{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,14]],"date-time":"2026-08-14T17:31:33Z","timestamp":1786728693342,"version":"build-2736575974"},"reference-count":8,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"5","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2023,9]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Primary sarcoma of the ovary is extremely rare. There are inadequate data in the literature regarding ovarian sarcoma in the pediatric age group. We report a case of an 8-year-old girl presenting with large abdominal mass and cachexia. Raised alpha-fetoprotein levels suggested germ cell tumor. Tru-cut biopsy histopathological report suggested a spindle cell tumor. The IHC staining suggested non rhabdomyosarcoma. As tumour was large and ovarian pediatric non rhabdomyosarcoma was not reported in the literature, we started on rhabdomyosarcoma neoadjuant regimen. Good response was noted for neoadjuvant chemotherapy, which was followed by complete surgical excision of the tumor and radiotherapy. At present, the overall outcome of the disease is dismal. Increased available data and gaining more evidence may help in improvising the treatment option.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/jiaps.jiaps_15_23","type":"journal-article","created":{"date-parts":[[2023,9,5]],"date-time":"2023-09-05T03:02:31Z","timestamp":1693882951000},"page":"436-438","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["Ovarian Sarcoma a Diagnostic Dilemma\u2013 A Case Report"],"prefix":"10.4103","volume":"28","author":[{"given":"Prashant K","family":"Zulpi","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Akshay B","family":"Kalavant","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anil B","family":"Halgeri","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"P","family":"Priyanka","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-15-20240905","doi-asserted-by":"crossref","first-page":"593","DOI":"10.1007\/s00383-007-2075-7","article-title":"Primary ovarian rhabdomyosarcoma in children","volume":"24","author":"Cribbs","year":"2008","journal-title":"Pediatr Surg Int"},{"key":"R2-15-20240905","doi-asserted-by":"crossref","first-page":"113","DOI":"10.1097\/00004347-199804000-00003","article-title":"Primary ovarian rhabdomyosarcoma: A report of 13 cases","volume":"17","author":"Nielsen","year":"1998","journal-title":"Int J Gynecol Pathol"},{"key":"R3-15-20240905","doi-asserted-by":"crossref","first-page":"917","DOI":"10.1016\/j.humpath.2015.02.008","article-title":"Ovarian embryonal rhabdomyosarcoma is a rare manifestation of the DICER1 syndrome","volume":"46","author":"de Kock","year":"2015","journal-title":"Hum Pathol"},{"key":"R4-15-20240905","doi-asserted-by":"crossref","first-page":"325","DOI":"10.1016\/0090-8258(83)90050-1","article-title":"Rhabdomyosarcoma of the ovary: Ultrastructural study of a case and review of literature","volume":"15","author":"Gu\u00e9rard","year":"1983","journal-title":"Gynecol Oncol"},{"key":"R5-15-20240905","doi-asserted-by":"crossref","first-page":"165","DOI":"10.4103\/0971-9261.154664","article-title":"Non-rhabdomyosarcoma soft-tissue sarcomas in children: Contemporary appraisal and experience from a single centre","volume":"20","author":"Qureshi","year":"2015","journal-title":"J Indian Assoc Pediatr Surg"},{"key":"R6-15-20240905","doi-asserted-by":"crossref","first-page":"S61","DOI":"10.1016\/S0893-3952(22)04459-3","article-title":"Germ cell tumors of the gonads: A selective review emphasizing problems in differential diagnosis, newly appreciated, and controversial issues","volume":"18","author":"Ulbright","year":"2005","journal-title":"Mod Pathol"},{"key":"R7-15-20240905","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1186\/1752-1947-6-13","article-title":"Ovarian germ cell tumors with rhabdomyosarcomatous components and later development of growing teratoma syndrome: A case report","volume":"6","author":"Al-Jumaily","year":"2012","journal-title":"J Med Case Rep"},{"key":"R9-15-20240905","doi-asserted-by":"crossref","first-page":"134","DOI":"10.4103\/IJPM.IJPM_548_16","article-title":"Primary rhabdomyosarcoma in ovary \u2013 Pathologist clinches it all","volume":"61","author":"Vanidassane","year":"2018","journal-title":"Indian J Pathol Microbiol"}],"container-title":["Journal of Indian Association of Pediatric Surgeons"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/jiaps.jiaps_15_23","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,14]],"date-time":"2026-08-14T16:30:36Z","timestamp":1786725036000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/jiaps.jiaps_15_23"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,9]]},"references-count":8,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2023]]}},"URL":"https:\/\/doi.org\/10.4103\/jiaps.jiaps_15_23","relation":{},"ISSN":["0971-9261"],"issn-type":[{"value":"0971-9261","type":"print"}],"subject":[],"published":{"date-parts":[[2023,9]]}}}