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Suraweera A, Becherel OJ, Chen P, Rundle N, Woods R, Nakamura J, Gatei M, Criscuolo C, Filla A, Chessa L, Fusser M, Epe B, Gueven N, Lavin MF. Senataxin, defective in ataxia oculomotor apraxia type 2, is involved in the defense against oxidative DNA damage. J Cell Biol. 2007; 177:969-979.","DOI":"10.1083\/jcb.200701042"},{"key":"6","doi-asserted-by":"crossref","unstructured":"6. Vantaggiato C, Cantoni O, Guidarelli A, Romaniello R, Citterio A, Arrigoni F, Doneda C5, Castelli M, Airoldi G, Bresolin N, Borgatti R, Bassi MT. Novel SETX variants in a patient with ataxia, neuropathy, and oculomotor apraxia are associated with normal sensitivity to oxidative DNA damaging agents. Brain Dev. 2014; 36:682-689.","DOI":"10.1016\/j.braindev.2013.10.003"},{"key":"7","doi-asserted-by":"crossref","unstructured":"7. Fogel BL, Cho E, Wahnich A, <i>et al<\/i>. Mutation of senataxin alters disease-specific transcriptional networks in patients with ataxia with oculomotor apraxia type 2. 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