{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,1]],"date-time":"2025-11-01T13:47:46Z","timestamp":1762004866468},"reference-count":24,"publisher":"Baishideng Publishing Group Inc.","issue":"6","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["WJH"],"published-print":{"date-parts":[[2017]]},"DOI":"10.4254\/wjh.v9.i6.343","type":"journal-article","created":{"date-parts":[[2017,2,27]],"date-time":"2017-02-27T00:05:19Z","timestamp":1488153919000},"page":"343","source":"Crossref","is-referenced-by-count":9,"title":["Hyperammonemia crisis following parturition in a female patient with ornithine transcarbamylase deficiency"],"prefix":"10.4254","volume":"9","author":[{"given":"Jun","family":"Kido","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tatsuya","family":"Kawasaki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hiroshi","family":"Mitsubuchi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hidenobu","family":"Kamohara","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takashi","family":"Ohba","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shirou","family":"Matsumoto","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fumio","family":"Endo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kimitoshi","family":"Nakamura","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"2060","reference":[{"key":"ref1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320390226"},{"key":"ref2","doi-asserted-by":"crossref","unstructured":"Brusilow SW, Valle DL, Batshaw M. New pathways of nitrogen excretion in inborn errors of urea synthesis. Lancet 1979;2:452-454.","DOI":"10.1016\/S0140-6736(79)91503-4"},{"key":"ref3","doi-asserted-by":"publisher","DOI":"10.1203\/00006450-199102000-00009"},{"key":"ref4","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajem.2015.12.013"},{"key":"ref5","doi-asserted-by":"crossref","unstructured":"Feillet F, Leonard JV. Alternative pathway therapy for urea cycle disorders. J Inherit Metab Dis 1998;21 Suppl 1:101-111.","DOI":"10.1023\/A:1005365825875"},{"key":"ref6","doi-asserted-by":"publisher","DOI":"10.1007\/s00431-006-0143-y"},{"key":"ref7","doi-asserted-by":"crossref","unstructured":"Schaefer F, Straube E, Oh J, Mehls O, Mayatepek E. Dialysis in neonates with inborn errors of metabolism. Nephrol Dial Transplant 1999;14:910-918.","DOI":"10.1093\/ndt\/14.4.910"},{"key":"ref8","doi-asserted-by":"crossref","unstructured":"Uchino T, Endo F, Matsuda I. Neurodevelopmental outcome of long-term therapy of urea cycle disorders in Japan. J Inherit Metab Dis 1998;21 Suppl 1:151-159.","DOI":"10.1023\/A:1005374027693"},{"key":"ref9","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-011-9427-0"},{"key":"ref10","doi-asserted-by":"crossref","unstructured":"Leonard JV. The nutritional management of urea cycle disorders. J Pediatr 2001;138:S40-44; discussion S44-45.","DOI":"10.1067\/mpd.2001.111835"},{"key":"ref11","doi-asserted-by":"publisher","DOI":"10.1111\/ped.12439"},{"key":"ref12","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-011-9389-2"},{"key":"ref13","doi-asserted-by":"publisher","DOI":"10.1136\/bcr-2012-007416"},{"key":"ref14","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M205094200"},{"key":"ref15","doi-asserted-by":"publisher","DOI":"10.1203\/00006450-198005000-00006"},{"key":"ref16","doi-asserted-by":"publisher","DOI":"10.1016\/j.neuint.2011.09.007"},{"key":"ref17","doi-asserted-by":"publisher","DOI":"10.1055\/s-0030-1254240"},{"key":"ref18","doi-asserted-by":"crossref","unstructured":"Maestri NE, McGowan KD, Brusilow SW. Plasma glutamine concentration: a guide in the management of urea cycle disorders. J Pediatr 1992;121:259-261.","DOI":"10.1016\/S0022-3476(05)81200-4"},{"key":"ref19","doi-asserted-by":"crossref","unstructured":"Berry GT, Steiner RD. Long-term management of patients with urea cycle disorders. J Pediatr 2001;138:S56-60; discussion S60-61.","DOI":"10.1067\/mpd.2001.111837"},{"key":"ref20","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM199006073222307"},{"key":"ref21","doi-asserted-by":"crossref","unstructured":"Whitington PF, Alonso EM, Boyle JT, Molleston JP, Rosenthal P, Emond JC, Millis JM. Liver transplantation for the treatment of urea cycle disorders. J Inherit Metab Dis 1998;21 Suppl 1:112-118.","DOI":"10.1023\/A:1005317909946"},{"key":"ref22","doi-asserted-by":"publisher","DOI":"10.1002\/lt.20587"},{"key":"ref23","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-3046.2010.01402.x"},{"key":"ref24","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-3046.2011.01494.x"}],"container-title":["World Journal of Hepatology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/www.wjgnet.com\/1948-5182\/full\/v9\/i6\/343.htm","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,9,18]],"date-time":"2019-09-18T23:44:47Z","timestamp":1568850287000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.wjgnet.com\/1948-5182\/full\/v9\/i6\/343.htm"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017]]},"references-count":24,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2017]]}},"URL":"https:\/\/doi.org\/10.4254\/wjh.v9.i6.343","relation":{},"ISSN":["1948-5182"],"issn-type":[{"value":"1948-5182","type":"print"}],"subject":[],"published":{"date-parts":[[2017]]}}}