jove.com\/video\/56550\/in-vitro-enzyme-measurement-to-test-pharmacological-chaperone","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,2,27]],"date-time":"2025-02-27T16:07:24Z","timestamp":1740672444000},"score":1,"resource":{"primary":{"URL":"https:\/\/app.jove.com\/t\/56550"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,12,20]]},"references-count":0,"journal-issue":{"issue":"130","published-online":{"date-parts":[[2017]]}},"URL":"https:\/\/doi.org\/10.3791\/56550","relation":{},"ISSN":["1940-087X"],"issn-type":[{"value":"1940-087X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,12,20]]}}}