{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,23]],"date-time":"2026-08-23T18:34:30Z","timestamp":1787510070791,"version":"build-2736575974"},"reference-count":19,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"1","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2023,1]]},"abstract":"<jats:sec>\n                    <jats:title\/>\n                    <jats:p>Biliary atresia (BA) is a rare disease characterised by biliary obstruction of unknown origin that presents in the neonatal period. It is classified into syndromic with various congenital anomalies and non-syndromic (isolated anomaly). We present a case of syndromic BA associated with polysplenia and intestinal malrotation, discovered incidentally during the Kasai procedure. The small intestine was found to be non-rotated with the duodenojejunal junction to the right of the vertebral column. The presence of accessory spleens was noted. Kasai portoenterostomy and Ladd\u2019s procedure were performed. The patient had an uneventful postoperative course with the passage of cholic stool from the third postoperative day. At the seventh-month follow-up, the stool remained cholic. A multidisciplinary approach in the care of babies with BA and long-term follow-up is crucial for a successful outcome.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/jwas.jwas_195_22","type":"journal-article","created":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T06:41:45Z","timestamp":1694760105000},"page":"106-110","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":6,"title":["Biliary Atresia Splenic Malformation"],"prefix":"10.4103","volume":"13","author":[{"given":"Olumide A.","family":"Elebute","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Manuella Talla","family":"Timo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Felix M.","family":"Alakaloko","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Justina O.","family":"Seyi-Olajide","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christopher O.","family":"Bode","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Adesoji O.","family":"Ademuyiwa","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-19-20240907","doi-asserted-by":"crossref","first-page":"FSO466","DOI":"10.2144\/fsoa-2019-0153","article-title":"Biliary atresia: Pathology, etiology and pathogenesis","volume":"6","author":"Vij","year":"2020","journal-title":"Future Sci OA"},{"key":"R2-19-20240907","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1186\/1750-1172-1-28","article-title":"Biliary atresia","volume":"1","author":"Chardot","year":"2006","journal-title":"Orphanet J Rare Dis"},{"key":"R3-19-20240907","doi-asserted-by":"crossref","first-page":"5675","DOI":"10.3390\/jcm10235675","article-title":"Biliary atresia: Clinical phenotypes and aetiological heterogeneity","volume":"10","author":"Davenport","year":"2021","journal-title":"J Clin Med"},{"key":"R4-19-20240907","doi-asserted-by":"crossref","first-page":"10","DOI":"10.4103\/0971-9261.158095","article-title":"A study of associated congenital anomalies with biliary atresia","volume":"21","author":"Gupta","year":"2016","journal-title":"J Indian Assoc Pediatr Surg"},{"key":"R5-19-20240907","first-page":"662","article-title":"Biliary atresia splenic malformation syndrome: An etiologic and prognostic subgroup","volume":"113","author":"Davenport","year":"1993","journal-title":"Surgery"},{"key":"R6-19-20240907","doi-asserted-by":"crossref","first-page":"342","DOI":"10.1038\/nrgastro.2015.74","article-title":"Pathogenesis of biliary atresia: Defining biology to understand clinical phenotypes","volume":"12","author":"Asai","year":"2015","journal-title":"Nat Rev Gastroenterol Hepatol"},{"key":"R7-19-20240907","first-page":"3","article-title":"Biliary atresia: An easily missed cause of jaundice amongst children in Uganda","volume":"21","author":"Kakembo","year":"2016","journal-title":"East Cent Afr J Surg"},{"key":"R8-19-20240907","doi-asserted-by":"crossref","first-page":"200","DOI":"10.1080\/02724936.1987.11748507","article-title":"Biliary atresia in Zaria, Nigeria: A review","volume":"7","author":"Mabogunje","year":"1987","journal-title":"Ann Trop Paediatr"},{"key":"R9-19-20240907","doi-asserted-by":"crossref","first-page":"69","DOI":"10.1179\/146532807X170538","article-title":"Management of biliary atresia in Nigeria: The ongoing challenge","volume":"27","author":"Mshelbwala","year":"2007","journal-title":"Ann Trop Paediatr"},{"key":"R10-19-20240907","doi-asserted-by":"crossref","first-page":"4","DOI":"10.4103\/1117-6806.111495","article-title":"Pattern and survival of biliary atresia patients; experience in Southern Nigeria","volume":"19","author":"Okoro","year":"2013","journal-title":"Niger J Surg"},{"key":"R11-19-20240907","first-page":"683","article-title":"Biliary atresia: Experience of a nord African center","volume":"93","author":"Kerkeni","year":"2015","journal-title":"Tunis Med"},{"key":"R12-19-20240907","first-page":"14","article-title":"Biliary atresia associated with polysplenia syndrome, situs inversus abdominus, and reverse rotation of intestine","volume":"3","author":"Mirza","year":"2012","journal-title":"APSP J Case Rep"},{"key":"R13-19-20240907","doi-asserted-by":"crossref","first-page":"1724","DOI":"10.1002\/hep.26512","article-title":"Extrahepatic anomalies in infants with biliary atresia: Results of a large prospective North American Multicenter Study","volume":"58","author":"Schwarz","year":"2013","journal-title":"Hepatology"},{"key":"R14-19-20240907","doi-asserted-by":"crossref","first-page":"393","DOI":"10.1016\/j.jpeds.2006.05.030","article-title":"The biliary atresia splenic malformation syndrome: A 28-year single-center retrospective study","volume":"149","author":"Davenport","year":"2006","journal-title":"J Pediatr"},{"key":"R15-19-20240907","doi-asserted-by":"crossref","first-page":"899","DOI":"10.1002\/hep.30515","article-title":"Identification of polycystic kidney disease 1 like 1 gene variants in children with biliary atresia splenic malformation syndrome","volume":"70","author":"Berauer","year":"2019","journal-title":"Hepatology"},{"key":"R16-19-20240907","doi-asserted-by":"crossref","first-page":"36","DOI":"10.32552\/2019.ActaMedica.355","article-title":"Biliary atresia splenic malformation syndrome: A single center experience","volume":"50","author":"Ozden","year":"2019","journal-title":"Acta Medica"},{"key":"R17-19-20240907","doi-asserted-by":"crossref","first-page":"746","DOI":"10.5858\/arpa.2011-0623-RA","article-title":"Biliary atresia: A multidisciplinary approach to diagnosis and management","volume":"136","author":"Moreira","year":"2012","journal-title":"Arch Pathol Lab Med"},{"key":"R18-19-20240907","doi-asserted-by":"crossref","first-page":"e000346","DOI":"10.1136\/wjps-2021-000346","article-title":"Outcomes of biliary atresia splenic malformation (BASM) syndrome following Kasai operation: A systematic review and meta-analysis","volume":"5","author":"Xu","year":"2022","journal-title":"World J Pediatr Surg"},{"key":"R19-19-20240907","doi-asserted-by":"crossref","first-page":"e1663","DOI":"10.1542\/peds.2015-3570","article-title":"Newborn screening for biliary atresia","volume":"136","author":"Wang","year":"2015","journal-title":"Pediatrics"}],"container-title":["Journal of West African College of Surgeons"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.4103\/jwas.jwas_195_22","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,19]],"date-time":"2026-08-19T19:13:49Z","timestamp":1787166829000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.4103\/jwas.jwas_195_22"}},"subtitle":["A Case Report from A Tertiary Centre in West Africa and the Lessons Learnt"],"short-title":[],"issued":{"date-parts":[[2023,1]]},"references-count":19,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2023]]}},"URL":"https:\/\/doi.org\/10.4103\/jwas.jwas_195_22","relation":{},"ISSN":["2276-6944"],"issn-type":[{"value":"2276-6944","type":"print"}],"subject":[],"published":{"date-parts":[[2023,1]]}}}