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Atypical presentations include: (1) highly asymmetric or even unilateral papilledema, and IIH without papilledema; (2) ocular motor disturbances from third nerve palsy, fourth nerve palsy, internuclear ophthalmoplegia, diffuse ophthalmoplegia, and skew deviation; (3) olfactory dysfunction; (4) trigeminal nerve dysfunction; (5) facial nerve dysfunction; (6) hearing loss and vestibular dysfunction; (7) lower cranial nerve dysfunction including deviated uvula, torticollis, and tongue weakness; (8) spontaneous skull base cerebrospinal fluid leak; and (9) seizures. Although atypical findings should raise a red flag and prompt further investigation for an alternative etiology, clinicians should be familiar with these unusual presentations.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.4103\/tjo.tjo_69_20","type":"journal-article","created":{"date-parts":[[2020,12,1]],"date-time":"2020-12-01T08:00:57Z","timestamp":1606809657000},"page":"25-38","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":48,"title":["Atypical presentations of idiopathic intracranial hypertension"],"prefix":"10.4103","volume":"11","author":[{"given":"Benson S.","family":"Chen","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nancy J.","family":"Newman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Val\u00e9rie","family":"Biousse","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-4-20240830","doi-asserted-by":"crossref","first-page":"492","DOI":"10.1097\/00000658-193710000-00002","article-title":"Intracranial pressure without brain tumor: Diagnosis and treatment","volume":"106","author":"Dandy","year":"1937","journal-title":"Ann Surg"},{"key":"R2-4-20240830","doi-asserted-by":"crossref","first-page":"1492","DOI":"10.1212\/01.WNL.0000029570.69134.1B","article-title":"Diagnostic criteria for idiopathic intracranial hypertension","volume":"59","author":"Friedman","year":"2002","journal-title":"Neurology"},{"key":"R3-4-20240830","doi-asserted-by":"crossref","first-page":"1159","DOI":"10.1212\/WNL.0b013e3182a55f17","article-title":"Revised diagnostic criteria for the pseudotumor cerebri syndrome in adults and children","volume":"81","author":"Friedman","year":"2013","journal-title":"Neurology"},{"key":"R4-4-20240830","first-page":"55","article-title":"Whence pseudotumor cerebri?","volume":"5","author":"Smith","year":"1985","journal-title":"J Clin Neuroophthalmol"},{"key":"R5-4-20240830","doi-asserted-by":"crossref","first-page":"1195","DOI":"10.1111\/head.13153","article-title":"Headache in idiopathic intracranial hypertension: Findings from the idiopathic intracranial hypertension treatment trial","volume":"57","author":"Friedman","year":"2017","journal-title":"Headache"},{"key":"R6-4-20240830","doi-asserted-by":"crossref","first-page":"1551","DOI":"10.1212\/WNL.58.10.1551","article-title":"Headache diagnoses in patients with treated idiopathic intracranial hypertension","volume":"58","author":"Friedman","year":"2002","journal-title":"Neurology"},{"key":"R7-4-20240830","doi-asserted-by":"crossref","first-page":"1458","DOI":"10.1111\/ene.12512","article-title":"The course of headache in idiopathic intracranial hypertension: A 12-month prospective follow-up study","volume":"21","author":"Yri","year":"2014","journal-title":"Eur J Neurol"},{"key":"R8-4-20240830","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1016\/j.preteyeres.2015.10.001","article-title":"Pathogenesis of optic disc edema in raised intracranial pressure","volume":"50","author":"Hayreh","year":"2016","journal-title":"Prog Retin Eye Res"},{"key":"R9-4-20240830","doi-asserted-by":"crossref","first-page":"1461","DOI":"10.1212\/WNL.38.9.1461","article-title":"The minor symptoms of increased intracranial pressure: 101 patients with benign intracranial hypertension","volume":"38","author":"Round","year":"1988","journal-title":"Neurology"},{"key":"R10-4-20240830","doi-asserted-by":"crossref","first-page":"415","DOI":"10.1136\/jnnp.74.4.415","article-title":"False localising signs","volume":"74","author":"Larner","year":"2003","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"R11-4-20240830","doi-asserted-by":"crossref","first-page":"490","DOI":"10.1093\/brain\/27.4.490","article-title":"The false localising signs of intracranial tumour","volume":"27","author":"Collier","year":"1904","journal-title":"Brain"},{"key":"R12-4-20240830","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1097\/00055735-200212000-00005","article-title":"False and non-localizing signs in neuro-ophthalmology","volume":"13","author":"Lepore","year":"2002","journal-title":"Curr Opin Ophthalmol"},{"key":"R13-4-20240830","doi-asserted-by":"crossref","first-page":"1237","DOI":"10.1001\/archopht.118.9.1237","article-title":"Divergence insufficiency revisited: Natural history of idiopathic cases and neurologic associations","volume":"118","author":"Jacobson","year":"2000","journal-title":"Arch Ophthalmol"},{"key":"R14-4-20240830","doi-asserted-by":"crossref","first-page":"776","DOI":"10.1136\/bjo.56.10.776","article-title":"Divergence paralysis with raised intracranial pressure. 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