{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T19:26:52Z","timestamp":1787772412131,"version":"build-2784847793"},"reference-count":9,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"1","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2023,1]]},"abstract":"<jats:sec>\n                    <jats:title>ABSTRACT<\/jats:title>\n                    <jats:p>Williams-Beuren syndrome is a rare genetic malformation with predilection for supravalvular aortic stenosis. Apart from cardiovascular malformation, hypocalcemia, developmental delay, and elfin facies, challenging airway make perioperative management more eventful. Association of infective endocarditis within the aortic arch and pseudoaneurysm formation is infrequent. We, hereby report a case of pseudoaneurysm formation and infective vegetation within the aortic arch in a patient with Williams syndrome and the role of transthoracic echocardiography in its perioperative management.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/aca.aca_122_21","type":"journal-article","created":{"date-parts":[[2024,5,28]],"date-time":"2024-05-28T05:52:05Z","timestamp":1716875525000},"page":"94-96","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":2,"title":["Williams-Beuren Syndrome with Pseudoaneurysm of Aortic Arch and Infective Vegetations for Modified Broms Procedure"],"prefix":"10.4103","volume":"26","author":[{"given":"Devishree","family":"Das","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Neeti","family":"Makhija","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-17-20240901","doi-asserted-by":"crossref","first-page":"874","DOI":"10.1016\/j.amjcard.2009.10.069","article-title":"Long-term outcomes of patients with cardiovascular abnormalities and Williams syndrome","volume":"105","author":"Collins","year":"2010","journal-title":"Am J Cardiol"},{"key":"R2-17-20240901","doi-asserted-by":"crossref","first-page":"239","DOI":"10.1056\/NEJMra0903074","article-title":"Williams-Beuren syndrome","volume":"362","author":"Pober","year":"2010","journal-title":"N Engl J Med"},{"key":"R3-17-20240901","first-page":"279","article-title":"Cardiovascular spectrum in Williams-Beuren syndrome: The Mexican experience in 40 patients","volume":"35","author":"De Rubens Figueroa","year":"2008","journal-title":"Tex Heart Inst J"},{"key":"R4-17-20240901","doi-asserted-by":"crossref","first-page":"554","DOI":"10.1136\/jmg.39.8.554","article-title":"Cardiovascular manifestations in 75 patients with Williams syndrome","volume":"39","author":"Eronen","year":"2002","journal-title":"J Med Genet"},{"key":"R5-17-20240901","first-page":"904","article-title":"[Cardiovascular manifestations in 40 patients with Williams syndrome]","volume":"35","author":"Xie","year":"2007","journal-title":"Zhonghua Xin Xue Guan Bing Za Zhi"},{"key":"R6-17-20240901","first-page":"25","article-title":"[Intractable infective endocarditis associated with supraaortic stenosis in Williams syndrome: A case report]","volume":"40","author":"Maruyoshi","year":"2002","journal-title":"J Cardiol"},{"key":"R7-17-20240901","doi-asserted-by":"crossref","first-page":"142","DOI":"10.3904\/kjim.1988.3.2.142","article-title":"Infective endocarditis in a patient with Williams\u2019 syndrome--case report","volume":"3","author":"Koh","year":"1988","journal-title":"Korean J Intern Med"},{"key":"R8-17-20240901","first-page":"292","article-title":"Supravalvular aortic stenosis associated to infectious endocarditis and cerebral vascular disease in a patient with Williams-Beuren Syndrome","volume":"85","author":"De Rubens Figueroa","year":"2015","journal-title":"Arch Cardiol Mex"},{"key":"R9-17-20240901","doi-asserted-by":"crossref","first-page":"50","DOI":"10.1016\/S1010-7940(01)01087-9","article-title":"Surgical repair of congenital supravalvular aortic stenosis in children","volume":"21","author":"Brown","year":"2002","journal-title":"Eur J Cardiothorac Surg"}],"container-title":["Annals of Cardiac Anaesthesia"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/aca.aca_122_21","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T18:45:11Z","timestamp":1787769911000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/aca.aca_122_21"}},"subtitle":["Anesthetic Concerns &amp; Echocardiographic Illustrations"],"short-title":[],"issued":{"date-parts":[[2023,1]]},"references-count":9,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2023]]}},"URL":"https:\/\/doi.org\/10.4103\/aca.aca_122_21","relation":{},"ISSN":["0971-9784"],"issn-type":[{"value":"0971-9784","type":"print"}],"subject":[],"published":{"date-parts":[[2023,1]]}}}