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Some stereotypical knowledge may be misleading; e.g. monogenic AIDs are not exclusively found in children, family history is often negative, fever frequently is not a\u00a0leading manifestation and frequency of attacks in adults is usually variable. Lack of genetic confirmation should not stop anti-inflammatory ex juvantibus therapy. The pattern of tissue injury in AIDs is basically different from that observed in autoimmunity. There is no autoaggression against organ-specific antigens, but substantial damage (amyloidosis, cachexia, premature cardiovascular disease) is secondary to long-lasting inflammation.&lt;br \/&gt;\nThe Polish national programme of anti-interleukin 1 treatment opens new possibilities for the treatment. However, monogenic AIDs are frequently misdiagnosed and more awareness is needed.<\/jats:p>","DOI":"10.5114\/reum.2019.91298","type":"journal-article","created":{"date-parts":[[2020,1,10]],"date-time":"2020-01-10T15:26:26Z","timestamp":1578669986000},"page":"326-335","source":"Crossref","is-referenced-by-count":5,"title":["Monogenic autoinflammatory diseases in adults \u2013 a\u00a0challenge to rheumatologic practice at the onset of the Polish national programme of interleukin 1 inhibitor treatment"],"prefix":"10.5114","volume":"57","author":[{"given":"Marcin","family":"Milchert","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Joanna","family":"Makowska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Olga","family":"Brzezi\u0144ska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marek","family":"Brzosko","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ewa","family":"Wi\u0119sik-Szewczyk","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"3061","published-online":{"date-parts":[[2019,12,31]]},"reference":[{"key":"ref-777676","doi-asserted-by":"crossref","first-page":"621","DOI":"10.1146\/annurev.immunol.25.022106.141627","article-title":"Horror autoinflammaticus: the molecular pathophysiology of autoinflammatory disease","volume":"27","author":"Masters SL","year":"2009","unstructured":"Masters SL, Simon A, Aksentijevich I, Kastner DL. 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