{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,14]],"date-time":"2026-08-14T20:31:51Z","timestamp":1786739511207,"version":"build-2736575974"},"reference-count":7,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2021,7]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Ovotesticular disorder represents 10% of cases of disorder of sex development characterized by the presence of both ovarian and testicular tissue in the same individual, with karyotype 46 XY being a rare sex chromosomal abnormality. We report the case of a 16-year-old person, who is reared as female, with a complaint of primary amenorrhea along with lack of secondary sexual characteristics, karyotype 46 XY. Prophylactic bilateral gonadectomy was done, and histopathological examination of bilateral gonads revealed ovarian stroma with a few Sertoli cell line tubules suggestive of bilateral ovotestis; hence, we concluded and framed our diagnosis of ovotesticular disorder.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/gmit.gmit_107_19","type":"journal-article","created":{"date-parts":[[2021,8,3]],"date-time":"2021-08-03T00:46:44Z","timestamp":1627951604000},"page":"171-173","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":7,"title":["46 XY Ovotesticular Disorder"],"prefix":"10.4103","volume":"10","author":[{"given":"Bhati","family":"Meenal","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gothwal","family":"Meenakshi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Singh","family":"Pratibha","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yadav","family":"Garima","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kathuria","family":"Priyanka","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Elhence","family":"Poonam","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-8-20240830","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1016\/j.eucr.2015.12.003","article-title":"Prophylactic bilateral gonadectomy for ovotesticular disorder of sex development in a patient with mosaic 45, X\/46, X, idic(Y)q11.222 karyotype","volume":"5","author":"Becker","year":"2016","journal-title":"Urol Case Rep"},{"key":"R2-8-20240830","doi-asserted-by":"crossref","first-page":"1532","DOI":"10.1016\/j.juro.2013.10.037","article-title":"Long-term followup of a large cohort of patients with ovotesticular disorder of sex development","volume":"191","author":"Sircili","year":"2014","journal-title":"J Urol"},{"key":"R3-8-20240830","doi-asserted-by":"crossref","first-page":"899","DOI":"10.1515\/jpem-2017-0039","article-title":"45, X\/46, XY ovotesticular disorder of sex development revisited: Undifferentiated gonadal tissue may be mistaken as ovarian tissue","volume":"30","author":"Andrade","year":"2017","journal-title":"J Pediatr Endocrinol Metab"},{"key":"R4-8-20240830","doi-asserted-by":"crossref","first-page":"S268","DOI":"10.4103\/2230-8210.119601","article-title":"A rare case report of 46 XY mixed gonadal dysgenesis","volume":"17","author":"Arora","year":"2013","journal-title":"Indian J Endocrinol Metab"},{"key":"R5-8-20240830","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1111\/and.12048","article-title":"Ovotesticular disorder of sexual development due to 47, XYY\/46, XY\/45, X mixed gonadal dysgenesis in a phenotypic male presenting as cyclical haematuria: Clinical presentation and assessment of long-term outcomes","volume":"46","author":"Dutta","year":"2014","journal-title":"Andrologia"},{"key":"R6-8-20240830","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1007\/BF02000779","article-title":"True hermaphroditism: Geographical distribution, clinical findings, chromosomes and gonadal histology","volume":"153","author":"Krob","year":"1994","journal-title":"Eur J Pediatr"},{"key":"R7-8-20240830","doi-asserted-by":"crossref","first-page":"1178","DOI":"10.1016\/j.urology.2011.02.036","article-title":"Ovotesticular disorder of sex development with mosaic 45, X\/46, X, idic(Y) (q11.23) karyotype and streak gonad","volume":"78","author":"Tran","year":"2011","journal-title":"Urology"}],"container-title":["Gynecology and Minimally Invasive Therapy"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/GMIT.GMIT_107_19","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,14]],"date-time":"2026-08-14T19:29:34Z","timestamp":1786735774000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/GMIT.GMIT_107_19"}},"subtitle":["A Rare Case Report with Review of Literature"],"short-title":[],"issued":{"date-parts":[[2021,7]]},"references-count":7,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2021]]}},"URL":"https:\/\/doi.org\/10.4103\/gmit.gmit_107_19","relation":{},"ISSN":["2213-3070"],"issn-type":[{"value":"2213-3070","type":"print"}],"subject":[],"published":{"date-parts":[[2021,7]]}}}