{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T20:03:50Z","timestamp":1787169830806,"version":"build-2736575974"},"reference-count":11,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"5","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2023,9]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Dystonia has been described in a few cases with SSPE, but there are only very few reports with status dystonicus and none from South India. Here, we report a six-year-old child presenting with severe dystonic posturing of all four limbs and trunk for 10 days duration following a febrile illness and initially treated elsewhere as viral encephalitis. Scalp EEG showed periodic high-amplitude slow wave discharges. MRI brain showed T2\/FLAIR hyperintensity in bilateral frontal, left parietal, and deep white matter, extending across the corpus collosum with diffuse cerebral atrophy. The titer for IgG antibodies to measles virus by ELISA was 1:625, suggestive of SSPE. With medications, dystonia used to subside transiently; however, the patient had worsening of symptoms and showed gradual deterioration.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/0028-3886.388104","type":"journal-article","created":{"date-parts":[[2023,10,18]],"date-time":"2023-10-18T07:01:15Z","timestamp":1697612475000},"page":"994-997","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":2,"title":["Status Dystonicus in Subacute Sclerosing Panencephalitis-A Rare Presentation in Emergency"],"prefix":"10.4103","volume":"71","author":[{"given":"Ganaraja Valakunja","family":"Harikrishna","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mundlamuri Ravindranadh","family":"Chowdary","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Seena","family":"Vengalil","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Atchayaram","family":"Nalini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ravi","family":"Yadav","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-25-20240907","first-page":"90","article-title":"Status dystonicus and rhabdomyolysis in a patient with subacute sclerosing panencephalitis","volume":"54","author":"Yi\u015f","year":"2012","journal-title":"Turk J Pediatr"},{"key":"R2-25-20240907","doi-asserted-by":"crossref","first-page":"109","DOI":"10.4103\/0028-3886.152678","article-title":"Subacute sclerosing panencephalitis masquerading as rapid-onset dystonia-parkinsonism in a child","volume":"63","author":"Kannan","year":"2015","journal-title":"Neurol India"},{"key":"R3-25-20240907","doi-asserted-by":"crossref","first-page":"1173","DOI":"10.1002\/1531-8257(200011)15:6<1173::AID-MDS1017>3.0.CO;2-U","article-title":"Implication of sensorimotor integration in the generation of periodic dystonic myoclonus in subacute sclerosing panencephalitis (SSPE)","volume":"15","author":"Oga","year":"2000","journal-title":"Mov Disord"},{"key":"R4-25-20240907","doi-asserted-by":"crossref","first-page":"899","DOI":"10.1177\/0883073808330184","article-title":"Subacute sclerosing panencephalitis (SSPE) presenting as acute disseminated encephalomyelitis in a child","volume":"24","author":"Goraya","year":"2009","journal-title":"J Child Neurol"},{"key":"R5-25-20240907","first-page":"441","article-title":"Dystonic storm: An atypical presentation of subacute sclerosing panencephalitis","volume":"55","author":"Goswami","year":"2018","journal-title":"Indian Pediatri"},{"key":"R6-25-20240907","doi-asserted-by":"crossref","first-page":"137","DOI":"10.4274\/haseki.1451","article-title":"Subacute slerosing panencephalitis presenting as hemidystonia","volume":"52","author":"Serin","year":"2014","journal-title":"Med Bull Haseki"},{"key":"R7-25-20240907","doi-asserted-by":"crossref","first-page":"154","DOI":"10.1002\/mds.10005","article-title":"Physiological assessment of paroxysmal dystonia secondary to subacute sclerosing panencephalitis","volume":"17","author":"Ondo","year":"2002","journal-title":"Mov Disord"},{"key":"R8-25-20240907","doi-asserted-by":"crossref","first-page":"bcr2012007052","DOI":"10.1136\/bcr-2012-007052","article-title":"Evolution of certain typical and atypical features in a case of subacute sclerosing panencephalitis","volume":"2012","author":"Raut","year":"2012","journal-title":"BMJ Case Rep"},{"key":"R9-25-20240907","doi-asserted-by":"crossref","first-page":"958","DOI":"10.1002\/mds.25532","article-title":"Emerging concepts in the physiological basis of dystonia","volume":"28","author":"Quartarone","year":"2013","journal-title":"Mov Disord"},{"key":"R10-25-20240907","doi-asserted-by":"crossref","first-page":"1667","DOI":"10.1002\/mds.27207","article-title":"Rethinking status dystonicus","volume":"32","author":"Ruiz-Lopez","year":"2017","journal-title":"Mov Disord"},{"key":"R11-25-20240907","doi-asserted-by":"crossref","first-page":"783","DOI":"10.1002\/mds.24981","article-title":"Status dystonicus: Predictors of outcome and progression patterns of underlying disease","volume":"27","author":"Fasano","year":"2012","journal-title":"Mov Disord"}],"container-title":["Neurology 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