{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,26]],"date-time":"2026-09-26T17:54:25Z","timestamp":1790445265802,"version":"4.1.0"},"reference-count":18,"publisher":"Georg Thieme Verlag KG","issue":"02","license":[{"start":{"date-parts":[[2021,7,19]],"date-time":"2021-07-19T00:00:00Z","timestamp":1626652800000},"content-version":"vor","delay-in-days":474,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Indian Journal of Radiology and Imaging"],"published-print":{"date-parts":[[2020,4]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac malformation characterized by absent, dysplastic, or rudimentary pulmonary valve leaflets in association with other cardiac anomalies. It has an incidence of 3-6% in cases of tetralogy of Fallot (TOF) and 0.2-0.4% of live-born infants with congenital heart disease (CHD). Absent pulmonary valve leads to dilated main pulmonary artery; presenting as a pulsatile, paracardiac cystic lesion on antenatal ultrasound (USG). We report a case of this rare anomaly in association with ventricular septal defect (VSD), TOF, and left axis deviation of heart detected at 23 weeks of gestation.<\/jats:p>","DOI":"10.4103\/ijri.ijri_508_19","type":"journal-article","created":{"date-parts":[[2020,7,16]],"date-time":"2020-07-16T07:09:20Z","timestamp":1594883360000},"page":"240-243","source":"Crossref","is-referenced-by-count":4,"title":["Fallot type of absent pulmonary valve syndrome - A case report"],"prefix":"10.1055","volume":"30","author":[{"given":"Divya B","family":"Desai","sequence":"additional","affiliation":[{"name":"Department of Radiodiagnosis, D Y Patil Hospital and Research Center, Sector-5, Nerul, Navi Mumbai, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Neeti P","family":"Mathur","sequence":"additional","affiliation":[{"name":"Department of Radiodiagnosis, D Y Patil Hospital and Research Center, Sector-5, Nerul, Navi Mumbai, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Arnab","family":"Marik","sequence":"additional","affiliation":[{"name":"Department of Radiodiagnosis, D Y Patil Hospital and Research Center, Sector-5, Nerul, Navi Mumbai, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"194","published-online":{"date-parts":[[2021,7,19]]},"reference":[{"key":"ref1","first-page":"488","article-title":"Raaetraaecissement congenital de l\u201d orifice pulmonaire","volume":"15","author":"N Cheevers","year":"1847","journal-title":"Arch Med Fourth Ser"},{"key":"ref2","doi-asserted-by":"crossref","first-page":"136","DOI":"10.1016\/0003-4975(96)00276-7","article-title":"Absent pulmonary valve syndrome: Surgical treatment and considerations","volume":"62","author":"F Godart","year":"1996","journal-title":"Ann Thorac Surg [Internet]"},{"key":"ref3","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1016\/j.ihj.2012.10.010","article-title":"Absent pulmonary valve syndrome with tetralogy of Fallot detected at an early gestational age of 27 weeks-A case report","volume":"65","author":"A N Bhupali","year":"2013","journal-title":"Indian Heart J"},{"key":"ref4","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1161\/01.CIR.57.1.159","article-title":"The absent pulmonary valve syndrome. 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