{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,4,4]],"date-time":"2024-04-04T00:30:12Z","timestamp":1712190612329},"reference-count":19,"publisher":"Scientific Scholar","issue":"5","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Indian J Nephrol"],"published-print":{"date-parts":[[2021]]},"DOI":"10.4103\/ijn.ijn_271_20","type":"journal-article","created":{"date-parts":[[2021,4,1]],"date-time":"2021-04-01T10:53:23Z","timestamp":1617274403000},"page":"478","source":"Crossref","is-referenced-by-count":0,"title":["Uncommon presentation of atypical hemolytic uremic syndrome: A Case Report"],"prefix":"10.25259","volume":"31","author":[{"given":"SandraM","family":"Martin","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alejandro","family":"Balestracci","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Iris","family":"Puyol","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ismael","family":"Toledo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gabriel","family":"Cao","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gema","family":"Arizeta","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"10894","reference":[{"key":"key-10.4103\/0971-4065.313019-1","doi-asserted-by":"crossref","first-page":"421","DOI":"10.1016\/j.nefro.2015.07.005","article-title":"An update for atypical haemolytic uraemic syndrome: Diagnosis and treatment.A consensus document","author":"Campistol","year":"2015","journal-title":"Nefrologia"},{"key":"key-10.4103\/0971-4065.313019-2","doi-asserted-by":"crossref","first-page":"408","DOI":"10.1016\/j.kint.2018.02.029","article-title":"Clinical and genetic predictors of atypical hemolytic uremic syndrome phenotype and outcome","author":"Schaefer","year":"2018","journal-title":"Kidney Int"},{"key":"key-10.4103\/0971-4065.313019-3","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1007\/s00467-015-3076-8","article-title":"An international consensus approach to the management of atypical hemolytic uremic syndrome in children","author":"Loirat","year":"2016","journal-title":"Pediatr Nephrol"},{"key":"key-10.4103\/0971-4065.313019-4","doi-asserted-by":"crossref","first-page":"539","DOI":"10.1016\/j.kint.2016.10.005","article-title":"Atypical hemolytic uremic syndrome and C3 glomerulopathy: Conclusions from a \u201cKidney disease: Improving global outcomes\u201d (KDIGO) controversies conference","author":"Goodship","year":"2017","journal-title":"Kidney Int"},{"key":"key-10.4103\/0971-4065.313019-5","doi-asserted-by":"crossref","first-page":"1088","DOI":"10.1007\/s10157-018-1549-3","article-title":"Clinical characteristics and genetic backgrounds of Japanese patients with atypical hemolytic uremic s\u00edndrome","author":"Fujisawa","year":"2018","journal-title":"Clin Exp Nephrol"},{"key":"key-10.4103\/0971-4065.313019-6","doi-asserted-by":"crossref","first-page":"418","DOI":"10.4274\/Tjh-2013.0226","article-title":"Hepatitis B vaccine-associated atypical hemolytic uremic syndrome","author":"Avc\u0131","year":"2013","journal-title":"Turk J Haematol"},{"key":"key-10.4103\/0971-4065.313019-7","doi-asserted-by":"crossref","first-page":"2009","DOI":"10.1007\/s00467-017-3783-4","article-title":"Influenza-associated thrombotic microangiopathies","author":"Bitzan","year":"2018","journal-title":"Pediatr Nephrol"},{"key":"key-10.4103\/0971-4065.313019-8","doi-asserted-by":"crossref","first-page":"347","DOI":"10.1007\/BF00857534","article-title":"Nephrotic syndrome in the 1st year of life","author":"Habib","year":"1993","journal-title":"Pediatr Nephrol"},{"key":"key-10.4103\/0971-4065.313019-9","doi-asserted-by":"crossref","first-page":"149","DOI":"10.1007\/s12519-016-0009-y","article-title":"The etiology of congenital nephrotic syndrome: Current status and challenges","author":"Wang","year":"2016","journal-title":"World J Pediatr"},{"key":"key-10.4103\/0971-4065.313019-10","doi-asserted-by":"crossref","first-page":"245","DOI":"10.1038\/nrneph.2014.250","article-title":"Podocyte dysfunction in atypical haemolytic uremic syndrome","author":"Noris","year":"2015","journal-title":"Nat Rev Nephrol"},{"key":"key-10.4103\/0971-4065.313019-11","doi-asserted-by":"crossref","first-page":"377","DOI":"10.1681\/ASN.2012090903","article-title":"DGKE variants cause a glomerular microangiopathy that mimics membranoproliferative GN","author":"Ozaltin","year":"2013","journal-title":"J Am Soc Nephrol"},{"key":"key-10.4103\/0971-4065.313019-12","doi-asserted-by":"crossref","first-page":"531","DOI":"10.1038\/ng.2590","article-title":"Recessive mutations in DGKE cause atypical hemolytic-uremic syndrome","author":"Lemaire","year":"2013","journal-title":"Nat Genet"},{"key":"key-10.4103\/0971-4065.313019-13","doi-asserted-by":"crossref","first-page":"345","DOI":"10.1056\/NEJMoa0810739","article-title":"Thrombomodulin mutations in atypical hemolytic-uremic syndrome","author":"Delvaeye","year":"2009","journal-title":"N Engl J Med"},{"key":"key-10.4103\/0971-4065.313019-14","doi-asserted-by":"crossref","first-page":"120","DOI":"10.1159\/000449423","article-title":"Nephrotic-range proteinuria and peripheral edema in a child: Not only idiopathic nephrotic syndrome","author":"Dolcemascolo","year":"2016","journal-title":"Case Rep Nephrol Dial"},{"key":"key-10.4103\/0971-4065.313019-15","unstructured":"Noris M, Bresin E, Mele C, Remuzzi G. Genetic Atypical Hemolytic-Uremic Syndrome. 2007; Nov 16 [Last updated on 2016 Jun 09]. In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, et al. editors. GeneReviews\u00ae [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2020. Available from: https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK1367."},{"key":"key-10.4103\/0971-4065.313019-16","doi-asserted-by":"crossref","first-page":"1363","DOI":"10.1007\/s00467-008-0803-4","article-title":"Efficacy of plasma therapy in atypical hemolytic uremic syndrome with complement factor H mutations","author":"Lapeyraque","year":"2008","journal-title":"Pediatr Nephrol"},{"key":"key-10.4103\/0971-4065.313019-17","doi-asserted-by":"crossref","first-page":"415","DOI":"10.1053\/j.ajkd.2004.10.018","article-title":"Successful plasma therapy for atypical hemolytic uremic syndrome caused by factor H deficiency owing to a novel mutation in the complement cofactor protein domain 15","author":"Licht","year":"2005","journal-title":"Am J Kidney Dis"},{"key":"key-10.4103\/0971-4065.313019-18","doi-asserted-by":"crossref","first-page":"1957","DOI":"10.1007\/s00467-008-0872-4","article-title":"Complement and the atypical hemolytic uremic syndrome in children","author":"Loirat","year":"2008","journal-title":"Pediatr Nephrol"},{"key":"key-10.4103\/0971-4065.313019-19","doi-asserted-by":"crossref","first-page":"2169","DOI":"10.1056\/NEJMoa1208981","article-title":"Terminal complement inhibitor eculizumab in atypical hemolytic uremic syndrome","author":"Legendre","year":"2013","journal-title":"N Engl J Med"}],"container-title":["Indian Journal of Nephrology"],"original-title":[],"language":"en","deposited":{"date-parts":[[2024,4,3]],"date-time":"2024-04-03T19:46:24Z","timestamp":1712173584000},"score":1,"resource":{"primary":{"URL":"https:\/\/indianjnephrol.org\/uncommon-presentation-of-atypical-hemolytic-uremic-syndrome-a-case-report\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021]]},"references-count":19,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2021]]}},"alternative-id":["313019"],"URL":"https:\/\/doi.org\/10.4103\/ijn.ijn_271_20","relation":{},"ISSN":["0971-4065"],"issn-type":[{"value":"0971-4065","type":"print"}],"subject":[],"published":{"date-parts":[[2021]]}}}