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For extensive disease, chemotherapy and radiotherapy can be utilized to stabilize the disease. Due to poor response and outcomes with current regimens, the focus has been shifted to approaches utilizing molecular targets and immunological agents. Despite all the advancements, the outcomes still remain discouraging for moderate- to high-grade lesions and thus necessitate studies to design promising treatment modalities.<\/jats:p>","DOI":"10.4103\/ojo.ojo_299_23","type":"journal-article","created":{"date-parts":[[2024,6,27]],"date-time":"2024-06-27T01:01:19Z","timestamp":1719450079000},"page":"254-260","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["Orbital malignant peripheral nerve sheath tumor: A case report and review"],"prefix":"10.4103","volume":"17","author":[{"given":"Syed Wajahat Ali","family":"Rizvi","sequence":"first","affiliation":[{"name":"Department of Ophthalmology, Jawaharlal Nehru Medical College, Aligarh Muslim University, Aligarh, Uttar Pradesh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Syed Ali Raza","family":"Rizvi","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology, Al Nahdha 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