{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T20:02:16Z","timestamp":1787169736370,"version":"build-2736575974"},"reference-count":11,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2021,7]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are no previous reports of absent right superior vena cava (SVC) in children with Holt-Oram syndrome. We present images of a case where the diagnosis of absent right SVC with persistent left SVC was made with intraoperative transesophageal echocardiography and discuss the anesthetic and perfusion implications of such findings.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/aca.aca_198_20","type":"journal-article","created":{"date-parts":[[2023,3,31]],"date-time":"2023-03-31T06:11:56Z","timestamp":1680243116000},"page":"358-361","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome"],"prefix":"10.4103","volume":"24","author":[{"given":"Satyajeet","family":"Misra","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Satyapriya","family":"Mohanty","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Siddhartha","family":"Sathia","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rudra Pratap","family":"Mahapatra","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Priyank","family":"Tapuria","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-14-20240901","doi-asserted-by":"crossref","first-page":"885","DOI":"10.1056\/NEJM199403313301302","article-title":"The clinical and genetic spectrum of the Holt-Oram syndrome (heart-hand 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vena cava: A case report and its clinical implications","volume":"20","author":"Bisoyi","year":"2017","journal-title":"Ann Card Anaesth"},{"key":"R7-14-20240901","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1016\/j.athoracsur.2006.02.062","article-title":"Surgical approach to left ventricular inflow obstruction due to dilated coronary sinus","volume":"82","author":"Vargas","year":"2006","journal-title":"Ann Thorac Surg"},{"key":"R8-14-20240901","doi-asserted-by":"crossref","first-page":"729","DOI":"10.1053\/j.jvca.2015.07.008","article-title":"Modified deep transgastric bicaval view for revealing superior vena caval obstruction in a patient undergoing sinus venosus atrial septal defect repair: A case report","volume":"30","author":"Aggarwal","year":"2016","journal-title":"J Cardiothorac Vasc Anesth"},{"key":"R9-14-20240901","doi-asserted-by":"crossref","first-page":"336","DOI":"10.1053\/j.jvca.2007.05.004","article-title":"An unusual case of looping of the central venous catheter: Who is the culprit?","volume":"22","author":"Misra","year":"2008","journal-title":"J Cardiothorac Vasc Anesth"},{"key":"R10-14-20240901","doi-asserted-by":"crossref","first-page":"110","DOI":"10.4103\/0971-9784.197849","article-title":"Holt-Oram syndrome: Anesthetic challenges and safe outcome","volume":"20","author":"Rana","year":"2017","journal-title":"Ann Card Anaesth"},{"key":"R11-14-20240901","doi-asserted-by":"crossref","first-page":"1326","DOI":"10.1053\/j.jvca.2013.03.017","article-title":"Malignant hyperthermia-like manifestations in a two-month-old child with Holt-Oram syndrome undergoing cardiac surgery","volume":"28","author":"Franklin","year":"2014","journal-title":"J Cardiothorac Vasc Anesth"},{"key":"R12-14-20240901","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1177\/021849230601400218","article-title":"Holt-oram syndrome with hemiazygous continuation of inferior vena cava","volume":"14","author":"Varma","year":"2006","journal-title":"Asian Cardiovasc Thorac Ann"}],"container-title":["Annals of Cardiac Anaesthesia"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/aca.ACA_198_20","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T19:12:41Z","timestamp":1787166761000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/aca.ACA_198_20"}},"subtitle":["Anesthetic and perfusion implications"],"short-title":[],"issued":{"date-parts":[[2021,7]]},"references-count":11,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2021]]}},"URL":"https:\/\/doi.org\/10.4103\/aca.aca_198_20","relation":{},"ISSN":["0971-9784"],"issn-type":[{"value":"0971-9784","type":"print"}],"subject":[],"published":{"date-parts":[[2021,7]]}}}