{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,18]],"date-time":"2026-05-18T11:51:02Z","timestamp":1779105062284,"version":"3.51.4"},"reference-count":31,"publisher":"Elsevier BV","license":[{"start":{"date-parts":[[2018,1,1]],"date-time":"2018-01-01T00:00:00Z","timestamp":1514764800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2018,1,1]],"date-time":"2018-01-01T00:00:00Z","timestamp":1514764800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"},{"start":{"date-parts":[[2018,12,31]],"date-time":"2018-12-31T00:00:00Z","timestamp":1546214400000},"content-version":"vor","delay-in-days":364,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Clinics"],"published-print":{"date-parts":[[2018]]},"DOI":"10.6061\/clinics\/2018\/e523","type":"journal-article","created":{"date-parts":[[2018,12,2]],"date-time":"2018-12-02T07:55:12Z","timestamp":1543737312000},"page":"e523","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":17,"special_numbering":"C","title":["Audiometric evaluation in individuals with mucopolysaccharidosis"],"prefix":"10.1016","volume":"73","author":[{"given":"Marcela Rosana Maia","family":"da Silveira","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ana Karina Lima","family":"Buriti","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ana Maria","family":"Martins","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Daniela","family":"Gil","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marisa Frasson","family":"de Azevedo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"issue":"8","key":"10.6061\/clinics\/2018\/e523_bib1","first-page":"48","article-title":"Morquio\u2019s syndrome. A case report and review of clinical findings","volume":"64","author":"Fitzgerald","year":"1998","journal-title":"N Y State Dent J"},{"key":"10.6061\/clinics\/2018\/e523_bib2","series-title":"Cecil Textbook of Medicine","first-page":"1116","author":"Goldman","year":"1999"},{"issue":"3","key":"10.6061\/clinics\/2018\/e523_bib3","doi-asserted-by":"crossref","first-page":"310","DOI":"10.1002\/ajmg.a.20314","article-title":"Incidence of the Mucopolysaccharidoses in Western Australia","volume":"123A","author":"Nelson","year":"2003","journal-title":"Am J Med Genet"},{"issue":"6","key":"10.6061\/clinics\/2018\/e523_bib4","first-page":"471","article-title":"Datos diagnostico sen la enfermedad de Morquio","volume":"26","author":"Redondo","year":"1987","journal-title":"An Esp de Pediatr"},{"issue":"5","key":"10.6061\/clinics\/2018\/e523_bib5","first-page":"443","article-title":"Morquio\u2019s syndrome","volume":"8","author":"Sataloff","year":"1987","journal-title":"Am J Otol"},{"key":"10.6061\/clinics\/2018\/e523_bib6","series-title":"Otolaryngology Head & Neck Surgery","author":"Cummings","year":"1998"},{"key":"10.6061\/clinics\/2018\/e523_bib7","series-title":"The metabolic basis of in herited disease","first-page":"751","article-title":"The mucopolysaccharide storage diseases","author":"Mckusick","year":"1983"},{"key":"10.6061\/clinics\/2018\/e523_bib8","series-title":"The metabolic and molecularbasis of Inherited disease","first-page":"2465","article-title":"The mucopolysaccharidosis","author":"Neufeld","year":"1989"},{"issue":"1","key":"10.6061\/clinics\/2018\/e523_bib9","doi-asserted-by":"crossref","first-page":"30","DOI":"10.1016\/S0194-5998(98)70371-7","article-title":"Otologic and laryngologic manifestations of mucopolysaccharidoses after bone marrow transplantation","volume":"118","author":"Papsin","year":"1998","journal-title":"Otolaryngol Head Neck Surg"},{"issue":"9","key":"10.6061\/clinics\/2018\/e523_bib10","doi-asserted-by":"crossref","first-page":"518","DOI":"10.1001\/archotol.1977.00780260048003","article-title":"Hearing patterns in Morquio\u2019s syndrome (mucopolysaccharidosis IV)","volume":"103","author":"Riedner","year":"1977","journal-title":"Arch Otolaryngol"},{"key":"10.6061\/clinics\/2018\/e523_bib11","series-title":"Impacto flaronidase on the evolution of upper airway manifestations and hearing in patients with mucopolysaccharidosis I","author":"Dualibi","year":"2007"},{"issue":"2","key":"10.6061\/clinics\/2018\/e523_bib12","doi-asserted-by":"crossref","first-page":"192","DOI":"10.1001\/archotol.1961.00740030197013","article-title":"Conditioned orientation reflex audiometry","volume":"74","author":"Suzuki","year":"1961","journal-title":"Arch Otolaryngol"},{"issue":"2","key":"10.6061\/clinics\/2018\/e523_bib13","doi-asserted-by":"crossref","first-page":"281","DOI":"10.3109\/00016486909125453","article-title":"Visual reinforcement audiometry","volume":"67","author":"Lid\u00e9n","year":"1969","journal-title":"Acta Otolaryngol"},{"key":"10.6061\/clinics\/2018\/e523_bib14","series-title":"New treatiseon Speech Therapy","first-page":"149","article-title":"Audiological evaluation in the firsty ear of life","author":"Azevedo","year":"2013"},{"key":"10.6061\/clinics\/2018\/e523_bib15","series-title":"Auditory Diagnosis","author":"Silman","year":"1991"},{"key":"10.6061\/clinics\/2018\/e523_bib16","series-title":"Hearing in children","first-page":"89","author":"Northern","year":"1984"},{"issue":"4","key":"10.6061\/clinics\/2018\/e523_bib17","doi-asserted-by":"crossref","first-page":"311","DOI":"10.1001\/archotol.1970.04310040005002","article-title":"Clinical experience with impedance audiometry","volume":"92","author":"Jerger","year":"1970","journal-title":"Arch Otolaryngol"},{"issue":"5","key":"10.6061\/clinics\/2018\/e523_bib18","doi-asserted-by":"crossref","first-page":"536","DOI":"10.1001\/archotol.1952.00710010550003","article-title":"Threshold of reflex contractions of muscles of middle ear and recruitment of loudness","volume":"55","author":"Metz","year":"1952","journal-title":"AMA Arch Otolaryng"},{"key":"10.6061\/clinics\/2018\/e523_bib19","series-title":"Auditory Processing","first-page":"57","article-title":"The effect of the stapedian reflex on the control of the passage of sound information","author":"Carvallo","year":"1996"},{"key":"10.6061\/clinics\/2018\/e523_bib20","series-title":"Auditory Processing: Evaluation manual","first-page":"27","article-title":"Auditory Processing: Basic audiological evaluation","author":"Carvallo","year":"1997"},{"issue":"3","key":"10.6061\/clinics\/2018\/e523_bib21","doi-asserted-by":"crossref","first-page":"281","DOI":"10.1016\/j.bjorl.2015.05.007","article-title":"Audiologic evaluations of children with mucopolysaccharidosis","volume":"82","author":"G\u00f6kdogan","year":"2016","journal-title":"Braz J Otorhinolaryngol"},{"issue":"3","key":"10.6061\/clinics\/2018\/e523_bib22","first-page":"290","article-title":"The importance of the otorhinolaryngologic evaluation in mucopolysaccharidosis patients","volume":"15","author":"Bicalho","year":"2011","journal-title":"Intl Arch Otorhinolaryngol"},{"issue":"4","key":"10.6061\/clinics\/2018\/e523_bib23","doi-asserted-by":"crossref","first-page":"533","DOI":"10.1016\/j.ymgme.2014.02.003","article-title":"Assessment of hearing loss by pure-tone audiometry in patients with mucopolysaccharidoses","volume":"111","author":"Lin","year":"2014","journal-title":"Mol Genet Metab"},{"issue":"6","key":"10.6061\/clinics\/2018\/e523_bib24","doi-asserted-by":"crossref","first-page":"472","DOI":"10.1177\/000348949210100605","article-title":"Otolaryngologic manifestations of the mucopolysaccharidoses","volume":"101","author":"Bredenkamp","year":"1992","journal-title":"Ann Otol Rhinol Laryngol"},{"issue":"3","key":"10.6061\/clinics\/2018\/e523_bib25","first-page":"177","article-title":"The management of otolaryngological problems in the mucopolysaccharidoses: a retrospective review","volume":"20","author":"Ruckenstein","year":"1991","journal-title":"J Otolaryngol"},{"issue":"9","key":"10.6061\/clinics\/2018\/e523_bib26","doi-asserted-by":"crossref","first-page":"518","DOI":"10.1001\/archotol.1977.00780260048003","article-title":"Hearing Patterns in Morquio\u2019s Syndrome (Mucopolysaccharidosis IV)","volume":"103","author":"Riedner","year":"1977","journal-title":"Arch Otolaryngol"},{"issue":"2","key":"10.6061\/clinics\/2018\/e523_bib27","doi-asserted-by":"crossref","first-page":"343","DOI":"10.1007\/s10545-011-9378-5","article-title":"Hearing loss in patients with mucopolysaccharidosis II: data from HOS - the Hunter Outcome Survey","volume":"35","author":"Keilmann","year":"2012","journal-title":"J Inherit Metab Dis"},{"issue":"2","key":"10.6061\/clinics\/2018\/e523_bib28","doi-asserted-by":"crossref","first-page":"203","DOI":"10.1590\/S1809-48722011000200013","article-title":"Audiologic Evaluation in Patients with Mucopolysaccharidosis in a Pediatric Hospital","volume":"15","author":"Gomes","year":"2011","journal-title":"Arq Int Otorrinolaringol"},{"issue":"4","key":"10.6061\/clinics\/2018\/e523_bib29","doi-asserted-by":"crossref","first-page":"243","DOI":"10.1097\/00003446-198407000-00009","article-title":"Hearing loss in Hunter\u2019s syndrome-mucopolysacciraridosis II","volume":"5","author":"Peck","year":"1984","journal-title":"Ear Hear"},{"issue":"11","key":"10.6061\/clinics\/2018\/e523_bib30","doi-asserted-by":"crossref","first-page":"1071","DOI":"10.1001\/jamaoto.2013.597","article-title":"Improvements in sensorineural hearing loss after cord blood transplant in patients with mucopolysaccharidosis","volume":"138","author":"Da Costa","year":"2012","journal-title":"Arch Otolaryngol Head Neck Surg"},{"key":"10.6061\/clinics\/2018\/e523_bib31","first-page":"S14","article-title":"Hearing loss in mucopolysaccharidosis and its impact on quality of life; A review of the literature","volume":"117","author":"Soni-Jaiswala","year":"2016","journal-title":"Molecular Genetics and Metabolism"}],"container-title":["Clinics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1807593222006044?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S1807593222006044?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2025,10,29]],"date-time":"2025-10-29T06:54:43Z","timestamp":1761720883000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S1807593222006044"},"secondary":[{"URL":"http:\/\/www.scielo.br\/scielo.php?script=sci_arttext&pid=S1807-59322018000100297&lng=en&nrm=iso&tlng=en","label":"SCIELO"},{"URL":"https:\/\/www.clinicsjournal.com\/article\/audiometric-evaluation-in-individuals-with-mucopolysaccharidosis\/","label":"CLINICS"}]},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018]]},"references-count":31,"alternative-id":["S1807593222006044"],"URL":"https:\/\/doi.org\/10.6061\/clinics\/2018\/e523","relation":{},"ISSN":["1807-5932"],"issn-type":[{"value":"1807-5932","type":"print"}],"subject":[],"published":{"date-parts":[[2018]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"Audiometric evaluation in individuals with mucopolysaccharidosis","name":"articletitle","label":"Article Title"},{"value":"Clinics","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.6061\/clinics\/2018\/e523","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2018 CLINICS. Published by Elsevier Spain","name":"copyright","label":"Copyright"}],"article-number":"e523"}}