{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T20:27:56Z","timestamp":1787776076736,"version":"build-2784847793"},"reference-count":14,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","license":[{"start":{"date-parts":[[2024,4,1]],"date-time":"2024-04-01T00:00:00Z","timestamp":1711929600000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2024,4]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Purpose:<\/jats:title>\n                    <jats:p>To report the atypical case of a patient with mucopolysaccharidosis type II (MPS II) in whom bilateral pigmented paravenous chorioretinal atrophy (PPRCA) was found.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods:<\/jats:title>\n                    <jats:p>An observational case report.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results:<\/jats:title>\n                    <jats:p>We present the case of a 31-year-old male patient who presented with decreased visual acuity and in whom fundus examination and multimodal imaging revealed a typical appearance of bilateral symmetrical PPRCA. Our patient also had thick facies with hypertelorism and stubby hands, which prompted an enzyme assay revealing MPS II.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusions:<\/jats:title>\n                    <jats:p>PPRCA is an uncommon condition with an uncertain origin that continues to be a subject of debate. Our case represents an unusual association that points to a potential genetic origin; however, further studies are needed to understand this condition.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/joco.joco_259_23","type":"journal-article","created":{"date-parts":[[2025,1,20]],"date-time":"2025-01-20T04:00:41Z","timestamp":1737345641000},"page":"201-204","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":2,"title":["Pigmented Paravenous Chorioretinal Atrophy and Mucopolysaccharidosis: A Case Report"],"prefix":"10.4103","volume":"36","author":[{"given":"Zineb","family":"Algouti","sequence":"first","affiliation":[{"name":"Department of Ophthalmology, Avicenna Military Hospital, Faculty of Medicine and Pharmacy, Caddi Ayyad University, Marrakech, Morocco"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Houda","family":"Bezza","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology, Avicenna Military Hospital, Faculty of Medicine and Pharmacy, Caddi Ayyad University, Marrakech, Morocco"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mohamed","family":"Kriet","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology, Avicenna Military Hospital, Faculty of Medicine and Pharmacy, Caddi Ayyad University, Marrakech, Morocco"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fouad","family":"El asri","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology, Avicenna Military Hospital, Faculty of Medicine and Pharmacy, Caddi Ayyad University, Marrakech, Morocco"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2025,1,18]]},"reference":[{"key":"R1-20250122","doi-asserted-by":"crossref","first-page":"645","DOI":"10.1136\/bjo.21.12.645","article-title":"Retino-choroiditis 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