{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,4,1]],"date-time":"2022-04-01T08:16:16Z","timestamp":1648800976220},"reference-count":0,"publisher":"Georg Thieme Verlag KG","issue":"03","license":[{"start":{"date-parts":[[2021,8,2]],"date-time":"2021-08-02T00:00:00Z","timestamp":1627862400000},"content-version":"vor","delay-in-days":4050,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Indian Journal of Radiology and Imaging"],"published-print":{"date-parts":[[2010,7]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We report a case of a 13-year-old girl with Hallervorden-Spatz disease (HSD) or pantothenate kinase-2 associated neurodegeneration (PKAN). HSD is a rare neurodegenerative disorder, which is characterized by a rapidly progressive extrapyramidal syndrome, dementia with optic atrophy, and retinal degeneration. It is associated with accumulation of cysteine-iron complex in the globus pallidi and substantia nigra. The MRI \"eye of the tiger\" sign is the characteristic. MRI spectroscopy is also characteristic. It shows markedly decreased NAA\/Cr values in the globus pallidi and substantia nigra with increased mI\/Cr values that suggest of gliosis.<\/jats:p>","DOI":"10.4103\/0971-3026.69353","type":"journal-article","created":{"date-parts":[[2010,9,14]],"date-time":"2010-09-14T11:32:34Z","timestamp":1284463954000},"page":"188-191","source":"Crossref","is-referenced-by-count":5,"title":["Case report: MR spectroscopy in pantothenate kinase-2 associated neurodegeneration"],"prefix":"10.1055","volume":"20","author":[{"given":"Umesh C","family":"Parashari","sequence":"additional","affiliation":[{"name":"Department of Radio Diagnosis, C.S.M. Medical University, (Upgraded K.G. Medical University) Lucknow, UP, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pallavi","family":"Aga","sequence":"additional","affiliation":[{"name":"Department of Radio Diagnosis, C.S.M. Medical University, (Upgraded K.G. Medical University) Lucknow, UP, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Anit","family":"Parihar","sequence":"additional","affiliation":[{"name":"Department of Radio Diagnosis, C.S.M. Medical University, (Upgraded K.G. Medical University) Lucknow, UP, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ragini","family":"Singh","sequence":"additional","affiliation":[{"name":"Department of Radio Diagnosis, C.S.M. Medical University, (Upgraded K.G. Medical University) Lucknow, UP, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vindhya","family":"Joshi","sequence":"additional","affiliation":[{"name":"Department of Radio Diagnosis, C.S.M. Medical University, (Upgraded K.G. Medical University) Lucknow, UP, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"194","published-online":{"date-parts":[[2021,8,2]]},"container-title":["Indian Journal of Radiology and Imaging"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.4103\/0971-3026.69353.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,8,2]],"date-time":"2021-08-02T23:40:43Z","timestamp":1627947643000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.4103\/0971-3026.69353"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,7]]},"references-count":0,"journal-issue":{"issue":"03","published-online":{"date-parts":[[2021,8,2]]},"published-print":{"date-parts":[[2010,7]]}},"URL":"https:\/\/doi.org\/10.4103\/0971-3026.69353","archive":["Portico","CLOCKSS"],"relation":{},"ISSN":["0971-3026","1998-3808"],"issn-type":[{"value":"0971-3026","type":"print"},{"value":"1998-3808","type":"electronic"}],"subject":[],"published":{"date-parts":[[2010,7]]}}}