{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T19:31:49Z","timestamp":1787772709459,"version":"build-2784847793"},"reference-count":6,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2021,4]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Congenital factor VII (FVII) deficiency is a rare bleeding disorder (RBD) with phenotypes ranging from asymptomatic state to life threatening bleeding episodes. There is no established recommendation for the perioperative management of patients scheduled for cardiac surgery. We have described the perioperative management of a patient with FVII deficiency treated for aortic valve stenosis, coronary artery disease, and atrial fibrillation. Balancing perioperative bleeding risk and risks of thrombotic events thereafter in such patients is difficult and requires a multidisciplinary approach.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/aca.aca_181_20","type":"journal-article","created":{"date-parts":[[2021,4,19]],"date-time":"2021-04-19T11:23:44Z","timestamp":1618831424000},"page":"244-246","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":2,"title":["Aortic Valve and Coronary Artery Bypass Surgery in a Patient with Factor VII Deficiency"],"prefix":"10.4103","volume":"24","author":[{"given":"Larissa","family":"Henze","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christian","family":"Junghanss","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alper","family":"\u00d6ner","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pascal M.","family":"Dohmen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anthony","family":"Alozie","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-22-20240901","doi-asserted-by":"crossref","first-page":"2052","DOI":"10.1182\/blood-2014-08-532820","article-title":"Rare bleeding disorders: Diagnosis and treatment","volume":"125","author":"Palla","year":"2015","journal-title":"Blood"},{"key":"R2-22-20240901","doi-asserted-by":"crossref","first-page":"703","DOI":"10.1177\/1076029616670257","article-title":"Factor VII deficiency: From Basics to clinical laboratory diagnosis and patient management","volume":"23","author":"Sevenet","year":"2017","journal-title":"Clin Appl Thromb Hemost"},{"key":"R3-22-20240901","doi-asserted-by":"crossref","first-page":"38","DOI":"10.3390\/jcm6040038","article-title":"Factor VII deficiency: Clinical phenotype, genotype and therapy","volume":"6","author":"Napolitano","year":"2017","journal-title":"J Clin Med"},{"key":"R4-22-20240901","doi-asserted-by":"crossref","first-page":"563","DOI":"10.1111\/bjh.15055","article-title":"Role of clinical and laboratory parameters for treatment choice in patients with inherited FVII deficiency undergoing surgical procedures: Evidence from the STER registry","volume":"180","author":"Di Minno","year":"2017","journal-title":"Br J Haematol"},{"key":"R5-22-20240901","doi-asserted-by":"crossref","first-page":"277","DOI":"10.1002\/ccr3.836","article-title":"Thrombosis in a bleeding disorder: Case of thromboembolism in factor VII deficiency","volume":"5","author":"Ramdass","year":"2017","journal-title":"Clin Case Rep"},{"key":"R6-22-20240901","doi-asserted-by":"crossref","first-page":"812","DOI":"10.1111\/hae.12702","article-title":"Long-term prophylaxis in severe factor VII deficiency","volume":"21","author":"Siboni","year":"2015","journal-title":"Haemophilia"}],"container-title":["Annals of Cardiac Anaesthesia"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/aca.ACA_181_20","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T19:09:54Z","timestamp":1787771394000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/aca.ACA_181_20"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,4]]},"references-count":6,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2021]]}},"URL":"https:\/\/doi.org\/10.4103\/aca.aca_181_20","relation":{},"ISSN":["0971-9784"],"issn-type":[{"value":"0971-9784","type":"print"}],"subject":[],"published":{"date-parts":[[2021,4]]}}}