{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,14]],"date-time":"2026-08-14T16:43:04Z","timestamp":1786725784500,"version":"build-2736575974"},"reference-count":10,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"5","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2023,9]]},"DOI":"10.4103\/aian.aian_697_23","type":"journal-article","created":{"date-parts":[[2023,10,11]],"date-time":"2023-10-11T15:32:24Z","timestamp":1697038344000},"page":"795-798","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":4,"title":["Longitudinally Extensive Transverse Myelitis with Optic Neuritis Related to Profound Biotinidase Deficiency: NMOSD Mimic!"],"prefix":"10.4103","volume":"26","author":[{"given":"Nagaraj Angadi","family":"Ravikumar","sequence":"first","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Debjyoti","family":"Dhar","sequence":"additional","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rohan","family":"Mahale","sequence":"additional","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ambati Mounika","family":"Reddy","sequence":"additional","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Athyadi U.","family":"Shreedevi","sequence":"additional","affiliation":[{"name":"Department of Psychiatry Social Work, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sameetha","family":"Prabhu","sequence":"additional","affiliation":[{"name":"Department of Pediatric Neurology, Aster Women and Children Hospital, Whitefield, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jitender","family":"Saini","sequence":"additional","affiliation":[{"name":"Department of Neuroimaging and Intervention Radiology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rita","family":"Christopher","sequence":"additional","affiliation":[{"name":"Department of Neurochemistry, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pooja","family":"Mailankody","sequence":"additional","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mathuranath","family":"PS","sequence":"additional","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hansashree","family":"Padmanabha","sequence":"additional","affiliation":[{"name":"Department of Neurology, National Institute of Mental Health and Neurosciences, Bengaluru, Karnataka, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2023,10,5]]},"reference":[{"key":"R1-20260512","first-page":"127","article-title":"Biotinidase deficiency: Prevalence, impact and management strategies","volume":"11","author":"Canda","year":"2020","journal-title":"Pediatr Health Med Ther"},{"key":"R2-20260512","doi-asserted-by":"crossref","first-page":"e120498","DOI":"10.5812\/ijp-120498","article-title":"A girl with myelopathy and vision loss, misdiagnosis as NMOSD: The first Iranian case: Report on biotinidase deficiency","volume":"32","author":"Nasehi","year":"2022","journal-title":"Iran J Pediatr"},{"key":"R3-20260512","doi-asserted-by":"crossref","first-page":"119","DOI":"10.1177\/1352458516646087","article-title":"Biotinidase deficiency mimicking neuromyelitis optica beginning at the age of 4: A treatable disease","volume":"23","author":"Girard","year":"2017","journal-title":"Mult Scler"},{"key":"R4-20260512","doi-asserted-by":"crossref","first-page":"1604","DOI":"10.1177\/1352458515596457","article-title":"Biotinidase deficiency mimicking neuromyelitis optica: Initially exhibiting symptoms in adulthood","volume":"21","author":"Bottin","year":"2015","journal-title":"Mult Scler"},{"key":"R5-20260512","doi-asserted-by":"crossref","first-page":"541","DOI":"10.4103\/aian.AIAN_4_19","article-title":"Subacute myelopathy: Think beyond neuromyelitis optica spectrum disorder","volume":"22","author":"Kasinathan","year":"2019","journal-title":"Ann Indian Acad Neurol"},{"key":"R6-20260512","doi-asserted-by":"crossref","first-page":"113","DOI":"10.1016\/j.ymgme.2015.08.012","article-title":"Biotinidase deficiency should be considered in individuals exhibiting myelopathy with or without and vision loss","volume":"116","author":"Wolf","year":"2015","journal-title":"Mol Genet Metab"},{"key":"R7-20260512","doi-asserted-by":"crossref","first-page":"102280","DOI":"10.1016\/j.msard.2020.102280","article-title":"Biotinidase deficiency in differential diagnosis of neuromyelitis optica spectrum disorder","volume":"44","author":"Bilge","year":"2020","journal-title":"Mult Scler Relat Disord"},{"key":"R8-20260512","doi-asserted-by":"crossref","first-page":"762","DOI":"10.1016\/j.braindev.2020.07.007","article-title":"Biotinidase deficiency presenting as Neuromyelitis Optica Spectrum Disorder","volume":"42","author":"Shah","year":"2020","journal-title":"Brain Dev"},{"key":"R9-20260512","doi-asserted-by":"crossref","first-page":"675","DOI":"10.1007\/s11011-017-9984-5","article-title":"A treatable cause of myelopathy and vision loss mimicking neuromyelitis optica spectrum disorder: Late-onset biotinidase deficiency","volume":"32","author":"Yilmaz","year":"2017","journal-title":"Metab Brain Dis"},{"key":"R10-20260512","doi-asserted-by":"crossref","first-page":"118","DOI":"10.1001\/jamaneurol.2020.3558","article-title":"Biotinidase deficiency as a mimic of neuromyelitis optica spectrum disorder in childhood","volume":"78","author":"Santoro","year":"2020","journal-title":"JAMA Neurol"}],"container-title":["Annals of Indian Academy of Neurology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/aian.aian_697_23","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,14]],"date-time":"2026-08-14T16:25:35Z","timestamp":1786724735000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/aian.aian_697_23"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,9]]},"references-count":10,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2023]]}},"URL":"https:\/\/doi.org\/10.4103\/aian.aian_697_23","relation":{},"ISSN":["0972-2327","1998-3549"],"issn-type":[{"value":"0972-2327","type":"print"},{"value":"1998-3549","type":"electronic"}],"subject":[],"published":{"date-parts":[[2023,9]]},"assertion":[{"value":"2023-08-06","name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2023-08-25","name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}}]}}