{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T16:37:57Z","timestamp":1787071077638,"version":"build-2736575974"},"reference-count":15,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2024,9]]},"abstract":"<jats:title>Abstract:<\/jats:title>\n                  <jats:p>Retinal vascular occlusions are rare in young people, and any occlusion warrants an extensive clinical evaluation to establish the etiology. Cardiac malformations are a source of embolism. We present a case of atrial septal defect (ASD) in a patient with type II Mayer-Rokitansky-K\u00fcster-Hauser syndrome, leading to unilateral branch retinal arterial occlusion (BRAO) in a young woman. A 21-year-old woman presented with sudden, painless, blurring of vision, and a superior visual field defect in her right eye. A fundus examination confirmed the BRAO diagnosis. Ocular and systemic evaluation revealed primary amenorrhea, ASD, ectopic kidneys, and pelvic cyst. Any vascular occlusion in a young patient must be thoroughly evaluated, including a detailed systemic history.<\/jats:p>","DOI":"10.4103\/ojo.ojo_48_24","type":"journal-article","created":{"date-parts":[[2024,10,30]],"date-time":"2024-10-30T13:16:44Z","timestamp":1730294204000},"page":"393-395","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["Branch retinal artery occlusion in a young patient with Mayer-Rokitansky-K\u00fcster-Hauser type 2 syndrome"],"prefix":"10.4103","volume":"17","author":[{"given":"Anita","family":"Bedwal","sequence":"first","affiliation":[{"name":"Department of Ophthalmology, Maharaja Agrasen Medical College, Hisar, Haryana, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mousumi","family":"Banerjee","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology, Maharaja Agrasen Medical College, Hisar, Haryana, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Parveen","family":"Rewri","sequence":"additional","affiliation":[{"name":"Department of Ophthalmology, Maharaja Agrasen Medical College, Hisar, Haryana, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2024,10,24]]},"reference":[{"key":"R1-20241030","doi-asserted-by":"crossref","first-page":"455","DOI":"10.1016\/j.ajo.2008.05.009","article-title":"Branch retinal artery occlusion:Visual prognosis","volume":"146","author":"Mason","year":"2008","journal-title":"Am J Ophthalmol"},{"key":"R2-20241030","first-page":"595","article-title":"Systemic diseases in non-inflammatory branch and central retinal artery occlusion \u2013An overview of 416 patients","volume":"12","author":"Schmidt","year":"2007","journal-title":"Eur J Med Res"},{"key":"R3-20241030","first-page":"3200","article-title":"Retinal artery occlusions and risk factors in the young","volume":"62","author":"Ward","year":"2021","journal-title":"Invest Ophthalmol Vis Sci"},{"key":"R4-20241030","doi-asserted-by":"crossref","first-page":"95","DOI":"10.4103\/0301-4738.94049","article-title":"Retinal arterial occlusions in the young:Systemic associations in Indian population","volume":"60","author":"Ratra","year":"2012","journal-title":"Indian J Ophthalmol"},{"key":"R5-20241030","doi-asserted-by":"crossref","first-page":"776","DOI":"10.1016\/S0002-9394(14)72731-X","article-title":"Retinal arterial occlusions in young adults","volume":"120","author":"Greven","year":"1995","journal-title":"Am J Ophthalmol"},{"key":"R6-20241030","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1186\/1750-1172-2-13","article-title":"Mayer-Rokitansky-K\u00fcster-Hauser (MRKH) syndrome","volume":"2","author":"Morcel","year":"2007","journal-title":"Orphanet J Rare Dis"},{"key":"R7-20241030","first-page":"549","article-title":"Concurrence of the Holt-Oram syndrome and the Rokitansky-Kuster-Hauser syndrome. 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