{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T19:27:21Z","timestamp":1787772441186,"version":"build-2784847793"},"reference-count":13,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2022,3]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>We report an infant reared as a girl who presented with ambiguous genitalia and urine coming per rectum. On examination, she had minimal clitoromegaly with labial fusion and Y urethral duplication. On investigations, genetic, metabolic, and endocrine causes for disorder of sexual differentiation were ruled out. This girl was operated via a posterior sagittal approach. This case was unique in that the urogenital sinus was deviated posteriorly and opened in the anterior rectal wall and the accessory urethra opened in clitoris, along with ambiguity of external genitalia, thus making it a rare variant of the posterior cloaca. The diagnosis requires a high index of suspicion in clinician and a meticulous examination of the external genitalia. Very little literature is available for this rare anomaly. Few reports have classified them as female pseudohermaphroditism with cloacal and urogenital sinus defects. Hence, we hereby discuss and review the literature for previously reported cases.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/jiaps.jiaps_352_20","type":"journal-article","created":{"date-parts":[[2024,5,24]],"date-time":"2024-05-24T10:16:51Z","timestamp":1716545811000},"page":"251-254","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["An Unusual Case of Type A Posterior Cloaca Associated with 46XX Disorder of Sexual Differentiation with Y Duplication of Urethra"],"prefix":"10.4103","volume":"27","author":[{"given":"Rahul K.","family":"Gupta","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pooja","family":"Tiwari","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sandesh V.","family":"Parelkar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Beejal V.","family":"Sanghvi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kedar P.","family":"Mudkhedkar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Satej S.","family":"Mhaskar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rujuta S.","family":"Shah","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-24-20240905","doi-asserted-by":"crossref","first-page":"1186","DOI":"10.1016\/S0022-5347(17)51747-4","article-title":"Female phallic urethra and persistent cloaca","volume":"130","author":"Sotolongo","year":"1983","journal-title":"J Urol"},{"key":"R2-24-20240905","doi-asserted-by":"crossref","first-page":"149","DOI":"10.1136\/bmj.1.4959.149","article-title":"A form of intersexuality","volume":"1","author":"Broster","year":"1956","journal-title":"Br Med J"},{"key":"R3-24-20240905","doi-asserted-by":"crossref","first-page":"407","DOI":"10.1016\/S0022-3468(98)90079-3","article-title":"Posterior cloaca: A unique defect","volume":"33","author":"Pe\u00f1a","year":"1998","journal-title":"J Pediatr Surg"},{"key":"R5-24-20240905","doi-asserted-by":"crossref","first-page":"1056","DOI":"10.1016\/S0022-5347(17)38987-5","article-title":"Persistent cloaca and phallic urethra","volume":"142","author":"Karlin","year":"1989","journal-title":"J Urol"},{"key":"R6-24-20240905","doi-asserted-by":"crossref","first-page":"890","DOI":"10.1016\/0022-3468(92)90393-L","article-title":"Cloacal malformations: Experience with 105 cases","volume":"27","author":"Hendren","year":"1992","journal-title":"J Pediatr Surg"},{"key":"R7-24-20240905","doi-asserted-by":"crossref","first-page":"444","DOI":"10.1007\/BF01686033","article-title":"Clitoromegaly, duplex urethra and dysplastic vagina. 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Report of six cases and embryological analysis","volume":"141","author":"Escobar","year":"1987","journal-title":"Am J Dis Child"},{"key":"R11-24-20240905","doi-asserted-by":"crossref","first-page":"37","DOI":"10.1002\/ajmg.1320250607","article-title":"An association of caudal malformations arising from a defect in the \u201caxial mesoderm\u201d developmental field","volume":"2","author":"Gardner","year":"1986","journal-title":"Am J Med Genet Suppl"},{"key":"R12-24-20240905","doi-asserted-by":"crossref","first-page":"1159","DOI":"10.1016\/S0022-5347(17)54280-9","article-title":"Accessory phallic urethra in the female patient","volume":"127","author":"Bellinger","year":"1982","journal-title":"J Urol"},{"key":"R13-24-20240905","doi-asserted-by":"crossref","first-page":"680","DOI":"10.1016\/j.urology.2010.12.044","article-title":"Newborn with persistent cloaca presenting with accessory phallic urethra and ambiguous genitalia","volume":"78","author":"Braga","year":"2011","journal-title":"Urology"},{"key":"R14-24-20240905","doi-asserted-by":"crossref","first-page":"131","DOI":"10.1111\/j.1464-410X.2005.05581.x","article-title":"Upper and lower urinary tract outcome after surgical repair of cloacal malformations: A three-decade experience","volume":"96","author":"Rink","year":"2005","journal-title":"BJU Int"}],"container-title":["Journal of Indian Association of Pediatric Surgeons"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/jiaps.JIAPS_352_20","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T18:46:57Z","timestamp":1787770017000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/jiaps.JIAPS_352_20"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,3]]},"references-count":13,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2022]]}},"URL":"https:\/\/doi.org\/10.4103\/jiaps.jiaps_352_20","relation":{},"ISSN":["0971-9261"],"issn-type":[{"value":"0971-9261","type":"print"}],"subject":[],"published":{"date-parts":[[2022,3]]}}}