{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T19:32:15Z","timestamp":1786649535832,"version":"build-2736575974"},"reference-count":10,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","license":[{"start":{"date-parts":[[2025,4,1]],"date-time":"2025-04-01T00:00:00Z","timestamp":1743465600000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2025,4]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n                  <jats:p>Idiopathic scoliosis (IS) is frequently associated with Chiari malformation (CM) and syringomyelia, conditions thought to share a common underlying cause: Atlantoaxial instability. Atlantoaxial stabilization has recently emerged as a novel treatment option. A 4-year-old girl presented with progressive scoliosis (Cobb angle of 28.6\u00b0), neck pain, CM, and syringomyelia. The patient was diagnosed with central or axial atlantoaxial instability and underwent C1-C2 fixation. Postoperatively, she experienced significant relief from neck pain. Follow-ups demonstrated progressive syrinx reduction, while X-rays revealed a Cobb angle decrease to 21\u00b0 in 18 months. This case highlights the potential of atlantoaxial stabilization to halt scoliosis progression in IS patients with CM and syringomyelia. Unlike traditional multisegmental stabilization, C1-C2 fixation offers a minimally invasive approach and preserves spinal mobility in growth-age patients. Atlantoaxial instability should be considered in IS cases with CM and syringomyelia. Atlantoaxial stabilization alone may provide effective treatment with favorable clinical and radiological outcomes.<\/jats:p>","DOI":"10.4103\/jcvjs.jcvjs_43_25","type":"journal-article","created":{"date-parts":[[2025,7,3]],"date-time":"2025-07-03T14:00:16Z","timestamp":1751551216000},"page":"250-253","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["The effect of atlantoaxial stabilization on juvenile idiopathic scoliosis involving Chiari malformation and syrinx"],"prefix":"10.4103","volume":"16","author":[{"given":"Sen Harun","family":"Emre","sequence":"first","affiliation":[{"name":"Department of Neurosurgery, School of Medicine, Okan University, Istanbul, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Simsek","family":"Serkan","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, School of Medicine, Ankara Medipol University, Ankara, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kaptanoglu","family":"Erkan","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, School of Medicine, Okan University, Istanbul, Turkey"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2025,7,3]]},"reference":[{"key":"R1-20250707","doi-asserted-by":"crossref","first-page":"1261","DOI":"10.1016\/j.spinee.2018.02.013","article-title":"Prevalence and risk factors for neural axis anomalies in idiopathic scoliosis:A systematic review","volume":"18","author":"Heemskerk","year":"2018","journal-title":"Spine J"},{"key":"R2-20250707","doi-asserted-by":"crossref","first-page":"703","DOI":"10.31616\/asj.2022.0077","article-title":"Concurrent presence of thoracolumbar scoliosis and chiari malformation:Is operative risk magnified?","volume":"17","author":"Naessig","year":"2023","journal-title":"Asian Spine J"},{"key":"R3-20250707","doi-asserted-by":"crossref","first-page":"1853","DOI":"10.1007\/s00381-019-04309-7","article-title":"Scoliosis in patients with Chiari malformation type I","volume":"35","author":"Noureldine","year":"2019","journal-title":"Childs Nerv Syst"},{"key":"R4-20250707","doi-asserted-by":"crossref","first-page":"22","DOI":"10.3171\/2010.9.PEDS10383","article-title":"Editorial. Chiari malformation type I and scoliosis:The complexity of curves","volume":"7","author":"Brockmeyer","year":"2011","journal-title":"J Neurosurg Pediatr"},{"key":"R5-20250707","doi-asserted-by":"crossref","first-page":"1105","DOI":"10.1007\/s43390-021-00286-7","article-title":"Scoliosis with Chiari I malformation without associated syringomyelia","volume":"9","author":"O'Neill","year":"2021","journal-title":"Spine Deform"},{"key":"R6-20250707","doi-asserted-by":"crossref","first-page":"702","DOI":"10.1016\/j.wneu.2017.02.063","article-title":"Role of atlantoaxial and subaxial spinal \u0131nstability in pathogenesis of spinal \u201cDegeneration\u201d-related cervical kyphosis","volume":"101","author":"Goel","year":"2017","journal-title":"World Neurosurg"},{"key":"R7-20250707","doi-asserted-by":"crossref","first-page":"e937","DOI":"10.1016\/j.wneu.2019.01.212","article-title":"Spinal kyphoscoliosis associated with chiari formation and syringomyelia 'Recovery'following atlantoaxial fixation:A preliminary report and early results based on experience with 11 surgically treated cases","volume":"125","author":"Goel","year":"2019","journal-title":"World Neurosurg"},{"key":"R8-20250707","doi-asserted-by":"crossref","first-page":"e921","DOI":"10.1016\/j.wneu.2020.06.076","article-title":"Chiari 1 formation redefined-clinical and radiographic observations in 388 surgically treated patients","volume":"141","author":"Goel","year":"2020","journal-title":"World Neurosurg"},{"key":"R9-20250707","doi-asserted-by":"crossref","first-page":"e1017","DOI":"10.1016\/j.wneu.2023.04.064","article-title":"C1-2 fusion in atlantoaxial dislocation and basilar \u0131nvagination with and without chiari malformation:Clinical\/radiological and craniometric results","volume":"175","author":"Zhu","year":"2023","journal-title":"World Neurosurg"},{"key":"R10-20250707","doi-asserted-by":"crossref","first-page":"39","DOI":"10.1016\/j.wneu.2020.07.223","article-title":"Atlantoaxial \u0131nstability as a cause of craniovertebral and cervical spinal alterations and dorsal kyphoscoliosis","volume":"144","author":"Goel","year":"2020","journal-title":"World Neurosurg"}],"container-title":["Journal of Craniovertebral Junction and Spine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/jcvjs.jcvjs_43_25","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T18:55:09Z","timestamp":1786647309000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/jcvjs.jcvjs_43_25"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,4]]},"references-count":10,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2025]]}},"URL":"https:\/\/doi.org\/10.4103\/jcvjs.jcvjs_43_25","relation":{},"ISSN":["0974-8237","0976-9285"],"issn-type":[{"value":"0974-8237","type":"print"},{"value":"0976-9285","type":"electronic"}],"subject":[],"published":{"date-parts":[[2025,4]]},"assertion":[{"value":"2025-02-27","name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2025-03-18","name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}}]}}