{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T19:25:27Z","timestamp":1787772327320,"version":"build-2784847793"},"reference-count":9,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","license":[{"start":{"date-parts":[[2012,7,1]],"date-time":"2012-07-01T00:00:00Z","timestamp":1341100800000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2012,7]]},"abstract":"<jats:p>Rabson-Mendenhall syndrome is a rare, autosomal recessive disorder affecting insulin receptor. This disorder is characterized by insulin-resistant diabetes mellitus, hyperinsulinemia, deficiency of subcutaneous fat, acanthosis nigrican, growth retardation, coarse and senile appearance, precocious puberty, and dental prematurity, enlarged genitalia, and pineal hyperplasia. Mutations of the insulin receptor gene affecting insulin action appear to be the basic mechanism underlying this syndrome. Herein, we present a case report on Rabson-Mendenhall syndrome in a 9-year-old girl.<\/jats:p>","DOI":"10.4103\/0970-4388.105026","type":"journal-article","created":{"date-parts":[[2012,12,21]],"date-time":"2012-12-21T04:11:33Z","timestamp":1356063093000},"page":"279-282","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":7,"title":["Rabson-Mendenhall syndrome"],"prefix":"10.4103","volume":"30","author":[{"given":"J","family":"Gupta","sequence":"first","affiliation":[{"name":"Department of Oral Medicine and Radiology, Mahatma Gandhi Postgraduate Institute of Dental Sciences, Gorimedu, Indira Nagar, Pondicherry, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jonathan M","family":"Daniel","sequence":"additional","affiliation":[{"name":"Department of Oral Medicine and Radiology, Mahatma Gandhi Postgraduate Institute of Dental Sciences, Gorimedu, Indira Nagar, Pondicherry, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"V","family":"Vasudevan","sequence":"additional","affiliation":[{"name":"Department of Oral Medicine and Radiology, Krishnadevaraya Dental College and Hospital, Bengaluru, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-20260227","first-page":"2623","article-title":"Progressive decline in insulin levels in Rabson-Mendenhall syndrome","volume":"84","author":"Longo","year":"1999","journal-title":"J Clin Endocrinol Metab"},{"key":"R2-20260227","doi-asserted-by":"crossref","first-page":"852","DOI":"10.1136\/adc.63.7.852","article-title":"Melatonin state in Mendenhall's syndrome","volume":"63","author":"Rittey","year":"1988","journal-title":"Arch Dis Child"},{"key":"R3-20260227","doi-asserted-by":"crossref","first-page":"938","DOI":"10.1056\/NEJM199109263251307","article-title":"Insulin resistance- Mechanisms, Syndromes, and Implications","volume":"325","author":"Moller","year":"1991","journal-title":"N Engl J Med"},{"key":"R4-20260227","doi-asserted-by":"crossref","first-page":"703","DOI":"10.1136\/adc.50.9.703","article-title":"Familial insulin-resistant diabetes, multiple somatic anomalies, and pineal hyperplasia","volume":"50","author":"West","year":"1975","journal-title":"Arch Dis Child"},{"key":"R5-20260227","doi-asserted-by":"crossref","first-page":"2454","DOI":"10.1007\/s00125-010-1879-5","article-title":"Multidrug therapy in a patient with Rabson-Mendenhall syndrome","volume":"53","author":"Moreira","year":"2010","journal-title":"Diabetologia"},{"key":"R6-20260227","author":"Kumar","year":"2005","journal-title":"Insulin resistance: Insulin action and its disturbance in disease"},{"key":"R8-20260227","first-page":"49","article-title":"Rabson-Mendenhall syndrome: A case report","volume":"4","author":"Alaei","year":"2010","journal-title":"Iran J Child Neurol"},{"key":"R9-20260227","doi-asserted-by":"crossref","first-page":"89","DOI":"10.1007\/s10266-009-0106-7","article-title":"Rabson-Mendenhall syndrome: Two case reports and a brief review of the literature","volume":"98","author":"Bathi","year":"2010","journal-title":"Odontology"},{"key":"R10-20260227","doi-asserted-by":"crossref","first-page":"S51","DOI":"10.1530\/EJE-07-0271","article-title":"IGF-I treatment of insulin resistance","volume":"157","author":"McDonald","year":"2007","journal-title":"Eur J Endocrinol"}],"container-title":["Journal of Indian Society of Pedodontics and Preventive Dentistry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/00005097-201230030-00020","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T18:38:56Z","timestamp":1787769536000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00005097-201230030-00020"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2012,7]]},"references-count":9,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2012]]}},"URL":"https:\/\/doi.org\/10.4103\/0970-4388.105026","relation":{},"ISSN":["0970-4388","1998-3905"],"issn-type":[{"value":"0970-4388","type":"print"},{"value":"1998-3905","type":"electronic"}],"subject":[],"published":{"date-parts":[[2012,7]]}}}