{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T19:35:06Z","timestamp":1786649706355,"version":"build-2736575974"},"reference-count":13,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","license":[{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2026,3]]},"abstract":"<jats:title>\n                    A\n                    <jats:sc>BSTRACT<\/jats:sc>\n                  <\/jats:title>\n                  <jats:p>Scimitar syndrome is a rare anomaly where there is an occurrence of partial or complete abnormality of venous drainage of the right pulmonary vein into the inferior vena cava. Here we present a 34-year-old female patient complaining of dyspnea on exertion and dry cough, after undergoing extensive imaging and hemodynamic testing, was found to have a syndrome identified with lung hypoplasia with moderate pulmonary arterial hypertension (PAH). This case emphasizes how crucial it is to rule out Scimitar syndrome in adults as one of the causes of PAH from imaging and sonography. The initial presentation will be breathlessness where every physician keeps an insight of performing cardiac evaluation that may finally end up with these rare diagnosis.<\/jats:p>","DOI":"10.4103\/jfmpc.jfmpc_1659_24","type":"journal-article","created":{"date-parts":[[2026,4,20]],"date-time":"2026-04-20T10:00:55Z","timestamp":1776679255000},"page":"1445-1447","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["A rare etiology of pulmonary hypertension: The scimitar syndrome"],"prefix":"10.4103","volume":"15","author":[{"given":"Lokesh","family":"Devalla","sequence":"first","affiliation":[{"name":"Department of Respiratory Medicine, Datta Meghe Medical College (DMMC), DMIHER, Nagpur, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pankaj B.","family":"Wagh","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Jawaharlal Nehru Medical College (JNMC), DMIHER, Sawangi Meghe, Wardha, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Babaji","family":"Ghewade","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Jawaharlal Nehru Medical College (JNMC), DMIHER, Sawangi Meghe, Wardha, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2026,4,20]]},"reference":[{"key":"R1-20260424","doi-asserted-by":"crossref","first-page":"502","DOI":"10.1016\/0002-9149(92)91198-D","article-title":"The \u201cadult\u201cform of the scimitar syndrome","volume":"15","author":"Dupuis","year":"1992","journal-title":"Am J Cardiol"},{"key":"R2-20260424","first-page":"1","article-title":"The familial occurrence of the hypoplastic right lung with systemic arterial supply and venous drainage\u201cscimitar syndrome\u201c","volume":"107","author":"Neill","year":"1960","journal-title":"Bull Johns Hopkins Hosp"},{"key":"R3-20260424","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1148\/radiographics.14.2.8190958","article-title":"Congenital pulmonary venolobar syndrome revisited","volume":"14","author":"Woodring","year":"1994","journal-title":"Radiographics"},{"key":"R4-20260424","doi-asserted-by":"crossref","first-page":"434","DOI":"10.1161\/CIRCULATIONAHA.109.931857","article-title":"Images in cardiovascular medicine. Scimitar syndrome:Added value by isotropic flow-sensitive four-dimensional magnetic resonance imaging with PC VIPR (phase-contrast vastly undersampled isotropic projection reconstruction)","volume":"121","author":"Frydrychowicz","year":"2010","journal-title":"Circulation"},{"key":"R5-20260424","first-page":"789","article-title":"Scimitar syndrome in adulthood","volume":"52","author":"Sellak","year":"2020","journal-title":"Atenci\u00f3n Primaria"},{"key":"R6-20260424","first-page":"1","article-title":"Treatment and prognosis of scimitar syndrome:A retrospective analysis in a single center of East China","volume":"9","author":"Wang","year":"2022","journal-title":"Front Cardiovasc Med"},{"key":"R7-20260424","doi-asserted-by":"crossref","first-page":"3770","DOI":"10.1111\/jocs.15857","article-title":"Surgical management of the scimitar syndrome","volume":"36","author":"Chowdhury","year":"2021","journal-title":"J Card Surg"},{"key":"R8-20260424","doi-asserted-by":"crossref","first-page":"1858","DOI":"10.1161\/01.CIR.99.14.1858","article-title":"Long-term prostacyclin for pulmonary hypertension with associated congenital heart defects","volume":"99","author":"Rosenzweig","year":"1999","journal-title":"Circulation"},{"key":"R9-20260424","first-page":"957","article-title":"Partial anomalous pulmonary venous connection:A rare cause of pulmonary hypertension","volume":"154","author":"Venkateswara","year":"2018","journal-title":"Chest"},{"key":"R10-20260424","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1016\/j.acvd.2022.01.004","article-title":"Multifactorial pulmonary hypertension in infantile scimitar syndrome","volume":"115","author":"Bonnet","year":"2022","journal-title":"Arch Cardiovasc Dis"},{"key":"R11-20260424","doi-asserted-by":"crossref","first-page":"592","DOI":"10.1016\/j.athoracsur.2017.06.061","article-title":"Scimitar syndrome in children and adults:Natural history, outcomes, and risk analysis","volume":"105","author":"Wang","year":"2018","journal-title":"Ann Thorac Surg"},{"key":"R12-20260424","first-page":"129","article-title":"Total pulmonary artery atresia associated with abnormal pulmonary venous drainage as a rare presentation of scimitar syndrome","volume":"5","author":"Javadrashid","year":"2013","journal-title":"J Cardiovasc Thorac Res"},{"key":"R13-20260424","first-page":"1","article-title":"Scimitar syndrome with absent right pulmonary artery and severe pulmonary hypertension treated with coil occlusion of aortopulmonary collaterals in a term neonate","volume":"25","author":"Parappil","year":"2015","journal-title":"BMJ Case Rep"}],"container-title":["Journal of Family Medicine and Primary Care"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/jfmpc.jfmpc_1659_24","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T18:57:25Z","timestamp":1786647445000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/jfmpc.jfmpc_1659_24"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,3]]},"references-count":13,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2026]]}},"URL":"https:\/\/doi.org\/10.4103\/jfmpc.jfmpc_1659_24","relation":{},"ISSN":["2249-4863","2278-7135"],"issn-type":[{"value":"2249-4863","type":"print"},{"value":"2278-7135","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,3]]},"assertion":[{"value":"2024-09-30","name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2025-10-01","name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}}]}}