{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T16:21:18Z","timestamp":1787761278718,"version":"build-2784847793"},"reference-count":15,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"9","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2017,9]]},"abstract":"<jats:p>Dermatofibrosarcoma protuberans is a soft tissue sarcoma that is dermal in origin. The incidence is &lt;0.1% of all malignancies and 1% of soft tissue sarcoma. Most commonly, it involves trunk (62%) followed by extremities (25%) and head and neck (13%). It is a slow growing tumor with locally aggressive behavior. Here, a 50-year-old female diagnosed with orbital dermatofibrosarcoma developed extra-axial component in right frontal region even on chemotherapy. Hence, the bad prognostic factors are yet to be established in dermatofibrosarcoma protuberans.<\/jats:p>","DOI":"10.4103\/ijo.ijo_770_16","type":"journal-article","created":{"date-parts":[[2017,9,18]],"date-time":"2017-09-18T23:17:01Z","timestamp":1505776621000},"page":"892-894","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":3,"title":["Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature"],"prefix":"10.4103","volume":"65","author":[{"given":"Deepti","family":"Sharma","sequence":"first","affiliation":[{"name":"Department of Radiation Oncology, Safdarjung Hospital, New Delhi, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Garima","family":"Singh","sequence":"additional","affiliation":[{"name":"Department of Radiation Oncology, Safdarjung Hospital, New Delhi, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Neha","family":"Kakkar","sequence":"additional","affiliation":[{"name":"Department of Radiation Oncology, Safdarjung Hospital, New Delhi, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vidya","family":"Jha","sequence":"additional","affiliation":[{"name":"Department of Radiation Oncology, Safdarjung Hospital, New Delhi, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-20251013","first-page":"447","article-title":"Surgical treatment of dermatofibrosarcoma protuberans. 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