{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,5,14]],"date-time":"2025-05-14T13:17:41Z","timestamp":1747228661952,"version":"3.40.5"},"reference-count":0,"publisher":"Sociedad Argentina de Gastroenterologia","issue":"4","license":[{"start":{"date-parts":[[2023,12,30]],"date-time":"2023-12-30T00:00:00Z","timestamp":1703894400000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["ACTA"],"abstract":"<jats:p>Introducci\u00f3n.\u00a0Los complejos de Von Meyenburg o hamartomas biliares son una anomal\u00eda cong\u00e9nita benigna rara de los conductos biliares intrahep\u00e1ticos. Generalmente son asintom\u00e1ticos y se encuentran de manera incidental en los estudios de im\u00e1genes pero pueden ser causa de ictericia, dolor abdominal y colangitis.\u00a0\nCaso cl\u00ednico.\u00a0Paciente de sexo masculino de 80 a\u00f1os, que ingresa en el servicio de urgencias por ictericia progresiva asociada a prurito, con hepatograma alterado y patr\u00f3n de colestasis. Se le realizan estudios de im\u00e1genes en los cuales no se evidencian alteraciones en el par\u00e9nquima hep\u00e1tico ni en las v\u00edas biliares. Se decide realizar una biopsia hep\u00e1tica en la que se observa colestasis canalicular perivenular y presencia de complejos de Von Meyenburg. El paciente recibi\u00f3 tratamiento con \u00e1cido ursodesoxic\u00f3lico con normalizaci\u00f3n de la colestasis en el seguimiento ambulatorio.\u00a0\nConclusi\u00f3n.\u00a0El diagn\u00f3stico de hamartomas biliares debe tenerse en cuenta en los pacientes con colestasis intrahep\u00e1tica en los que no se identifica la etiolog\u00eda con los estudios iniciales. Representan un desaf\u00edo diagn\u00f3stico ya que no siempre se observan en los estudios de im\u00e1genes.<\/jats:p>","DOI":"10.52787\/agl.v53i4.323","type":"journal-article","created":{"date-parts":[[2024,6,21]],"date-time":"2024-06-21T19:47:59Z","timestamp":1718999279000},"page":"390-394","source":"Crossref","is-referenced-by-count":0,"title":["Complejos de Von Meyenburg o hamartomas biliares: reporte de un caso"],"prefix":"10.52787","volume":"53","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-1867-3583","authenticated-orcid":false,"given":"Ros\u00e1ngela","family":"Ram\u00edrez Barranco","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Carmen Yanette","family":"Su\u00e1rez Quintero","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4270-7146","authenticated-orcid":false,"given":"Fredy","family":"\u00c1vila Almanza","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"30608","published-online":{"date-parts":[[2023,12,30]]},"container-title":["Acta Gastroenterol\u00f3gica Latinoamericana"],"original-title":[],"link":[{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/download\/323\/695","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/download\/323\/711","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/download\/323\/711","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,6,21]],"date-time":"2024-06-21T19:48:00Z","timestamp":1718999280000},"score":1,"resource":{"primary":{"URL":"https:\/\/actaojs.org.ar\/ojs\/index.php\/acta\/article\/view\/323"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,12,30]]},"references-count":0,"journal-issue":{"issue":"4","published-online":{"date-parts":[[2023,12,30]]}},"URL":"https:\/\/doi.org\/10.52787\/agl.v53i4.323","relation":{},"ISSN":["2469-1119"],"issn-type":[{"type":"print","value":"2469-1119"}],"subject":[],"published":{"date-parts":[[2023,12,30]]}}}