{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,27]],"date-time":"2026-02-27T13:25:24Z","timestamp":1772198724986,"version":"3.50.1"},"reference-count":24,"publisher":"Georg Thieme Verlag KG","issue":"02","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Hamostaseologie"],"published-print":{"date-parts":[[2017]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p>National Patient Registries (NPR) have an important role in the management of haemophilia and other inherited bleeding disorders, representing powerful instruments to support healthcare and research. Computer software to assist the NPR is crucial, as it facilitates the introduction of the data from a national universe that will be centralized and merged into a unique location, thus ensuring a greater reliability and accuracy of the collected data, avoiding duplication of patients. In Portugal, despite the efforts and recognition of the need of a NPR, just recently the protocol for the establishment of the computer software to support the Portuguese National Registry of Haemophilia and other Congenital Coagulopathies (PorR H&amp;CC) was approved. This paper aims to present this newly developed computerized solution, as well as to report the main variables and information that will be available. The development of this application, which includes a set of sociodemographic, clinical and treatment data, was based on the principles of WFH, and the database that supports the NPR, with anonymized data, is operated and maintained in accordance with the Data Protection Law. Currently, the first data are available on the application. Our focus now is to ensure more registries and continuous data entry in order to have complete information on the characterization of the haemophilia patient population in Portugal.<\/jats:p>","DOI":"10.5482\/hamo-15-09-0027","type":"journal-article","created":{"date-parts":[[2016,2,11]],"date-time":"2016-02-11T13:52:27Z","timestamp":1455198747000},"page":"131-137","source":"Crossref","is-referenced-by-count":5,"title":["Portuguese Haemophilia Registry"],"prefix":"10.5482","volume":"37","author":[{"given":"Vasco","family":"Saavedra","sequence":"first","affiliation":[]},{"given":"Beatriz","family":"Santos","sequence":"first","affiliation":[]},{"given":"Carlos","family":"Ferreira","sequence":"first","affiliation":[]},{"given":"Leonor","family":"Teixeira","sequence":"additional","affiliation":[]}],"member":"194","published-online":{"date-parts":[[2017,12,28]]},"reference":[{"key":"10.5482\/HAMO-15-09-0027-1","unstructured":"Evatt B. World Federation of Hemophilia Guide to Developing a National Patient Registry. Montr\u00e9al - Qu\u00e9bec 2005"},{"key":"10.5482\/HAMO-15-09-0027-2","unstructured":"World Federation of Hemophilia. World Federation of Hemophilia Report on the ANNUAL GLOBAL SURVEY 2011. Montr\u00e9al - Qu\u00e9bec 2012"},{"key":"10.5482\/HAMO-15-09-0027-3","doi-asserted-by":"publisher","DOI":"10.1046\/j.1537-2995.1995.35795357873.x"},{"key":"10.5482\/HAMO-15-09-0027-4","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2007.01625.x"},{"key":"10.5482\/HAMO-15-09-0027-5","doi-asserted-by":"publisher","DOI":"10.1111\/hae.12406"},{"key":"10.5482\/HAMO-15-09-0027-6","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2008.01907.x"},{"key":"10.5482\/HAMO-15-09-0027-7","doi-asserted-by":"publisher","DOI":"10.1002\/cpt.83"},{"key":"10.5482\/HAMO-15-09-0027-8","doi-asserted-by":"publisher","DOI":"10.1111\/hae.12125"},{"key":"10.5482\/HAMO-15-09-0027-9","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1055\/s-0037-1617212","volume":"29","author":"Reitter","year":"2009","journal-title":"H\u00e4mostaseologie"},{"key":"10.5482\/HAMO-15-09-0027-10","doi-asserted-by":"publisher","DOI":"10.1007\/s00508-009-1156-0"},{"key":"10.5482\/HAMO-15-09-0027-11","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2008.01679.x"},{"key":"10.5482\/HAMO-15-09-0027-12","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2008.01921.x"},{"key":"10.5482\/HAMO-15-09-0027-13","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2009.02101.x"},{"key":"10.5482\/HAMO-15-09-0027-14","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2010.02371.x"},{"key":"10.5482\/HAMO-15-09-0027-15","doi-asserted-by":"crossref","first-page":"S20","DOI":"10.1055\/s-0037-1619770","volume":"32","author":"Von","year":"2012","journal-title":"H\u00e4mostaseologie"},{"issue":"Suppl 1","key":"10.5482\/HAMO-15-09-0027-16","doi-asserted-by":"crossref","first-page":"S16","DOI":"10.1055\/s-0037-1617205","volume":"29","author":"Brand","year":"2009","journal-title":"H\u00e4mostaseologie"},{"key":"10.5482\/HAMO-15-09-0027-17","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2004.00962.x"},{"key":"10.5482\/HAMO-15-09-0027-18","doi-asserted-by":"crossref","first-page":"S15","DOI":"10.1055\/s-0037-1619799","volume":"33","author":"Hesse","year":"2013","journal-title":"H\u00e4mostaseologie"},{"key":"10.5482\/HAMO-15-09-0027-19","doi-asserted-by":"crossref","first-page":"12","DOI":"10.1055\/s-0037-1617109","volume":"28","author":"Haschberger","year":"2008","journal-title":"H\u00e4mostaseologie"},{"key":"10.5482\/HAMO-15-09-0027-20","doi-asserted-by":"crossref","unstructured":"Teixeira L, Saavedra V, Ferreira C et al. Requirements engineering using mockups and prototyping tools: developing an healthcare web-application. In: Yamamoto S, editor. HCI International. Creta: Springer International Publishing Switzerland 2014: 652-663","DOI":"10.1007\/978-3-319-07731-4_64"},{"key":"10.5482\/HAMO-15-09-0027-21","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2011.02574.x"},{"key":"10.5482\/HAMO-15-09-0027-22","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2516.2004.00995.x"},{"key":"10.5482\/HAMO-15-09-0027-23","doi-asserted-by":"publisher","DOI":"10.1186\/1472-6947-13-113"},{"key":"10.5482\/HAMO-15-09-0027-24","doi-asserted-by":"crossref","unstructured":"Teixeira L, Ferreira C, Santos BS, Martins N. Modeling a Web-based Information System for managing clinical information in hemophilia care. In: Annual International Conference of the IEEE Engineering in Medicine and Biology Society IEEE Engineering in Medicine and Biology Society Conference 2006: 2610-2613","DOI":"10.1109\/IEMBS.2006.259679"}],"container-title":["H\u00e4mostaseologie"],"original-title":[],"language":"de","link":[{"URL":"http:\/\/www.thieme-connect.de\/products\/ejournals\/pdf\/10.5482\/HAMO-15-09-0027.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,9,4]],"date-time":"2019-09-04T12:52:38Z","timestamp":1567601558000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.thieme-connect.de\/DOI\/DOI?10.5482\/HAMO-15-09-0027"}},"subtitle":["Set of variables for a computerized solution"],"short-title":[],"issued":{"date-parts":[[2017]]},"references-count":24,"journal-issue":{"issue":"02","published-online":{"date-parts":[[2017,11,20]]},"published-print":{"date-parts":[[2017]]}},"URL":"https:\/\/doi.org\/10.5482\/hamo-15-09-0027","relation":{},"ISSN":["0720-9355","2567-5761"],"issn-type":[{"value":"0720-9355","type":"print"},{"value":"2567-5761","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017]]}}}