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We report the clinical course, imaging, and postmortem findings of a 38-year-old female with HPS-related progressive pulmonary fibrosis, highlighting the role of imaging in assessment of disease severity and prognosis.<\/jats:p>","DOI":"10.4103\/2156-7514.143437","type":"journal-article","created":{"date-parts":[[2014,10,27]],"date-time":"2014-10-27T05:45:26Z","timestamp":1414388726000},"page":"59","update-policy":"https:\/\/doi.org\/10.25259\/crossmark_policy","source":"Crossref","is-referenced-by-count":11,"title":["Hermansky-Pudlak Syndrome Complicated by Pulmonary Fibrosis: Radiologic-Pathologic Correlation and Review of Pulmonary Complications"],"prefix":"10.25259","volume":"4","author":[{"given":"Tatiana","family":"Kelil","sequence":"first","affiliation":[{"name":"Department of Imaging, Brigham and Women's Hospital, Boston, MA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jeanne","family":"Shen","sequence":"additional","affiliation":[{"name":"Department of Pathology, Brigham and Women's Hospital, Boston, MA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ailbhe C","family":"O\u2019Neill","sequence":"additional","affiliation":[{"name":"Department of Imaging, Dana Farber Cancer Institute, Boston, MA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Stephanie A","family":"Howard","sequence":"additional","affiliation":[{"name":"Department of Imaging, Brigham and Women's Hospital, Boston, MA, USA"},{"name":"Department of Imaging, Dana Farber Cancer Institute, Boston, MA, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"10894","published-online":{"date-parts":[[2014,10,27]]},"reference":[{"key":"10.4103\/2156-7514.143437\/ref-1","doi-asserted-by":"crossref","first-page":"737","DOI":"10.1016\/0002-9343(79)91111-2","article-title":"Hermansky-Pudlak syndrome. 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This joint statement of the American Thoracic Society (ATS), and the European Respiratory Society (ERS) was adopted by the ATS board of directors, June 2001 and by the ERS Executive Committee, June 2001","volume":"165","author":"American Thoracic Society; European Respiratory Society","year":"2002","journal-title":"Am J Respir Crit Care Med"}],"container-title":["Journal of Clinical Imaging Science"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/clinicalimagingscience.org\/hermansky-pudlak-syndrome-complicated-by-pulmonary-fibrosis-radiologic-pathologic-correlation-and-review-of-pulmonary-complications\/","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/clinicalimagingscience.org\/hermansky-pudlak-syndrome-complicated-by-pulmonary-fibrosis-radiologic-pathologic-correlation-and-review-of-pulmonary-complications\/","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,8,30]],"date-time":"2019-08-30T01:14:10Z","timestamp":1567127650000},"score":1,"resource":{"primary":{"URL":"https:\/\/clinicalimagingscience.org\/hermansky-pudlak-syndrome-complicated-by-pulmonary-fibrosis-radiologic-pathologic-correlation-and-review-of-pulmonary-complications\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2014,10,27]]},"references-count":10,"alternative-id":["10.4103\/2156-7514.143437"],"URL":"https:\/\/doi.org\/10.4103\/2156-7514.143437","relation":{},"ISSN":["2156-7514"],"issn-type":[{"value":"2156-7514","type":"electronic"}],"subject":[],"published":{"date-parts":[[2014,10,27]]},"article-number":"59"}}