{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T20:00:05Z","timestamp":1787169605146,"version":"build-2736575974"},"reference-count":8,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2013,4]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Morquio-Brailsford syndrome is a type of mucopolysaccharidoses. It is a rare disease with features of short stature, atlantoaxial instability with risk of cord damage, odontoid hypoplasia, pectus carinatum, spine deformities, hepatomegaly, and restrictive lung disease. Neck movements during intubation are associated with the risk of quadriparesis due to cervical instability. This, along with the distortion of the airway anatomy due to deposition of mucopolysaccharides makes airway management arduous. We present our experience in management of difficult airway in a 3-year-old girl with Morquio-Brailsford syndrome posted for magnetic resonance imaging and computerized tomography scan of a suspected unstable cervical spine. As utmost sagacity during intubation is required, the child was intubated inside operation theatre in the presence of experienced anesthesiologists and then shifted to the peripheral location. Intubation was done with an endotracheal tube railroaded over a pediatric fibreoptic bronchoscope passed through the lumen of a classic laryngeal mask airway, keeping head in neutral position.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/0970-9185.111666","type":"journal-article","created":{"date-parts":[[2013,5,13]],"date-time":"2013-05-13T02:58:05Z","timestamp":1368413885000},"page":"258-261","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":6,"title":["Safe intubation in Morquio-Brailsford syndrome"],"prefix":"10.4103","volume":"29","author":[{"given":"Souvik","family":"Chaudhuri","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Arun Kumar Handigodu","family":"Duggappa","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shaji","family":"Mathew","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sandeep","family":"Venkatesh","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-27-20260210","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1136\/thorax.58.5.458","article-title":"Upper airway abnormalities and tracheal problems in Morquio\u2019s disease","volume":"58","author":"Walker","year":"2003","journal-title":"Thorax"},{"key":"R2-27-20260210","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1186\/1471-2253-10-2","article-title":"Anaesthetic considerations of adults with Morquio\u2019s syndrome: A case report","volume":"10","author":"McLaughlin","year":"2010","journal-title":"BMC Anaesthesiol"},{"key":"R3-27-20260210","first-page":"130","article-title":"General anaesthesia in an adult patient with Morquio syndrome with emphasis on airway issues","volume":"12","author":"Kadic","year":"2012","journal-title":"Bosn J Basic Med Sci"},{"key":"R4-27-20260210","doi-asserted-by":"crossref","first-page":"242","DOI":"10.1016\/S0952-8180(99)00007-0","article-title":"Anesthetic care for the child with Morquio syndrome: General versus regional anesthesia","volume":"11","author":"Tobias","year":"1999","journal-title":"J Clin Anesth"},{"key":"R5-27-20260210","first-page":"477","article-title":"Securing the airway in children with the Morquio-Brailsford syndrome","volume":"42","author":"Tzanova","year":"1993","journal-title":"Anaesthesist"},{"key":"R6-27-20260210","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1097\/00003643-200706001-00714","article-title":"Anesthetic implications of Morquio syndrome: Impossible intubation though fiberoptic endoscopy","volume":"24","author":"Mourao","year":"2007","journal-title":"Eur J Anaesthesiol"},{"key":"R7-27-20260210","doi-asserted-by":"crossref","first-page":"430","DOI":"10.1213\/00000539-199608000-00041","article-title":"The anesthetic management of patients with multiple pterygium syndrome","volume":"83","author":"Kuzma","year":"1996","journal-title":"Anesth Analg"},{"key":"R10-27-20260210","first-page":"453","article-title":"Mucopolysaccharidoses: An adventurous anaesthetic encounter","volume":"52","author":"Kurdi","year":"2008","journal-title":"Indian J Anaesth"}],"container-title":["Journal of Anaesthesiology Clinical Pharmacology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/01607275-201329020-00027","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T19:10:34Z","timestamp":1787166634000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/01607275-201329020-00027"}},"subtitle":["A challenge for the anesthesiologist"],"short-title":[],"issued":{"date-parts":[[2013,4]]},"references-count":8,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2013]]}},"URL":"https:\/\/doi.org\/10.4103\/0970-9185.111666","relation":{},"ISSN":["0970-9185"],"issn-type":[{"value":"0970-9185","type":"print"}],"subject":[],"published":{"date-parts":[[2013,4]]}}}