{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,26]],"date-time":"2026-09-26T10:59:59Z","timestamp":1790420399924,"version":"4.1.0"},"reference-count":159,"publisher":"Ubiquity Press, Ltd.","issue":"1","license":[{"start":{"date-parts":[[2020,1,1]],"date-time":"2020-01-01T00:00:00Z","timestamp":1577836800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2020,8,6]]},"DOI":"10.5334\/tohm.548","type":"journal-article","created":{"date-parts":[[2020,8,7]],"date-time":"2020-08-07T04:38:55Z","timestamp":1596775135000},"source":"Crossref","is-referenced-by-count":34,"title":["Review of Hereditary and Acquired Rare Choreas"],"prefix":"10.5334","volume":"10","author":[{"given":"Daniel","family":"Martinez-Ramirez","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ruth H.","family":"Walker","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mayela","family":"Rodr\u00edguez-Violante","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Emilia M.","family":"Gatto","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"3285","reference":[{"key":"key20200807035017_B1","first-page":"514","article-title":"Diagnosis and treatment of chorea syndromes","volume":"15","year":"2015","journal-title":"Current neurology and neuroscience reports"},{"key":"key20200807035017_B2","first-page":"308","article-title":"Chorea and ballism","volume":"5","year":"1992","journal-title":"Curr Opin Neurol Neurosurg"},{"key":"key20200807035017_B3","first-page":"1001","article-title":"Chorea","volume":"25","year":"2019","journal-title":"Continuum (Minneap Minn)"},{"key":"key20200807035017_B4","first-page":"1186","article-title":"Chorea","volume":"22","year":"2016","journal-title":"Continuum (Minneap Minn)"},{"key":"key20200807035017_B5","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1002\/mds.26521","article-title":"Genetics of movement disorders in the next-generation sequencing era","volume":"31","year":"2016","journal-title":"Mov Disord"},{"key":"key20200807035017_B6","doi-asserted-by":"crossref","first-page":"942","DOI":"10.1016\/S1474-4422(11)70196-X","article-title":"Exome sequencing: A transformative technology","volume":"10","year":"2011","journal-title":"Lancet Neurol"},{"key":"key20200807035017_B7","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1111\/ane.12609","article-title":"Hereditary chorea \u2013 what else to consider when the Huntington\u2019s disease genetics test is negative?","volume":"135","year":"2017","journal-title":"Acta Neurol Scand"},{"key":"key20200807035017_B8","doi-asserted-by":"crossref","first-page":"1105","DOI":"10.1001\/jamaneurol.2016.2215","article-title":"Expanding the Spectrum of Genes Involved in Huntington Disease Using a Combined Clinical and Genetic Approach","volume":"73","year":"2016","journal-title":"JAMA Neurol"},{"key":"key20200807035017_B9","doi-asserted-by":"crossref","first-page":"423","DOI":"10.1002\/mds.26115","article-title":"A de novo ADCY5 mutation causes early-onset autosomal dominant chorea and dystonia","volume":"30","year":"2015","journal-title":"Mov Disord"},{"key":"key20200807035017_B10","doi-asserted-by":"crossref","first-page":"292","DOI":"10.1212\/WNL.0000000000000061","article-title":"C9orf72 expansions are the most common genetic cause of Huntington disease phenocopies","volume":"82","year":"2014","journal-title":"Neurology"},{"key":"key20200807035017_B11","doi-asserted-by":"crossref","first-page":"544","DOI":"10.1038\/s41582-018-0047-2","article-title":"C9orf72-mediated ALS and FTD: multiple pathways to disease","volume":"14","year":"2018","journal-title":"Nat Rev Neurol"},{"key":"key20200807035017_B12","doi-asserted-by":"crossref","first-page":"741","DOI":"10.1007\/s10072-018-3268-7","article-title":"Clinical spectrum of C9orf72 expansion in a cohort of Huntington\u2019s disease phenocopies","volume":"39","year":"2018","journal-title":"Neurol Sci"},{"key":"key20200807035017_B13","doi-asserted-by":"crossref","first-page":"280","DOI":"10.1055\/s-0034-1386766","article-title":"Genetic cerebellar ataxias","volume":"34","year":"2014","journal-title":"Semin Neurol"},{"key":"key20200807035017_B14","doi-asserted-by":"crossref","first-page":"170","DOI":"10.1007\/s12311-008-0016-1","article-title":"Spinocerebellar ataxia 17 (SCA17) and Huntington\u2019s disease-like 4 (HDL4)","volume":"7","year":"2008","journal-title":"Cerebellum"},{"key":"key20200807035017_B15","doi-asserted-by":"crossref","first-page":"1521","DOI":"10.1002\/mds.20529","article-title":"Spinocerebellar ataxia type 17: extension of phenotype with putaminal rim hyperintensity on magnetic resonance imaging","volume":"20","year":"2005","journal-title":"Mov Disord"},{"key":"key20200807035017_B16","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1016\/j.parkreldis.2018.05.021","article-title":"Huntington\u2019s disease-like disorders in Latin America and the Caribbean","volume":"53","year":"2018","journal-title":"Parkinsonism Relat Disord"},{"key":"key20200807035017_B17","doi-asserted-by":"crossref","first-page":"1527","DOI":"10.1002\/mds.10587","article-title":"Phenotypic features of Huntington\u2019s disease-like 2","volume":"18","year":"2003","journal-title":"Mov Disord"},{"key":"key20200807035017_B18","article-title":"Emerging differences between Huntington\u2019s disease-like 2 and Huntington\u2019s disease: A comparison using MRI brain volumetry","volume":"21","year":"2019","journal-title":"Neuroimage Clin"},{"key":"key20200807035017_B19","doi-asserted-by":"crossref","first-page":"37","DOI":"10.3233\/JHD-160232","article-title":"A Systematic Review of the Huntington Disease-Like 2 Phenotype","volume":"6","year":"2017","journal-title":"J Huntingtons Dis"},{"key":"key20200807035017_B20","doi-asserted-by":"crossref","first-page":"577","DOI":"10.5334\/tohm.439","article-title":"Dentatorubral-pallidoluysian Atrophy: An Update","volume":"8","year":"2018","journal-title":"Tremor Other Hyperkinet Mov (N Y)"},{"key":"key20200807035017_B21","doi-asserted-by":"crossref","first-page":"587","DOI":"10.1016\/B978-0-444-51892-7.00041-3","article-title":"Dentatorubral-pallidoluysian atrophy","volume":"103","year":"2012","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B22","doi-asserted-by":"crossref","first-page":"293","DOI":"10.1016\/B978-0-444-63233-3.00019-1","article-title":"Neurodegeneration with brain iron accumulation","volume":"147","year":"2018","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B23","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.nbd.2011.12.054","article-title":"Iron dysregulation in movement disorders","volume":"46","year":"2012","journal-title":"Neurobiol Dis"},{"key":"key20200807035017_B24","doi-asserted-by":"crossref","first-page":"1051","DOI":"10.3233\/JAD-180123","article-title":"Unusual Clinical Presentations Challenging the Early Clinical Diagnosis of Creutzfeldt-Jakob Disease","volume":"64","year":"2018","journal-title":"J Alzheimers Dis"},{"key":"key20200807035017_B25","doi-asserted-by":"crossref","first-page":"420","DOI":"10.1097\/WCO.0b013e3283632d90","article-title":"Huntington\u2019s disease and Huntington\u2019s disease-like syndromes: An overview","volume":"26","year":"2013","journal-title":"Curr Opin Neurol"},{"key":"key20200807035017_B26","doi-asserted-by":"crossref","first-page":"517","DOI":"10.1038\/ncpneuro0606","article-title":"The Huntington\u2019s disease-like syndromes: what to consider in patients with a negative Huntington\u2019s disease gene test","volume":"3","year":"2007","journal-title":"Nat Clin Pract Neurol"},{"key":"key20200807035017_B27","doi-asserted-by":"crossref","first-page":"149","DOI":"10.14802\/jmd.18017","article-title":"Chorea in Sporadic Creutzfeldt-Jakob Disease","volume":"11","year":"2018","journal-title":"J Mov Disord"},{"key":"key20200807035017_B28","doi-asserted-by":"crossref","first-page":"356","DOI":"10.1016\/j.jns.2014.09.050","article-title":"Should spinocerebellar ataxias be included in the differential diagnosis for Huntington\u2019s diseases-like syndromes?","volume":"347","year":"2014","journal-title":"Journal of the neurological sciences"},{"key":"key20200807035017_B29","doi-asserted-by":"crossref","first-page":"135","DOI":"10.1007\/978-3-319-71779-1_6","article-title":"Spinocerebellar Ataxia Type 1: Molecular Mechanisms of Neurodegeneration and Preclinical Studies","volume":"1049","year":"2018","journal-title":"Adv Exp Med Biol"},{"key":"key20200807035017_B30","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1007\/978-3-319-71779-1_8","article-title":"Spinocerebellar Ataxia Type 2","volume":"1049","year":"2018","journal-title":"Adv Exp Med Biol"},{"key":"key20200807035017_B31","doi-asserted-by":"crossref","first-page":"437","DOI":"10.1016\/B978-0-444-51892-7.00027-9","article-title":"Machado-Joseph disease\/spinocerebellar ataxia type 3","volume":"103","year":"2012","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B32","doi-asserted-by":"crossref","first-page":"650","DOI":"10.1136\/jnnp-2012-302532","article-title":"The differential diagnosis of Huntington\u2019s disease-like syndromes: \u2018red flags\u2019 for the clinician","volume":"84","year":"2013","journal-title":"Journal of neurology, neurosurgery, and psychiatry"},{"key":"key20200807035017_B33","doi-asserted-by":"crossref","first-page":"621","DOI":"10.1016\/j.parkreldis.2009.06.001","article-title":"Spinocerebellar ataxia 8: variable phenotype and unique pathogenesis","volume":"15","year":"2009","journal-title":"Parkinsonism Relat Disord"},{"key":"key20200807035017_B34","doi-asserted-by":"crossref","first-page":"274","DOI":"10.3988\/jcn.2013.9.4.274","article-title":"Non-Ataxic Phenotypes of SCA8 Mimicking Amyotrophic Lateral Sclerosis and Parkinson Disease","volume":"9","year":"2013","journal-title":"J Clin Neurol"},{"key":"key20200807035017_B35","doi-asserted-by":"crossref","first-page":"1248","DOI":"10.1002\/mds.26679","article-title":"Huntington\u2019s disease-like presentation in Spinocerebellar ataxia type 12","volume":"31","year":"2016","journal-title":"Mov Disord"},{"key":"key20200807035017_B36","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1016\/j.parkreldis.2019.05.001","article-title":"Spinocerebellar ataxia 48 presenting with ataxia associated with cognitive, psychiatric, and extrapyramidal features: A report of two Italian families","volume":"65","year":"2019","journal-title":"Parkinsonism Relat Disord"},{"key":"key20200807035017_B37","doi-asserted-by":"crossref","first-page":"1462","DOI":"10.1038\/s41431-018-0185-4","article-title":"Primary brain calcification: An international study reporting novel variants and associated phenotypes","volume":"26","year":"2018","journal-title":"Eur J Hum Genet"},{"key":"key20200807035017_B38","doi-asserted-by":"crossref","first-page":"3395","DOI":"10.1093\/brain\/awt255","article-title":"Phenotypic spectrum of probable and genetically-confirmed idiopathic basal ganglia calcification","volume":"136","year":"2013","journal-title":"Brain: A journal of neurology"},{"key":"key20200807035017_B39","doi-asserted-by":"crossref","first-page":"486","DOI":"10.1002\/ana.98","article-title":"Familial dyskinesia and facial myokymia (FDFM): A novel movement disorder","volume":"49","year":"2001","journal-title":"Ann Neurol"},{"key":"key20200807035017_B40","doi-asserted-by":"crossref","first-page":"512","DOI":"10.1002\/mdc3.12816","article-title":"ADCY5-Related Dyskinesia: Improving Clinical Detection of an Evolving Disorder","volume":"6","year":"2019","journal-title":"Mov Disord Clin Pract"},{"key":"key20200807035017_B41","doi-asserted-by":"crossref","first-page":"1033","DOI":"10.1002\/mds.26598","article-title":"Phenotypic insights into ADCY5-associated disease","volume":"31","year":"2016","journal-title":"Mov Disord"},{"key":"key20200807035017_B42","doi-asserted-by":"crossref","first-page":"80","DOI":"10.1212\/WNL.0000000000001720","article-title":"ADCY5 mutations are another cause of benign hereditary chorea","volume":"85","year":"2015","journal-title":"Neurology"},{"key":"key20200807035017_B43","doi-asserted-by":"crossref","first-page":"314","DOI":"10.5334\/tohm.269","article-title":"Benign Hereditary Chorea: An Update","volume":"5","year":"2015","journal-title":"Tremor Other Hyperkinet Mov (N Y)"},{"key":"key20200807035017_B44","doi-asserted-by":"crossref","first-page":"532","DOI":"10.1016\/j.pediatrneurol.2014.06.001","article-title":"Benign hereditary chorea: A case report and brief review of inherited choreas","volume":"51","year":"2014","journal-title":"Pediatr Neurol"},{"key":"key20200807035017_B45","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1002\/mdc3.12690","article-title":"Is Benign Hereditary Chorea Really Benign? Brain-Lung-Thyroid Syndrome Caused by NKX2-1 Mutations","volume":"6","year":"2019","journal-title":"Mov Disord Clin Pract"},{"key":"key20200807035017_B46","doi-asserted-by":"crossref","first-page":"956","DOI":"10.1136\/jnnp-2012-302505","article-title":"Benign hereditary chorea: Phenotype, prognosis, therapeutic outcome and long term follow-up in a large series with new mutations in the TITF1\/NKX2-1 gene","volume":"83","year":"2012","journal-title":"Journal of neurology, neurosurgery, and psychiatry"},{"key":"key20200807035017_B47","doi-asserted-by":"crossref","first-page":"1439","DOI":"10.1111\/dmcn.14332","article-title":"Expanding the phenotypic spectrum of Allan-Herndon-Dudley syndrome in patients with SLC16A2 mutations","volume":"61","year":"2019","journal-title":"Dev Med Child Neurol"},{"key":"key20200807035017_B48","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1002\/mds.870070119","article-title":"Chorea and tuberous sclerosis","volume":"7","year":"1992","journal-title":"Mov Disord"},{"key":"key20200807035017_B49","doi-asserted-by":"crossref","first-page":"458","DOI":"10.1002\/mds.24014","article-title":"Unilateral basal ganglia atrophy in a patient with tuberous sclerosis complex and hemichorea","volume":"27","year":"2012","journal-title":"Mov Disord"},{"key":"key20200807035017_B50","article-title":"Current state of knowledge in Chorea-Acanthocytosis as core Neuroacanthocytosis syndrome","year":"2017","journal-title":"Eur J Med Genet"},{"key":"key20200807035017_B51","doi-asserted-by":"crossref","first-page":"1255","DOI":"10.1002\/1531-8257(200011)15:6<1255::AID-MDS1031>3.0.CO;2-C","article-title":"Accuracy of clinical diagnostic criteria for Friedreich\u2019s ataxia","volume":"15","year":"2000","journal-title":"Mov Disord"},{"key":"key20200807035017_B52","doi-asserted-by":"crossref","first-page":"19","DOI":"10.1093\/bmb\/ldx034","article-title":"Friedreich\u2019s ataxia: Clinical features, pathogenesis and management","volume":"124","year":"2017","journal-title":"Br Med Bull"},{"key":"key20200807035017_B53","doi-asserted-by":"crossref","first-page":"585","DOI":"10.1002\/mds.10175","article-title":"Friedreich\u2019s ataxia with chorea and myoclonus caused by a compound heterozygosity for a novel deletion and the trinucleotide GAA expansion","volume":"17","year":"2002","journal-title":"Mov Disord"},{"key":"key20200807035017_B54","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1002\/mds.870130223","article-title":"Generalized chorea in two patients harboring the Friedreich\u2019s ataxia gene trinucleotide repeat expansion","volume":"13","year":"1998","journal-title":"Mov Disord"},{"key":"key20200807035017_B55","doi-asserted-by":"crossref","first-page":"e160816","DOI":"10.1001\/jamaophthalmol.2016.0816","article-title":"Aceruloplasminemia With Positive Ceruloplasm Gene Mutation","volume":"134","year":"2016","journal-title":"JAMA Ophthalmol"},{"key":"key20200807035017_B56","doi-asserted-by":"crossref","first-page":"445","DOI":"10.1086\/302744","article-title":"Localization of the gene for a novel autosomal recessive neurodegenerative Huntington-like disorder to 4p15.3","volume":"66","year":"2000","journal-title":"Am J Hum Genet"},{"key":"key20200807035017_B57","doi-asserted-by":"crossref","first-page":"417","DOI":"10.1016\/j.ncl.2020.01.005","article-title":"Wilson Disease: An Overview and Approach to Management","volume":"38","year":"2020","journal-title":"Neurol Clin"},{"key":"key20200807035017_B58","doi-asserted-by":"crossref","first-page":"178","DOI":"10.3174\/ajnr.A5936","article-title":"MR Imaging of the Brain in Neurologic Wilson Disease","volume":"40","year":"2019","journal-title":"AJNR Am J Neuroradiol"},{"key":"key20200807035017_B59","doi-asserted-by":"crossref","first-page":"103","DOI":"10.1016\/S1474-4422(14)70190-5","article-title":"Wilson\u2019s disease and other neurological copper disorders","volume":"14","year":"2015","journal-title":"Lancet Neurol"},{"key":"key20200807035017_B60","doi-asserted-by":"crossref","first-page":"3","DOI":"10.1016\/j.jns.2015.05.022","article-title":"Ataxia-telangiectasia \u2013 A historical review and a proposal for a new designation: ATM syndrome","volume":"355","year":"2015","journal-title":"Journal of the neurological sciences"},{"key":"key20200807035017_B61","doi-asserted-by":"crossref","first-page":"73","DOI":"10.1016\/B978-0-444-64189-2.00005-6","article-title":"Recessive ataxias","volume":"155","year":"2018","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B62","doi-asserted-by":"crossref","first-page":"293","DOI":"10.1055\/s-0034-1386767","article-title":"Hereditary spastic paraplegia: Clinical principles and genetic advances","volume":"34","year":"2014","journal-title":"Semin Neurol"},{"key":"key20200807035017_B63","doi-asserted-by":"crossref","first-page":"102","DOI":"10.1002\/acn3.511","article-title":"Xeroderma pigmentosum is a definite cause of Huntington\u2019s disease-like syndrome","volume":"5","year":"2018","journal-title":"Ann Clin Transl Neurol"},{"key":"key20200807035017_B64","doi-asserted-by":"crossref","first-page":"97","DOI":"10.1007\/s11910-017-0806-2","article-title":"Emerging Monogenic Complex Hyperkinetic Disorders","volume":"17","year":"2017","journal-title":"Current neurology and neuroscience reports"},{"key":"key20200807035017_B65","doi-asserted-by":"crossref","first-page":"239","DOI":"10.1016\/j.parkreldis.2019.01.017","article-title":"Neurodevelopmental disorder associated with IRF2BPL gene mutation: Expanding the phenotype?","volume":"62","year":"2019","journal-title":"Parkinsonism Relat Disord"},{"key":"key20200807035017_B66","article-title":"Molecular Basis and Clinical Overview of McLeod Syndrome Compared With Other Neuroacanthocytosis Syndromes: A Review","year":"2018","journal-title":"JAMA Neurol"},{"key":"key20200807035017_B67","doi-asserted-by":"crossref","first-page":"701","DOI":"10.1016\/B978-0-444-64076-5.00045-4","article-title":"Neurogenetics of Pelizaeus-Merzbacher disease","volume":"148","year":"2018","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B68","doi-asserted-by":"crossref","first-page":"332","DOI":"10.1002\/mdc3.12920","article-title":"A Family with Late-Onset and Predominant Choreic Niemann Pick Type C: A Treatable Piece in the Etiological Puzzle of Choreas","volume":"7","year":"2020","journal-title":"Mov Disord Clin Pract"},{"key":"key20200807035017_B69","doi-asserted-by":"crossref","first-page":"82","DOI":"10.1016\/j.spen.2018.02.003","article-title":"Movement Disorders and Neurometabolic Diseases","volume":"25","year":"2018","journal-title":"Semin Pediatr Neurol"},{"key":"key20200807035017_B70","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1002\/mds.27140","article-title":"Treatable inherited rare movement disorders","volume":"33","year":"2018","journal-title":"Mov Disord"},{"key":"key20200807035017_B71","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1016\/j.ymgme.2019.04.002","article-title":"Clinical and biochemical footprints of inherited metabolic diseases. II. Metabolic liver diseases","volume":"127","year":"2019","journal-title":"Mol Genet Metab"},{"key":"key20200807035017_B72","doi-asserted-by":"crossref","first-page":"598","DOI":"10.1002\/mds.27568","article-title":"Movement Disorders in Treatable Inborn Errors of Metabolism","volume":"34","year":"2019","journal-title":"Mov Disord"},{"key":"key20200807035017_B73","first-page":"441","article-title":"Clinical manifestation of mitochondrial diseases","volume":"19","year":"2015","journal-title":"Dev Period Med"},{"key":"key20200807035017_B74","doi-asserted-by":"crossref","first-page":"1230","DOI":"10.1007\/s00415-017-8722-6","article-title":"Movement disorders in mitochondrial disease","volume":"265","year":"2018","journal-title":"J Neurol"},{"key":"key20200807035017_B75","doi-asserted-by":"crossref","first-page":"524","DOI":"10.1016\/j.neurol.2016.07.003","article-title":"Movement disorders in mitochondrial diseases","volume":"172","year":"2016","journal-title":"Rev Neurol (Paris)"},{"key":"key20200807035017_B76","doi-asserted-by":"crossref","first-page":"625","DOI":"10.1002\/mds.27655","article-title":"Genetic mimics of cerebral palsy","volume":"34","year":"2019","journal-title":"Mov Disord"},{"key":"key20200807035017_B77","doi-asserted-by":"crossref","first-page":"278","DOI":"10.1136\/bmj.4.5730.278","article-title":"Choreoathetotic movement disorder in alcoholism","volume":"4","year":"1970","journal-title":"Br Med J"},{"key":"key20200807035017_B78","doi-asserted-by":"crossref","first-page":"427","DOI":"10.1053\/ajkd.2001.21337","article-title":"Chorea induced by thiamine deficiency in hemodialysis patients","volume":"37","year":"2001","journal-title":"Am J Kidney Dis"},{"key":"key20200807035017_B79","doi-asserted-by":"crossref","first-page":"335","DOI":"10.1016\/B978-0-444-52014-2.00026-4","article-title":"Chorea caused by toxins","volume":"100","year":"2011","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B80","doi-asserted-by":"crossref","first-page":"1073","DOI":"10.1016\/B978-0-7020-4087-0.00072-3","article-title":"Chronic myeloproliferative diseases","volume":"120","year":"2014","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B81","doi-asserted-by":"crossref","first-page":"106","DOI":"10.4103\/0972-2327.128569","article-title":"Essential thrombocythemia: Rare cause of chorea","volume":"17","year":"2014","journal-title":"Ann Indian Acad Neurol"},{"key":"key20200807035017_B82","doi-asserted-by":"crossref","first-page":"1133","DOI":"10.1212\/WNL.0b013e3182886991","article-title":"Autoimmune chorea in adults","volume":"80","year":"2013","journal-title":"Neurology"},{"key":"key20200807035017_B83","doi-asserted-by":"crossref","first-page":"94","DOI":"10.1016\/j.jns.2015.11.052","article-title":"Executive dysfunction, obsessive-compulsive symptoms, and attention deficit and hyperactivity disorder in Systemic Lupus Erythematosus: Evidence for basal ganglia dysfunction?","volume":"360","year":"2016","journal-title":"Journal of the neurological sciences"},{"key":"key20200807035017_B84","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1016\/j.jns.2017.12.035","article-title":"Autoimmune and paraneoplastic movement disorders: An update","volume":"385","year":"2018","journal-title":"Journal of the neurological sciences"},{"key":"key20200807035017_B85","doi-asserted-by":"crossref","first-page":"412","DOI":"10.1136\/jnnp-2016-314475","article-title":"Autoimmune choreas","volume":"88","year":"2017","journal-title":"Journal of neurology, neurosurgery, and psychiatry"},{"key":"key20200807035017_B86","doi-asserted-by":"crossref","first-page":"543","DOI":"10.1002\/mds.25354","article-title":"The spectrum of movement disorders in children with anti-NMDA receptor encephalitis","volume":"28","year":"2013","journal-title":"Mov Disord"},{"key":"key20200807035017_B87","doi-asserted-by":"crossref","first-page":"935","DOI":"10.1002\/mds.25011","article-title":"Movement disorders in autoimmune diseases","volume":"27","year":"2012","journal-title":"Mov Disord"},{"key":"key20200807035017_B88","doi-asserted-by":"crossref","first-page":"1235","DOI":"10.1016\/B978-0-444-52910-7.00046-5","article-title":"Immune-mediated extrapyramidal movement disorders, including Sydenham chorea","volume":"112","year":"2013","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B89","doi-asserted-by":"crossref","first-page":"391","DOI":"10.1016\/S1474-4422(15)00401-9","article-title":"A clinical approach to diagnosis of autoimmune encephalitis","volume":"15","year":"2016","journal-title":"Lancet Neurol"},{"key":"key20200807035017_B90","doi-asserted-by":"crossref","first-page":"840","DOI":"10.1056\/NEJMra1708712","article-title":"Antibody-Mediated Encephalitis","volume":"378","year":"2018","journal-title":"N Engl J Med"},{"key":"key20200807035017_B91","article-title":"Anti-NMDA receptor encephalitis associated with ovarian tumor: The gynecologist point of view","year":"2020","journal-title":"Arch Gynecol Obstet"},{"key":"key20200807035017_B92","doi-asserted-by":"crossref","first-page":"71","DOI":"10.7861\/clinmedicine.17-1-71","article-title":"Behcet\u2019s disease","volume":"17","year":"2017","journal-title":"Clin Med (Lond)"},{"key":"key20200807035017_B93","doi-asserted-by":"crossref","first-page":"235","DOI":"10.5152\/eurjrheum.2018.18033","article-title":"Clinical characteristics and prognosis of Neuro-Behcet\u2019s disease","volume":"5","year":"2018","journal-title":"Eur J Rheumatol"},{"key":"key20200807035017_B94","doi-asserted-by":"crossref","first-page":"32","DOI":"10.1097\/BOR.0000000000000562","article-title":"Nervous system involvement in Behcet\u2019s syndrome","volume":"31","year":"2019","journal-title":"Curr Opin Rheumatol"},{"key":"key20200807035017_B95","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1016\/j.autrev.2015.11.011","article-title":"Behcet disease presenting with movement disorders and antibasal ganglia antibodies","volume":"15","year":"2016","journal-title":"Autoimmun Rev"},{"key":"key20200807035017_B96","doi-asserted-by":"crossref","first-page":"398","DOI":"10.1016\/j.parkreldis.2008.06.007","article-title":"Bilateral basal ganglia lesions of primary Sjogren syndrome presenting with generalized chorea","volume":"15","year":"2009","journal-title":"Parkinsonism Relat Disord"},{"key":"key20200807035017_B97","doi-asserted-by":"crossref","first-page":"389","DOI":"10.1097\/RHU.0b013e318277369e","article-title":"Neurosjogren: Early therapy is associated with successful outcomes","volume":"18","year":"2012","journal-title":"J Clin Rheumatol"},{"key":"key20200807035017_B98","doi-asserted-by":"crossref","first-page":"647","DOI":"10.1001\/jama.2017.9730","article-title":"Celiac Disease and Nonceliac Gluten Sensitivity: A Review","volume":"318","year":"2017","journal-title":"JAMA"},{"key":"key20200807035017_B99","doi-asserted-by":"crossref","first-page":"8","DOI":"10.1016\/j.clineuro.2015.07.009","article-title":"Gluten chorea","volume":"138","year":"2015","journal-title":"Clin Neurol Neurosurg"},{"key":"key20200807035017_B100","article-title":"Further Evidence for Celiac Disease-associated Chorea","volume":"1","year":"2011","journal-title":"Tremor Other Hyperkinet Mov (N Y)"},{"key":"key20200807035017_B101","doi-asserted-by":"crossref","first-page":"1736","DOI":"10.1212\/WNL.0000000000003887","article-title":"Clinical manifestations of the anti-IgLON5 disease","volume":"88","year":"2017","journal-title":"Neurology"},{"key":"key20200807035017_B102","doi-asserted-by":"crossref","first-page":"90","DOI":"10.1111\/apha.12614","article-title":"Autoimmunity against dopamine receptors in neuropsychiatric and movement disorders: a review of Sydenham chorea and beyond","volume":"216","year":"2016","journal-title":"Acta Physiol (Oxf)"},{"key":"key20200807035017_B103","doi-asserted-by":"crossref","first-page":"496","DOI":"10.1097\/WCO.0000000000000351","article-title":"Stiff person syndrome and other immune-mediated movement disorders \u2013 new insights","volume":"29","year":"2016","journal-title":"Curr Opin Neurol"},{"key":"key20200807035017_B104","doi-asserted-by":"crossref","first-page":"839","DOI":"10.1152\/physrev.00010.2016","article-title":"Autoantibodies to Synaptic Receptors and Neuronal Cell Surface Proteins in Autoimmune Diseases of the Central Nervous System","volume":"97","year":"2017","journal-title":"Physiol Rev"},{"key":"key20200807035017_B105","doi-asserted-by":"crossref","first-page":"279","DOI":"10.1016\/B978-0-444-52014-2.00020-3","article-title":"Hyperthyroid chorea","volume":"100","year":"2011","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B106","doi-asserted-by":"crossref","first-page":"e616","DOI":"10.1542\/peds.2012-0686","article-title":"Rising serum thyroxine levels and chorea in graves\u2019 disease","volume":"131","year":"2013","journal-title":"Pediatrics"},{"key":"key20200807035017_B107","doi-asserted-by":"crossref","first-page":"589","DOI":"10.1016\/S1474-4422(06)70494-X","article-title":"Seminar on choreas","volume":"5","year":"2006","journal-title":"Lancet Neurol"},{"key":"key20200807035017_B108","doi-asserted-by":"crossref","first-page":"840","DOI":"10.1016\/j.braindev.2012.01.014","article-title":"Exacerbation of idiopathic paroxysmal kinesigenic dyskinesia in remission state caused by secondary hypoparathyroidism with hypocalcemia after thyroidectomy: Evidence for ion channelopathy","volume":"34","year":"2012","journal-title":"Brain Dev"},{"key":"key20200807035017_B109","doi-asserted-by":"crossref","first-page":"560","DOI":"10.1136\/pgmj.55.646.560","article-title":"Hypocalcaemic chorea secondary to malabsorption","volume":"55","year":"1979","journal-title":"Postgrad Med J"},{"key":"key20200807035017_B110","doi-asserted-by":"crossref","first-page":"343","DOI":"10.1111\/j.1445-5994.1998.tb01959.x","article-title":"Hypocalcaemic chorea secondary to malabsorption","volume":"28","year":"1998","journal-title":"Aust N Z J Med"},{"key":"key20200807035017_B111","doi-asserted-by":"crossref","first-page":"2026","DOI":"10.1002\/mds.21094","article-title":"Hypocalcemic choreoathetosis and tetany after bisphosphonate treatment","volume":"21","year":"2006","journal-title":"Mov Disord"},{"key":"key20200807035017_B112","doi-asserted-by":"crossref","first-page":"46","DOI":"10.1212\/WNL.26.1.46","article-title":"Hypernatremia and chorea. A report of two cases","volume":"26","year":"1976","journal-title":"Neurology"},{"key":"key20200807035017_B113","first-page":"343","article-title":"Movement disorders identified in patients with intracranial tuberculomas","volume":"26","year":"2011","journal-title":"Neurologia"},{"key":"key20200807035017_B114","first-page":"215","article-title":"Abnormal movements in a case of extrapontine myelinolysis. Review of the literature","volume":"26","year":"1998","journal-title":"Rev Neurol"},{"key":"key20200807035017_B115","first-page":"89","article-title":"Osmotic Demyelination Syndrome Presenting with Chorea","volume":"64","year":"2016","journal-title":"J Assoc Physicians India"},{"key":"key20200807035017_B116","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1002\/mds.870060215","article-title":"Delayed onset movement disorders as a complication of central pontine myelinolysis","volume":"6","year":"1991","journal-title":"Mov Disord"},{"key":"key20200807035017_B117","doi-asserted-by":"crossref","first-page":"419","DOI":"10.1002\/mds.26148","article-title":"Chorea due to diabetic hyperglycemia and uremia: Distinct clinical and imaging features","volume":"30","year":"2015","journal-title":"Mov Disord"},{"key":"key20200807035017_B118","article-title":"Neurologic conditions and disorders of uremic syndrome of chronic kidney disease: Presentations, causes and treatment strategies","year":"2018","journal-title":"Expert Rev Clin Pharmacol"},{"key":"key20200807035017_B119","doi-asserted-by":"crossref","first-page":"347","DOI":"10.1007\/s11011-017-0107-0","article-title":"Acquired hepatocerebral degeneration (AHD): A peculiar neurological impairment in advanced chronic liver disease","volume":"33","year":"2018","journal-title":"Metab Brain Dis"},{"key":"key20200807035017_B120","doi-asserted-by":"crossref","first-page":"463","DOI":"10.5334\/tohm.379","article-title":"Recent Updates on Acquired Hepatocerebral Degeneration","volume":"7","year":"2017","journal-title":"Tremor Other Hyperkinet Mov (N Y)"},{"key":"key20200807035017_B121","doi-asserted-by":"crossref","first-page":"e144","DOI":"10.1212\/WNL.0000000000003153","article-title":"Teaching NeuroImages: Acquired hepatocerebral degeneration: An underrecognized complication of advanced liver disease","volume":"87","year":"2016","journal-title":"Neurology"},{"key":"key20200807035017_B122","doi-asserted-by":"crossref","first-page":"387","DOI":"10.1016\/B978-0-444-52014-2.00030-6","article-title":"Birth-related syndromes of athetosis and kernicterus","volume":"100","year":"2011","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B123","doi-asserted-by":"crossref","first-page":"226","DOI":"10.1111\/j.1468-1331.2011.03469.x","article-title":"A clinical profile of 103 patients with secondary movement disorders: correlation of etiology with phenomenology","volume":"19","year":"2012","journal-title":"Eur J Neurol"},{"key":"key20200807035017_B124","doi-asserted-by":"crossref","first-page":"20","DOI":"10.1016\/j.siny.2014.11.002","article-title":"Movement disorders due to bilirubin toxicity","volume":"20","year":"2015","journal-title":"Semin Fetal Neonatal Med"},{"key":"key20200807035017_B125","doi-asserted-by":"crossref","first-page":"2","DOI":"10.1016\/j.parkreldis.2018.09.006","article-title":"Simultaneous acute presentation of generalized chorea and subacute combined degeneration secondary to vitamin B12 deficiency","volume":"55","year":"2018","journal-title":"Parkinsonism Relat Disord"},{"key":"key20200807035017_B126","doi-asserted-by":"crossref","first-page":"200","DOI":"10.1016\/j.mayocpiqo.2019.03.002","article-title":"The Many Faces of Cobalamin (Vitamin B12) Deficiency","volume":"3","year":"2019","journal-title":"Mayo Clin Proc Innov Qual Outcomes"},{"key":"key20200807035017_B127","doi-asserted-by":"crossref","first-page":"e138","DOI":"10.1111\/j.1468-1331.2011.03478.x","article-title":"Chorea associated with vitamin B12 deficiency","volume":"18","year":"2011","journal-title":"Eur J Neurol"},{"key":"key20200807035017_B128","doi-asserted-by":"crossref","first-page":"370","DOI":"10.1590\/s1980-5764-2016dn1004020","article-title":"Wernicke\u2019s encephalopathy with chorea: Neuroimaging findings","volume":"10","year":"2016","journal-title":"Dement Neuropsychol"},{"key":"key20200807035017_B129","doi-asserted-by":"crossref","first-page":"418","DOI":"10.1002\/mds.870100403","article-title":"Movement disorders in multiple sclerosis","volume":"10","year":"1995","journal-title":"Mov Disord"},{"key":"key20200807035017_B130","doi-asserted-by":"crossref","first-page":"31","DOI":"10.2217\/nmt-2016-0053","article-title":"Movement disorders in multiple sclerosis and their treatment","volume":"6","year":"2016","journal-title":"Neurodegener Dis Manag"},{"key":"key20200807035017_B131","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/j.jns.2013.02.007","article-title":"Movement disorders in multiple sclerosis and other demyelinating diseases","volume":"328","year":"2013","journal-title":"Journal of the neurological sciences"},{"key":"key20200807035017_B132","doi-asserted-by":"crossref","first-page":"2058","DOI":"10.1007\/s00415-011-6074-1","article-title":"Chorea and related movement disorders of paraneoplastic origin: The PNS EuroNetwork experience","volume":"258","year":"2011","journal-title":"J Neurol"},{"key":"key20200807035017_B133","first-page":"452","article-title":"Paraneoplastic disorders","volume":"21","year":"2015","journal-title":"Continuum (Minneap Minn)"},{"key":"key20200807035017_B134","first-page":"e3097","article-title":"P\/Q and N-type Voltage-gated Calcium Channel Binding Antibodies Associated with Paraneoplastic Chorea and Mixed Invasive Ductal and Lobular Carcinoma of the Breasts in an Elderly Patient","volume":"10","year":"2018","journal-title":"Cureus"},{"key":"key20200807035017_B135","doi-asserted-by":"crossref","first-page":"285","DOI":"10.1007\/s11910-009-0043-4","article-title":"Paraneoplastic movement disorders","volume":"9","year":"2009","journal-title":"Current neurology and neuroscience reports"},{"key":"key20200807035017_B136","first-page":"428","article-title":"Chorea\u2013a rare complication of enteric fever","volume":"30","year":"1993","journal-title":"Indian Pediatr"},{"key":"key20200807035017_B137","doi-asserted-by":"crossref","first-page":"1232","DOI":"10.1136\/bmj.284.6324.1232","article-title":"Chorea after legionnaire\u2019s disease","volume":"284","year":"1982","journal-title":"Br Med J (Clin Res Ed)"},{"key":"key20200807035017_B138","doi-asserted-by":"crossref","first-page":"561","DOI":"10.1002\/1531-8257(200005)15:3<561::AID-MDS1021>3.0.CO;2-K","article-title":"Movement disorders in 30 patients with tuberculous meningitis","volume":"15","year":"2000","journal-title":"Mov Disord"},{"key":"key20200807035017_B139","doi-asserted-by":"crossref","first-page":"254","DOI":"10.1590\/0004-282X20130230","article-title":"Hemichorea in tuberculous meningitis","volume":"72","year":"2014","journal-title":"Arq Neuropsiquiatr"},{"key":"key20200807035017_B140","doi-asserted-by":"crossref","first-page":"1375","DOI":"10.1016\/S0196-0644(94)70365-5","article-title":"Choreoathetotic movement disorder in a boy with Mycoplasma pneumoniae encephalitis","volume":"23","year":"1994","journal-title":"Ann Emerg Med"},{"key":"key20200807035017_B141","first-page":"30","article-title":"Movement disorders in adult-onset measles encephalitis","volume":"18","year":"2003","journal-title":"Neurologia"},{"key":"key20200807035017_B142","doi-asserted-by":"crossref","first-page":"404","DOI":"10.1007\/BF00386059","article-title":"Hemichorea associated with varicella-zoster reinfection and endocarditis. A case report","volume":"234","year":"1985","journal-title":"Eur Arch Psychiatry Neurol Sci"},{"key":"key20200807035017_B143","doi-asserted-by":"crossref","first-page":"591","DOI":"10.5334\/tohm.422","article-title":"Transient Generalized Chorea in Influenza A Encephalopathy","volume":"8","year":"2018","journal-title":"Tremor Other Hyperkinet Mov (N Y)"},{"key":"key20200807035017_B144","doi-asserted-by":"crossref","first-page":"676","DOI":"10.1212\/WNL.29.5.676","article-title":"ECHO 25 focal encephalitis and subacute hemichorea","volume":"29","year":"1979","journal-title":"Neurology"},{"key":"key20200807035017_B145","doi-asserted-by":"crossref","first-page":"341","DOI":"10.1016\/0887-8994(94)90014-0","article-title":"Choreoathetosis as an initial sign of relapsing of herpes simplex encephalitis","volume":"11","year":"1994","journal-title":"Pediatr Neurol"},{"key":"key20200807035017_B146","doi-asserted-by":"crossref","first-page":"186","DOI":"10.1001\/archneur.1986.00520020072025","article-title":"Unusual acute neurologic presentations with Epstein-Barr virus infection","volume":"43","year":"1986","journal-title":"Arch Neurol"},{"key":"key20200807035017_B147","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1016\/j.jns.2012.11.007","article-title":"Clinical and radiological spectrum of Japanese encephalitis","volume":"325","year":"2013","journal-title":"Journal of the neurological sciences"},{"key":"key20200807035017_B148","doi-asserted-by":"crossref","first-page":"1544","DOI":"10.3201\/eid1909.130804","article-title":"Chorea and tick-borne encephalitis, Poland","volume":"19","year":"2013","journal-title":"Emerg Infect Dis"},{"key":"key20200807035017_B149","doi-asserted-by":"crossref","first-page":"714","DOI":"10.1016\/j.bbadis.2008.08.001","article-title":"Viral parkinsonism","volume":"1792","year":"2009","journal-title":"Biochim Biophys Acta"},{"key":"key20200807035017_B150","doi-asserted-by":"crossref","first-page":"323","DOI":"10.1016\/B978-0-444-52014-2.00025-2","article-title":"Hyperkinetic movement disorders associated with HIV and other viral infections","volume":"100","year":"2011","journal-title":"Handb Clin Neurol"},{"key":"key20200807035017_B151","doi-asserted-by":"crossref","first-page":"347","DOI":"10.4103\/0028-3886.53277","article-title":"Chorea as the presenting feature of neurosyphilis","volume":"57","year":"2009","journal-title":"Neurol India"},{"key":"key20200807035017_B152","doi-asserted-by":"crossref","first-page":"246","DOI":"10.1002\/mds.25281","article-title":"Neurosyphilis orofacial dyskinesia: The candy sign","volume":"28","year":"2013","journal-title":"Mov Disord"},{"key":"key20200807035017_B153","doi-asserted-by":"crossref","first-page":"235","DOI":"10.1007\/BF02427611","article-title":"Chorea as a symptom of neuroborreliosis: A case study","volume":"19","year":"1998","journal-title":"Ital J Neurol Sci"},{"key":"key20200807035017_B154","doi-asserted-by":"crossref","first-page":"737","DOI":"10.1016\/S0022-3476(05)81365-4","article-title":"Choreoathetosis after surgery for congenital heart disease","volume":"124","year":"1994","journal-title":"J Pediatr"},{"key":"key20200807035017_B155","doi-asserted-by":"crossref","first-page":"390","DOI":"10.1016\/j.ejpn.2011.04.005","article-title":"Movement disorder emergencies in childhood","volume":"15","year":"2011","journal-title":"Eur J Paediatr Neurol"},{"key":"key20200807035017_B156","doi-asserted-by":"crossref","first-page":"1457","DOI":"10.1136\/jnnp.51.11.1457-a","article-title":"Chorea: A new manifestation of mastocytosis","volume":"51","year":"1988","journal-title":"Journal of neurology, neurosurgery, and psychiatry"},{"key":"key20200807035017_B157","doi-asserted-by":"crossref","first-page":"451","DOI":"10.1111\/j.1346-8138.2001.tb00009.x","article-title":"A case of mastocytosis with chorea","volume":"28","year":"2001","journal-title":"J Dermatol"},{"key":"key20200807035017_B158","doi-asserted-by":"crossref","first-page":"653","DOI":"10.1055\/s-0037-1608845","article-title":"Movement Disorders in Women","volume":"37","year":"2017","journal-title":"Semin Neurol"},{"key":"key20200807035017_B159","doi-asserted-by":"crossref","first-page":"231","DOI":"10.1016\/B978-0-444-52014-2.00015-X","article-title":"Chorea gravidarum","volume":"100","year":"2011","journal-title":"Handb Clin Neurol"}],"container-title":["Tremor and Other Hyperkinetic Movements"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/doi.org\/10.5334\/tohm.548","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,7,11]],"date-time":"2022-07-11T09:25:05Z","timestamp":1657531505000},"score":1,"resource":{"primary":{"URL":"https:\/\/tremorjournal.org\/articles\/10.5334\/tohm.548\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020]]},"references-count":159,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2020,8,6]]}},"alternative-id":["10.5334\/tohm.548"],"URL":"https:\/\/doi.org\/10.5334\/tohm.548","relation":{},"ISSN":["2160-8288"],"issn-type":[{"value":"2160-8288","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020]]},"article-number":"24"}}