{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,5,14]],"date-time":"2025-05-14T13:17:35Z","timestamp":1747228655370,"version":"3.40.5"},"reference-count":0,"publisher":"Sociedad Argentina de Gastroenterologia","issue":"3","license":[{"start":{"date-parts":[[2022,9,29]],"date-time":"2022-09-29T00:00:00Z","timestamp":1664409600000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["ACTA"],"abstract":"<jats:p>La derivaci\u00f3n biliar parcial externa en pacientes con colestasis intrahep\u00e1tica familiar progresiva y s\u00edndrome de Alagille reduce los niveles sangu\u00edneos de sales biliares modificando su circulaci\u00f3n enterohep\u00e1tica. Si esta cirug\u00eda es realizada antes de la instalaci\u00f3n de la cirrosis, podr\u00eda mejorar la sintomatolog\u00eda y modificar la progresi\u00f3n de la fibrosis hep\u00e1tica y, con ello, la evoluci\u00f3n de la enfermedad, evitando o retrasando la necesidad de trasplante hep\u00e1tico. Presentamos los casos de ocho pacientes a quienes se les realiz\u00f3 una derivaci\u00f3n biliar parcial externa: cinco con diagn\u00f3stico de colestasis intrahep\u00e1tica familiar progresiva, y tres con s\u00edndrome de Alagille y prurito invalidante. En todos ellos se descart\u00f3 por medio de biopsia hep\u00e1tica la presencia de cirrosis. De los cinco pacientes con colestasis intrahep\u00e1tica familiar progresiva, dos se encuentran vivos, con su h\u00edgado nativo y escasa sintomatolog\u00eda a cuatro y veinte a\u00f1os del procedimiento, respectivamente. Los tres pacientes con s\u00edndrome de Alagille presentaron una mejor\u00eda de la sintomatolog\u00eda, con resoluci\u00f3n en dos de ellos.<\/jats:p>","DOI":"10.52787\/agl.v52i3.230","type":"journal-article","created":{"date-parts":[[2022,9,30]],"date-time":"2022-09-30T12:51:34Z","timestamp":1664542294000},"page":"388-394","source":"Crossref","is-referenced-by-count":0,"title":["Derivaci\u00f3n biliar parcial externa en colestasis intrahep\u00e1tica familiar progresiva y s\u00edndrome de Alagille: serie de casos"],"prefix":"10.52787","volume":"52","author":[{"given":"Fabian","family":"Salgueiro","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6869-7014","authenticated-orcid":false,"given":"Carol","family":"Lezama Elecharri","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8129-8202","authenticated-orcid":false,"given":"Marcela","family":"Galoppo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9412-0921","authenticated-orcid":false,"given":"Micaela","family":"Wisniacki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1722-2067","authenticated-orcid":false,"given":"Mar\u00eda","family":"Solaegui","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alejandra","family":"Pedreira","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8418-1579","authenticated-orcid":false,"given":"Sabrina","family":"Torres","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3856-0252","authenticated-orcid":false,"given":"Elena","family":"De Matteo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6070-9124","authenticated-orcid":false,"given":"Miguel","family":"Palmeiro","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8154-7918","authenticated-orcid":false,"given":"Pablo","family":"Volont\u00e9","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cristina","family":"Galoppo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"30608","published-online":{"date-parts":[[2022,9,29]]},"container-title":["Acta Gastroenterol\u00f3gica Latinoamericana"],"original-title":[],"link":[{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/download\/230\/519","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/download\/230\/559","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/download\/230\/559","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,9,30]],"date-time":"2022-09-30T12:51:34Z","timestamp":1664542294000},"score":1,"resource":{"primary":{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/view\/230"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,9,29]]},"references-count":0,"journal-issue":{"issue":"3","published-online":{"date-parts":[[2022,9,29]]}},"URL":"https:\/\/doi.org\/10.52787\/agl.v52i3.230","relation":{},"ISSN":["2469-1119"],"issn-type":[{"type":"print","value":"2469-1119"}],"subject":[],"published":{"date-parts":[[2022,9,29]]}}}