{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,29]],"date-time":"2026-09-29T22:46:01Z","timestamp":1790721961483,"version":"4.1.0"},"reference-count":16,"publisher":"Termedia Sp. z.o.o.","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pol J Radiol"],"published-print":{"date-parts":[[2018,2,4]]},"abstract":"<jats:p>Erdheim-Chester disease (ECD) is a rare sporadic non-Langerhans cell histiocytic (LCH) proliferative disorder with systemic predilection. It usually affects adults in the 5th-7th decades of life and has non-specific clinical manifestations. Its suspicion is often heralded by the presence of characteristic radiological findings and subsequently confirmed by demonstration of CD68-positive xanthogranulomatous infiltrates on histopathology. Despite being a non-malignant entity, it might be fatal due to organ dysfunction. Imaging plays a key role in the diagnosis, management, and follow-up. Imaging findings are essential to establish the diagnosis, assess actual disease burden, and explore the aetiopathogenesis and therapeutic options to halt disease progression and associated morbidity.<\/jats:p>","DOI":"10.5114\/pjr.2018.73290","type":"journal-article","created":{"date-parts":[[2018,3,8]],"date-time":"2018-03-08T09:51:40Z","timestamp":1520502700000},"page":"54-62","source":"Crossref","is-referenced-by-count":53,"title":["Imaging findings in Erdheim-Chester disease: what every radiologist needs to know"],"prefix":"10.5114","volume":"83","author":[{"given":"Pawan","family":"Kumar","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anuradha","family":"Singh","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shivanand","family":"Gamanagatti","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sanjeev","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sheragaru Hanumanthappa","family":"Chandrashekhara","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"3061","published-online":{"date-parts":[[2018,2,4]]},"reference":[{"key":"ref-1135852","doi-asserted-by":"crossref","unstructured":"Veyssier-Belot C, Cacoub P, Caparros-Lefebvre D et al: Erdheim- Chester disease. 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