{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T19:41:47Z","timestamp":1786650107444,"version":"build-2736575974"},"reference-count":8,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"4","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2015,10]]},"abstract":"<jats:p>Primitive neuroectodermal tumors (PNET) of the kidney are rare, the diagnosis usually being made at histopathology. A young female presented with a massive right renal mass with features of hepatic dysfunction. Computed tomography scan of the abdomen revealed a large tumor of right kidney with tumor thrombus extending from inferior vena cava (IVC) to right atrium with features suggesting buddchiari syndrome (BCS). Needle biopsy of mass showed a round cell neoplasm and positive staining for neuron specific enolase and minimum inhibitory concentration-2 on immunohistochemistry. She was managed with neo-adjuvant chemotherapy, surgery and adjuvant chemotherapy. To the best of our knowledge this is the first case of renal PNET with inferior IVC tumor thrombus extending to right atrium with BCS. We suggest that renal PNET should be kept in mind as a differential diagnosis in young adults presenting with a large kidney mass extending to IVC that shows evidence of necrosis on imaging, which may be associated with BCS as in index case.<\/jats:p>","DOI":"10.4103\/0973-1482.139528","type":"journal-article","created":{"date-parts":[[2016,2,19]],"date-time":"2016-02-19T01:07:21Z","timestamp":1455844041000},"page":"1038-1038","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":3,"title":["Fulminant Buddchiari syndrome caused by renal primitive neuroectodermal tumor with inferior vena cava thrombus extending to atrium"],"prefix":"10.4103","volume":"11","author":[{"given":"Uttam K.","family":"Mete","sequence":"first","affiliation":[{"name":"Departments of Urology, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dig Vijay","family":"Singh","sequence":"additional","affiliation":[{"name":"Departments of Urology, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anish","family":"Bhattacharya","sequence":"additional","affiliation":[{"name":"Department of Nuclear Medicine, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nandita","family":"Kakkar","sequence":"additional","affiliation":[{"name":"Department of Pathology, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2016,2,15]]},"reference":[{"key":"R1-20260109","doi-asserted-by":"crossref","first-page":"364","DOI":"10.1016\/S0168-8278(02)00434-8","article-title":"Budd-Chiari syndrome: A review by an expert panel","volume":"38","author":"Janssen","year":"2003","journal-title":"J Hepatol"},{"key":"R2-20260109","doi-asserted-by":"crossref","first-page":"222","DOI":"10.1097\/MEG.0b013e328305ba06","article-title":"Fulminant Budd-Chiari syndrome caused by renal cell carcinoma with hepatic vein invasion: Report of a case","volume":"21","author":"Shih","year":"2009","journal-title":"Eur J Gastroenterol Hepatol"},{"key":"R3-20260109","doi-asserted-by":"crossref","first-page":"71","DOI":"10.1053\/ejso.1998.0603","article-title":"Surgical treatment of renal cell carcinoma associated with Budd-Chiari syndrome: Report of four cases and review of the literature","volume":"25","author":"Kume","year":"1999","journal-title":"Eur J Surg Oncol"},{"key":"R4-20260109","doi-asserted-by":"crossref","first-page":"320","DOI":"10.1097\/00000478-200203000-00005","article-title":"Primary Ewing's sarcoma\/primitive neuroectodermal tumor of the kidney: A clinicopathologic and immunohistochemical analysis of 11 cases","volume":"26","author":"Jimenez","year":"2002","journal-title":"Am J Surg Pathol"},{"key":"R5-20260109","first-page":"654","article-title":"Inferior vena cava thrombus in renal primitive neuroectodermal tumor is not rare","volume":"102","author":"Xu","year":"2010","journal-title":"J Natl Med Assoc"},{"key":"R6-20260109","doi-asserted-by":"crossref","first-page":"1486","DOI":"10.1016\/S0022-5347(05)64481-3","article-title":"Primitive neuroectodermal tumor of the kidney with inferior vena cava and atrial tumor thrombus","volume":"168","author":"Thomas","year":"2002","journal-title":"J Urol"},{"key":"R7-20260109","doi-asserted-by":"crossref","first-page":"427.e13-6","DOI":"10.1016\/j.urology.2006.02.032","article-title":"Renal primitive neuroectodermal tumor in childhood with intracardiac extension","volume":"68","author":"Sellaturay","year":"2006","journal-title":"Urology"},{"key":"R8-20260109","doi-asserted-by":"crossref","first-page":"3","DOI":"10.1186\/1471-2407-4-3","article-title":"Primitive Neuroectodermal Tumor (PNET) of the kidney: A case report","volume":"4","author":"Pomara","year":"2004","journal-title":"BMC Cancer"}],"container-title":["Journal of Cancer Research and Therapeutics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/01363817-201511040-00153","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T19:02:43Z","timestamp":1786647763000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/01363817-201511040-00153"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,10]]},"references-count":8,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2015]]}},"URL":"https:\/\/doi.org\/10.4103\/0973-1482.139528","relation":{},"ISSN":["0973-1482","1998-4138"],"issn-type":[{"value":"0973-1482","type":"print"},{"value":"1998-4138","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015,10]]}}}