{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T19:36:45Z","timestamp":1786649805201,"version":"build-2736575974"},"reference-count":9,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"4","license":[{"start":{"date-parts":[[2025,4,18]],"date-time":"2025-04-18T00:00:00Z","timestamp":1744934400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2025,7]]},"abstract":"<jats:title>\n                    A\n                    <jats:sc>BSTRACT<\/jats:sc>\n                  <\/jats:title>\n                  <jats:p>Lipofibromatosis is a rare and benign soft-tissue tumor predominantly affecting children. It commonly presents as a slow-growing, painless mass, often misdiagnosed due to its rarity and variable presentation. We report the unusual case of an 8-month-old male with a congenital upper thoracic mass initially suspected to be a lipomyelomeningocele. Clinical examination and ultrasound supported this diagnosis, but magnetic resonance imaging findings suggested a soft-tissue tumor. The child underwent excisional biopsy, and intraoperative findings revealed a highly vascular, well-defined mass without spinal cord involvement. Histopathological analysis confirmed lipofibromatosis. The postoperative course was uneventful, and no recurrence was observed after 1 year of follow-up. This case highlights the diagnostic challenges associated with lipofibromatosis and its potential for misdiagnosis, and the importance of histopathology in establishing a definitive diagnosis. Early complete surgical excision remains the preferred treatment to prevent recurrence.<\/jats:p>","DOI":"10.4103\/jiaps.jiaps_3_25","type":"journal-article","created":{"date-parts":[[2025,4,18]],"date-time":"2025-04-18T07:00:30Z","timestamp":1744959630000},"page":"532-534","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["Giant Lipofibromatosis Over Back Mimicking Thoracic Lipomyelomeningocele in Paediatric Age Group: Case Report and Review of Literature"],"prefix":"10.4103","volume":"30","author":[{"given":"Keerthana","family":"Bachala","sequence":"first","affiliation":[{"name":"Department of Paediatric Surgery, AIIMS, Patna, Bihar, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Amit Kumar","family":"Sinha","sequence":"additional","affiliation":[{"name":"Department of Paediatric Surgery, AIIMS, Patna, Bihar, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Amit","family":"Kumar","sequence":"additional","affiliation":[{"name":"Department of Paediatric Surgery, AIIMS, Patna, Bihar, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shreyas","family":"Dudhani","sequence":"additional","affiliation":[{"name":"Department of Paediatric Surgery, AIIMS, Patna, Bihar, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gaurav","family":"Shandilya","sequence":"additional","affiliation":[{"name":"Department of Paediatric Surgery, AIIMS, Patna, Bihar, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2025,4,18]]},"reference":[{"key":"R1-20250704","doi-asserted-by":"crossref","first-page":"633","DOI":"10.1007\/s00256-014-1827-4","article-title":"Lipofibromatosis: Magnetic resonance imaging features and pathological correlation in three 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Zhi"},{"key":"R5-20250704","doi-asserted-by":"crossref","first-page":"423","DOI":"10.1038\/s41379-018-0150-3","article-title":"Aberrant receptor tyrosine kinase signaling in lipofibromatosis: A clinicopathological and molecular genetic study of 20 cases","volume":"32","author":"Al-Ibraheemi","year":"2019","journal-title":"Mod Pathol"},{"key":"R6-20250704","doi-asserted-by":"crossref","first-page":"298","DOI":"10.1111\/pde.12335","article-title":"Lipofibromatosis: An institutional and literature review of an uncommon entity","volume":"31","author":"Boos","year":"2014","journal-title":"Pediatr Dermatol"},{"key":"R7-20250704","first-page":"133","article-title":"Lipofibromatosis: A clinicopathological study of six cases","volume":"25","author":"Luo","year":"2018","journal-title":"Chin J Diagn Pathol"},{"key":"R8-20250704","doi-asserted-by":"crossref","first-page":"703","DOI":"10.1097\/SAP.0b013e3181a13df6","article-title":"Diffuse lipofibromatosis of the lower extremity masquerading as a vascular anomaly","volume":"62","author":"Greene","year":"2009","journal-title":"Ann Plast Surg"},{"issue":"Suppl 1","key":"R9-20250704","doi-asserted-by":"crossref","first-page":"S43","DOI":"10.1007\/s00247-010-1850-0","article-title":"Imaging characteristics of lipofibromatosis presenting as a shoulder mass in a 16-month-old girl","volume":"40","author":"Walton","year":"2010","journal-title":"Pediatr Radiol"}],"container-title":["Journal of Indian Association of Pediatric Surgeons"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/jiaps.jiaps_3_25","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,13]],"date-time":"2026-08-13T18:58:37Z","timestamp":1786647517000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/jiaps.jiaps_3_25"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,4,18]]},"references-count":9,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2025]]}},"URL":"https:\/\/doi.org\/10.4103\/jiaps.jiaps_3_25","relation":{},"ISSN":["0971-9261","1998-3891"],"issn-type":[{"value":"0971-9261","type":"print"},{"value":"1998-3891","type":"electronic"}],"subject":[],"published":{"date-parts":[[2025,4,18]]},"assertion":[{"value":"2025-01-07","name":"received","label":"Received","group":{"name":"publication_history","label":"Publication 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