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We describe unusual complications of HHT in a 68-year-old male who developed high-output cardiac failure with pulmonary hypertension in combination with hepatic encephalopathy due to hepatic AVMs. This case shows the importance of a multi-system approach to HHT and considers the treatment of its hepatic complications.<\/jats:p>","DOI":"10.4997\/jrcpe.2014.207","type":"journal-article","created":{"date-parts":[[2014,7,8]],"date-time":"2014-07-08T05:46:51Z","timestamp":1404798411000},"page":"126-129","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":5,"title":["Pulmonary Hypertension and Hepatic Encephalopathy: Lethal Complications of Rendu-Osler-Weber Disease"],"prefix":"10.1177","volume":"44","author":[{"given":"TJ","family":"Ford","sequence":"first","affiliation":[{"name":"Advanced Trainee in Cardiology, Prince of Wales Hospital, Sydney, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"MW","family":"Fong","sequence":"additional","affiliation":[{"name":"Basic Physician Trainee, Prince of Wales Hospital, Sydney, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"BC","family":"Cheah","sequence":"additional","affiliation":[{"name":"Medical Student, University of New South Wales, Sydney"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C","family":"Alexopolous","sequence":"additional","affiliation":[{"name":"Consultant Cardiologist, Port Macquarie Base Hospital, Port Macquarie, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2014,6]]},"reference":[{"key":"e_1_2_1_2_2","first-page":"63","article-title":"Multiple hereditary telangiectases causing hemorrhage (hereditary hemorrhagic telangiectasia)","volume":"20","author":"Hanes FM","year":"1909","unstructured":"HanesFM. 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