{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T19:26:54Z","timestamp":1787772414650,"version":"build-2784847793"},"reference-count":12,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"5","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2021,9]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Olmsted syndrome is a rare genodermatosis. Palmoplantar keratoderma and periorificial keratodermic plaques are the most important clinical findings. Additional findings associated with a large number of systems may accompany such as teeth, nail deformities, alopecia, mental retardation, and bone\u2013joint anomalies. Therefore, it is difficult to make a differential diagnosis from other palmoplantar keratodermas. It also needs to be differentiated from acrodermatitis enteropathica because of periorificial plaques. The absence of regression in lesions with zinc treatment excludes this disease. We present here an Olmsted syndrome case with essential thrombocytosis for the first time.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/ijd.ijd_595_20","type":"journal-article","created":{"date-parts":[[2024,5,29]],"date-time":"2024-05-29T12:21:23Z","timestamp":1716985283000},"page":"574","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["Case of Olmsted Syndrome with Essential Thrombocytosis Misdiagnosed as Acrodermatitis Enteropathica"],"prefix":"10.4103","volume":"66","author":[{"given":"Filiz Topalo\u011flu","family":"Demir","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ceyda","family":"\u00c7aytemel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nazl\u0131","family":"Caf","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Zafer","family":"T\u00fcrko\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mesut","family":"Ayer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nesimi","family":"B\u00fcy\u00fckbabani","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-34-20240829","doi-asserted-by":"crossref","first-page":"757","DOI":"10.1001\/archpedi.1927.04130170055008","article-title":"Keratodermia palmaris et plantaris 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mutations","volume":"156","author":"Greco","year":"2020","journal-title":"JAMA Dermatol"},{"key":"R12-34-20240829","doi-asserted-by":"crossref","first-page":"196","DOI":"10.1001\/jamadermatol.2019.4141","article-title":"Targeted inhibition of the epidermal growth factor receptor and mammalian target of rapamycin signaling pathways in Olmsted syndrome","volume":"156","author":"Zhang","year":"2020","journal-title":"JAMA Dermatol"}],"container-title":["Indian Journal of 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