{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,31]],"date-time":"2026-07-31T15:14:04Z","timestamp":1785510844916,"version":"3.56.0"},"reference-count":22,"publisher":"Open Medical Publishing","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"abstract":"<jats:sec id=\"background\">\n                    <jats:title>Background<\/jats:title>\n                    <jats:p>Osteogenesis imperfecta (OI) is a genetic disorder of bone fragility and deformity that frequently requires surgical management. The Fassier-Duval (FD) telescopic nail is a treatment of choice for the lower limb deformities and fractures in children with OI, with the aim of decreasing the number of surgeries and improving the results. This study prospectively assesses the clinical and radiological outcomes of FD telescopic nailing in lower limb deformities and fractures in children with OI.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec id=\"methods\">\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>This prospective study included 31 children with OI treated for deformities\/fractures of the femur or tibia. All had a minimum of 2 years of follow-up, subjected to FD telescopic nailing. All patients were on pre-operative bisphosphonate therapy. Functional outcome scores (BAMF, PODCI), ambulatory ability, radiographic correction (CORA angles), union rates, complication and revision surgery rates were assessed.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec id=\"results\">\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>The mean age was 5.7\u00b12.1 years; 18 males, 13 females. Most patients had moderate\/severe OI. BAMF score improved from 5.8\u00b11.6 to 8.2\u00b11.3 (p&lt;0.001). PODCI score increased from 42.5\u00b17.2 to 46.2\u00b17.5 (p&lt;0.001). The mean angular coronal\/sagittal deformity preoperatively was 33.5\u00b0\/35.6\u00b0 and was corrected to ~1\u00b0 postoperatively (p&lt;0.001). Mean time of callus formation was 5.6 weeks. Union was achieved within 6.5 months in all patients. The overall complication rate was 22.5%. Revision surgery was done in 7.5%.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec id=\"conclusions\">\n                    <jats:title>Conclusions<\/jats:title>\n                    <jats:p>FD telescopic nailing with osteotomy is a useful method for short-term treatment of lower limb deformities and fractures in children with OI, with significant functional and radiological improvements, increased mobility, and an acceptable complication\/revision rate.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.52965\/001c.165094","type":"journal-article","created":{"date-parts":[[2026,7,31]],"date-time":"2026-07-31T14:54:35Z","timestamp":1785509675000},"source":"Crossref","is-referenced-by-count":0,"title":["Outcomes of Telescopic Nailing of Lower Limb Deformities and Fractures in Children with Osteogenesis Imperfecta: A Prospective Study"],"prefix":"10.52965","volume":"18","author":[{"given":"yasser","family":"ahmed othman sorour","sequence":"first","affiliation":[{"id":[{"id":"https:\/\/ror.org\/02wgx3e98","id-type":"ROR","asserted-by":"publisher"}],"name":"Sohag University","department":["Orthopedic"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marwan","family":"Shams","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/02wgx3e98","id-type":"ROR","asserted-by":"publisher"}],"name":"Sohag University","department":["Orthopedic"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Abdelmageed","family":"Aboelabbas Abdelmageed Wahaballah","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/02wgx3e98","id-type":"ROR","asserted-by":"publisher"}],"name":"Sohag University","department":["Orthopedic"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ahmad","family":"Ibraheem Addosooki","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/02wgx3e98","id-type":"ROR","asserted-by":"publisher"}],"name":"Sohag University","department":["Orthopedic"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ashraf","family":"Marzouk","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/02wgx3e98","id-type":"ROR","asserted-by":"publisher"}],"name":"Sohag University","department":["Orthopedic"]}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"30777","published-online":{"date-parts":[[2026,7,31]]},"reference":[{"issue":"4","key":"ref1","doi-asserted-by":"publisher","first-page":"R95","DOI":"10.1530\/EJE-20-0299","article-title":"Osteogenesis imperfecta: an update on clinical features and therapies","volume":"183","author":"R. Marom","year":"2020","journal-title":"Eur J Endocrinol"},{"issue":"5","key":"ref2","doi-asserted-by":"publisher","first-page":"561","DOI":"10.1097\/00004694-199809000-00001","article-title":"The POSNA pediatric musculoskeletal functional health questionnaire: report on reliability, validity, and sensitivity to change. Pediatric Outcomes Instrument Development Group. Pediatric Orthopaedic Society of North America","volume":"18","author":"L. H. Daltroy","year":"1998","journal-title":"J Pediatr Orthop"},{"issue":"1","key":"ref3","doi-asserted-by":"publisher","first-page":"33","DOI":"10.1097\/00002060-200301000-00006","article-title":"Brief Assessment of Motor Function: Reliability and Concurrent Validity of the Gross Motor Scale","volume":"82","author":"H. L. Cintas","year":"2003","journal-title":"American Journal of Physical Medicine & Rehabilitation"},{"issue":"280","key":"ref4","doi-asserted-by":"publisher","first-page":"65","DOI":"10.1097\/00003086-199207000-00009","article-title":"Mechanical axis deviation of the lower limbs. Preoperative planning of multiapical frontal plane angular and bowing deformities of the femur and tibia","author":"D. Paley","year":"1992","journal-title":"Clin Orthop Relat Res"},{"issue":"3","key":"ref5","doi-asserted-by":"publisher","first-page":"573","DOI":"10.1542\/peds.111.3.573","article-title":"Intravenous bisphosphonate therapy in children with osteogenesis imperfecta","volume":"111","author":"M. J. Falk","year":"2003","journal-title":"Pediatrics"},{"issue":"3","key":"ref6","doi-asserted-by":"publisher","first-page":"217","DOI":"10.1007\/s11832-011-0341-7","article-title":"Fassier-Duval femoral rodding in children with osteogenesis imperfecta receiving bisphosphonates: functional outcomes at one year","volume":"5","author":"J. Ruck","year":"2011","journal-title":"J Child Orthop"},{"issue":"3","key":"ref7","doi-asserted-by":"publisher","first-page":"581","DOI":"10.1038\/s41436-019-0688-6","article-title":"Pediatric Outcomes Data Collection Instrument is a Useful Patient-Reported Outcome Measure for Physical Function in Children with Osteogenesis Imperfecta","volume":"22","author":"C. N. Murali","year":"2020","journal-title":"Genetics in Medicine"},{"issue":"7","key":"ref8","doi-asserted-by":"publisher","first-page":"1151","DOI":"10.3390\/jpm12071151","article-title":"Surgical Strategy to Decrease the Revision Rate of Fassier\u2013Duval Nailing in the Lower Limbs of Osteogenesis Imperfecta","volume":"12","author":"Y. C. Hung","year":"2022","journal-title":"Journal of Personalized Medicine"},{"issue":"4","key":"ref9","doi-asserted-by":"publisher","first-page":"338","DOI":"10.1097\/BPB.0000000000000483","article-title":"Intraoperative bleeding in patients with osteogenesis imperfecta type III treated by Fassier-Duval femoral rodding: analysis of risk factors","volume":"27","author":"P. Persiani","year":"2018","journal-title":"J Pediatr Orthop B"},{"issue":"4","key":"ref10","doi-asserted-by":"publisher","first-page":"e347","DOI":"10.1097\/BPO.0000000000001763","article-title":"Problems, Complications, and Factors Predisposing to Failure of Fassier-Duval Rodding in Children With Osteogenesis Imperfecta: A Double-center Study","volume":"41","author":"B. J. Musielak","year":"2021","journal-title":"Journal of Pediatric Orthopaedics"},{"issue":"19","key":"ref11","doi-asserted-by":"publisher","first-page":"10281","DOI":"10.3390\/ijms221910281","article-title":"Congenital Metabolic Bone Disorders as a Cause of Bone Fragility","volume":"22","author":"F. Marini","year":"2021","journal-title":"Int J Mol Sci"},{"issue":"6","key":"ref12","doi-asserted-by":"publisher","first-page":"331","DOI":"10.1097\/BPO.0000000000000824","article-title":"Mid-term Results of Femoral and Tibial Osteotomies and Fassier-Duval Nailing in Children With Osteogenesis Imperfecta","volume":"38","author":"K. A. Azzam","year":"2018","journal-title":"J Pediatr Orthop"},{"issue":"1","key":"ref13","doi-asserted-by":"publisher","first-page":"97","DOI":"10.1302\/1863-2548.12.170009","article-title":"Effects of a telescopic intramedullary rod for treating patients with osteogenesis imperfecta of the femur","volume":"12","author":"D. L. Rosemberg","year":"2018","journal-title":"Journal of Children's Orthopaedics"},{"issue":"4","key":"ref14","doi-asserted-by":"publisher","first-page":"554","DOI":"10.4103\/ortho.IJOrtho_202_18","article-title":"Results of Rodding and Impact on Ambulation and Refracture in Osteogenesis Imperfecta: Study of 21 Children","volume":"53","author":"A. R. Bhaskar","year":"2019","journal-title":"Indian J Orthop"},{"key":"ref15","doi-asserted-by":"publisher","first-page":"17052","DOI":"10.1038\/nrdp.2017.52","article-title":"Osteogenesis imperfecta","volume":"3","author":"J. C. Marini","year":"2017","journal-title":"Nat Rev Dis Primers"},{"key":"ref16","doi-asserted-by":"publisher","first-page":"194","DOI":"10.1016\/j.actbio.2020.04.040","article-title":"Osteopontin regulates type I collagen fibril formation in bone tissue","volume":"120","author":"B. Depalle","year":"2021","journal-title":"Acta Biomater"},{"key":"ref17","doi-asserted-by":"publisher","first-page":"27","DOI":"10.1016\/j.metabol.2017.06.001","article-title":"Osteogenesis imperfecta - A clinical update","volume":"80","author":"S. Tournis","year":"2018","journal-title":"Metabolism"},{"issue":"5-6","key":"ref18","doi-asserted-by":"publisher","first-page":"597","DOI":"10.1089\/hum.2024.191","article-title":"Comprehensive Review of Osteogenesis Imperfecta: Current Treatments and Future Innovations","volume":"36","author":"S. Chaugule","year":"2025","journal-title":"Hum Gene Ther"},{"issue":"1","key":"ref19","doi-asserted-by":"publisher","first-page":"12","DOI":"10.1302\/1863-2548.13.180184","article-title":"The orthopaedic management of long bone deformities in genetically and acquired generalized bone weakening conditions","volume":"13","author":"T. Wirth","year":"2019","journal-title":"J Child Orthop"},{"issue":"2","key":"ref20","doi-asserted-by":"publisher","first-page":"185","DOI":"10.1177\/18632521261423059","article-title":"Evolution and outcomes of telescoping intramedullary rods in pediatric bone fragility disorders: A systematic review","volume":"20","author":"P. J. Mounsef","year":"2026","journal-title":"J Child Orthop"},{"issue":"4","key":"ref21","doi-asserted-by":"publisher","first-page":"458","DOI":"10.1097\/BPO.0b013e31821bfb50","article-title":"Experience with the Fassier-Duval telescopic rod: first 24 consecutive cases with a minimum of 1-year follow-up","volume":"31","author":"O. Birke","year":"2011","journal-title":"J Pediatr Orthop"},{"issue":"1, Supplement","key":"ref22","doi-asserted-by":"publisher","first-page":"102759","DOI":"10.1016\/j.otsr.2020.102759","article-title":"Telescopic rodding in children: Technical progression from Dubow\u2013Bailey to Fassier\u2013DuvalTM","volume":"107","author":"A. Fassier","year":"2021","journal-title":"Orthopaedics & Traumatology: Surgery & Research"}],"container-title":["Orthopedic Reviews"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/orthopedicreviews.openmedicalpublishing.org\/article\/165094-outcomes-of-telescopic-nailing-of-lower-limb-deformities-and-fractures-in-children-with-osteogenesis-imperfecta-a-prospective-study","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,7,31]],"date-time":"2026-07-31T14:54:35Z","timestamp":1785509675000},"score":1,"resource":{"primary":{"URL":"https:\/\/orthopedicreviews.openmedicalpublishing.org\/article\/165094-outcomes-of-telescopic-nailing-of-lower-limb-deformities-and-fractures-in-children-with-osteogenesis-imperfecta-a-prospective-study"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,7,31]]},"references-count":22,"URL":"https:\/\/doi.org\/10.52965\/001c.165094","relation":{},"ISSN":["2035-8164"],"issn-type":[{"value":"2035-8164","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,7,31]]}}}