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The relationship between complement levels and disease activity in Japanese family cases of hereditary angioedema with C1-INH deficiency. Allergol Int. 2018; 67:518-520.","DOI":"10.1016\/j.alit.2018.03.002"},{"key":"6","doi-asserted-by":"crossref","unstructured":"6. Bork K, Hardt J, Witzke G. Fatal laryngeal attacks and mortality in hereditary angioedema due to C1-INH deficiency. J Allergy Clin Immunol. 2012; 130:692-697.","DOI":"10.1016\/j.jaci.2012.05.055"},{"key":"7","doi-asserted-by":"crossref","unstructured":"7. Honda D, Ohsawa I, Shimizu Y, Maiguma M, Hidaka T, Suzuki H, Io H, Mano S, Takahara H, Rinno H, Tomino Y, Suzuki Y. Suffocation due to acute airway edema in a patient with hereditary angioedema highlighted the need for urgent improvements in treatment availability in Japan. Intern Med. 2018; 57:3193-3197.","DOI":"10.2169\/internalmedicine.9262-17"},{"key":"8","doi-asserted-by":"crossref","unstructured":"8. Ohsawa I, Honda D, Nagamachi S, Hisada A, Shimamoto M, Inoshita H, Mano S, Tomino Y. Clinical manifestations, diagnosis, and treatment of hereditary angioedema: survey data from 94 physicians in Japan. Ann Allergy Asthma Immunol. 2015; 114:492-498.","DOI":"10.1016\/j.anai.2015.03.010"},{"key":"9","doi-asserted-by":"crossref","unstructured":"9. Maurer M, Magerl M, Ansotegui I, <i>et al.<\/i> The international WAO\/EAACI guideline for the management of hereditary angioedema \u2013 the 2017 revision and update. Allergy. 2018; 73:1575-1596.","DOI":"10.1111\/all.13384"},{"key":"10","unstructured":"10. Horiuchi T, Ohsawa I, Okada, H, <i>et al.<\/i> Hereditary Angioedema (HAE) Guidelines - Revised 2014 Edition. Created by the Japanese Association for Complement Research <i>http:\/\/square.umin.ac.jp\/compl\/common\/images\/disease-information\/hae\/HAEGuideline2014.pdf<\/i> (accessed October 7, 2010). (in Japanese)"},{"key":"11","doi-asserted-by":"crossref","unstructured":"11. Ohsawa I, Honda D, Nagamachi S, Hisada A, Shimamoto M, Inoshita H, Mano S, Tomino Y. Clinical and laboratory characteristics that differentiate hereditary angioedema in 72 patients with angioedema. Allergol Int. 2014; 63:595-602.","DOI":"10.2332\/allergolint.14-OA-0700"},{"key":"12","doi-asserted-by":"crossref","unstructured":"12. Honda D, Ohsawa I, Sato N, Inoshita H, Mano S, Tomino Y, Suzuki Y. Diminished capacity of opsonization and immune complex solubilization, and detection of anti-C1q antibodies in sera from patients with hereditary angioedema. Allergol Int. 2017; 66:603-609.","DOI":"10.1016\/j.alit.2017.03.008"},{"key":"13","unstructured":"13. Serum immunological test, C1 esterase inhibitor activity, SRL, Japan. <i>https:\/\/test-guide.srl.info\/hachioji\/test\/detail\/011656409<\/i> (accessed October 7, 2010). (in Japanese)"},{"key":"14","doi-asserted-by":"crossref","unstructured":"14. Brackertz D, Isler E, Kueppers F. Half-life of Cl-INH in hereditary angioneurotic oedema (HAE). Clin Allergy. 1975; 1:89-94.","DOI":"10.1111\/j.1365-2222.1975.tb01839.x"},{"key":"15","unstructured":"15. Caliezi C, Wuillemin WA, Zeerleder S, Redondo M, Eisele B, Hack CE. C1-Esterase inhibitor: an anti-inflammatory agent and its potential use in the treatment of diseases other than hereditary angioedema. Pharmacol Rev. 2000; 52:91-112."},{"key":"16","doi-asserted-by":"crossref","unstructured":"16. Ohsawa I, Honda D, Hisada A, Inoshita H, Onda-Tsueshita K, Mano S, Sato N, Nakamura Y, Shimizu T, Gotoh H, Goto Y, Suzuki Y, Tomino Y. Clinical features of hereditary and mast cell-mediated angioedema focusing on the differential diagnosis in Japanese patients. Intern Med. 2018; 57:319-324.","DOI":"10.2169\/internalmedicine.8624-16"},{"key":"17","doi-asserted-by":"crossref","unstructured":"17. Bork K, Wulff K, Witzke G, Stanger C, Lohse P, Hardt J. Antihistamine-resistant angioedema in women with negative family history: estrogens and F12 gene mutations. Am J Med. 2013; 126:1142.e9-14.","DOI":"10.1016\/j.amjmed.2013.05.017"},{"key":"18","unstructured":"18. Package insert, berichrom C1 inhibitor, SYSMEX. <i>https:\/\/sysmex-support.com\/jp\/section\/coagulation\/package_insert<\/i> (accessed October 7, 2010). 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