{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,26]],"date-time":"2026-09-26T18:27:47Z","timestamp":1790447267303,"version":"4.1.0"},"reference-count":11,"publisher":"MDPI AG","issue":"2","license":[{"start":{"date-parts":[[2018,6,27]],"date-time":"2018-06-27T00:00:00Z","timestamp":1530057600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Reports"],"abstract":"<jats:p>Rapunzel syndrome is a rare form of tricobezoar with a tail extending from the stomach into the small bowel; surgical removal is generally required. About 60 cases have been reported and described in the literature since 1968. We present the case of an 8-year-old girl who, during the course of a genetic consultation, was initially assigned with a clinical suspicion of ectodermal dysplasia. Surgical intervention, which resulted in the extraction of a tricobezoar of enormous size and extension, led us to the diagnosis of Rapunzel syndrome. The possibility of a tricobezoar should be considered in all cases of adolescent patients who present signs of intestinal occlusion or sub-occlusion, suffer from psychiatric disorders, and have a history of trichotillomania. Endoscopic methodology, medical imaging and clinical diagnostics are fundamental for a differential diagnosis. Psychiatric follow-up is advised to prevent recurrence.<\/jats:p>","DOI":"10.4081\/pr.2018.7689","type":"journal-article","created":{"date-parts":[[2018,7,13]],"date-time":"2018-07-13T10:05:17Z","timestamp":1531476317000},"page":"7689","source":"Crossref","is-referenced-by-count":14,"title":["Rapunzel Syndrome: How to Orient the Diagnosis"],"prefix":"10.3390","volume":"10","author":[{"given":"Enrico","family":"Finale","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Piergiorgio","family":"Franceschini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cesare","family":"Danesino","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michelangelo","family":"Barbaglia","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andrea","family":"Guala","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1968","published-online":{"date-parts":[[2018,6,27]]},"reference":[{"key":"ref1","first-page":"339","article-title":"The Rapunzel syndrome. 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A case report","volume":"168","author":"Ko\u00e7","year":"2009","journal-title":"Eur J Ped"},{"key":"ref5","doi-asserted-by":"crossref","first-page":"2240","DOI":"10.1007\/s11605-007-0460-0","article-title":"Rapunzel syndrome complicated with gastric perforation diagnosed on operation table","volume":"12","author":"Mohite","year":"2008","journal-title":"J Gastrointestin Surg"},{"key":"ref6","doi-asserted-by":"crossref","first-page":"653","DOI":"10.1016\/S0025-6196(11)64889-1","article-title":"Gastric trichobezoar: Case report and literature review","volume":"73","author":"Phillips","year":"1998","journal-title":"Mayo Clin Proc"},{"key":"ref7","doi-asserted-by":"crossref","first-page":"2361","DOI":"10.1111\/j.1440-1746.2007.05230.x","article-title":"Gastrointestinal: Rapunzel syndrome","volume":"22","author":"Irving","year":"2007","journal-title":"J Gastroenterol Hepatol"},{"key":"ref8","doi-asserted-by":"crossref","first-page":"166","DOI":"10.12659\/PJR.896154","article-title":"Rapunzel Syndrome: Rare \u201ctale\u201d of a broken \u201ctail\u201d","volume":"81","author":"Chauhan","year":"2016","journal-title":"Pol J Radiol"},{"key":"ref9","doi-asserted-by":"crossref","first-page":"e3745","DOI":"10.1097\/MD.0000000000003745","article-title":"A case report: large trichobezoar causing Rapunzel Syndrome","volume":"95","author":"Kim","year":"2016","journal-title":"Medicine"},{"key":"ref10","first-page":"28","article-title":"Trichobezoar and Rapunzel syndrome: A review","volume":"4","author":"Sharma","year":"2015","journal-title":"Oncol Gastroenterol Hepatol Rep"},{"key":"ref11","doi-asserted-by":"crossref","first-page":"79","DOI":"10.1515\/jtim-2015-0008","article-title":"Rapunzel syndrome","volume":"3","author":"Altonbary","year":"2015","journal-title":"J Transl Int Med"}],"container-title":["Pediatric Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.pagepress.org\/journals\/index.php\/pr\/article\/viewFile\/7689\/7375","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/www.mdpi.com\/2036-7503\/10\/2\/7689\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,2,10]],"date-time":"2022-02-10T04:05:05Z","timestamp":1644465905000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.mdpi.com\/2036-7503\/10\/2\/7689"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,6,27]]},"references-count":11,"journal-issue":{"issue":"2","published-online":{"date-parts":[[2018,5]]}},"alternative-id":["pr.2018.7689"],"URL":"https:\/\/doi.org\/10.4081\/pr.2018.7689","relation":{},"ISSN":["2036-7503"],"issn-type":[{"value":"2036-7503","type":"electronic"}],"subject":[],"published":{"date-parts":[[2018,6,27]]}}}