{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,26]],"date-time":"2026-09-26T15:09:39Z","timestamp":1790435379737,"version":"4.1.0"},"reference-count":11,"publisher":"Springer Science and Business Media LLC","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2024,5,7]]},"DOI":"10.7759\/cureus.59821","type":"journal-article","created":{"date-parts":[[2024,5,7]],"date-time":"2024-05-07T16:57:07Z","timestamp":1715101027000},"source":"Crossref","is-referenced-by-count":1,"title":["Anti-CASPR2 Antibody-Associated Syndrome Presenting With Episodic Ataxia"],"prefix":"10.7759","author":[{"given":"Sofia","family":"Lopes","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Leonor","family":"Francisco","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stefanie","family":"Moreira","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sara","family":"Varanda","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jos\u00e9 Manuel","family":"Ara\u00fajo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","reference":[{"key":"ref1","doi-asserted-by":"publisher","DOI":"10.1523\/JNEUROSCI.3398-08.2008","article-title":"Multiple molecular interactions determine the clustering of Caspr2 and Kv1 channels in myelinated axons","volume":"28","author":"Horresh I","year":"2008","unstructured":"Horresh I, Poliak S, Grant S, Bredt D, Rasband MN, Peles E. Multiple molecular interactions determine the clustering of Caspr2 and Kv1 channels in myelinated axons. J Neurosci. 2008, 28:14213-22. 10.1523\/JNEUROSCI.3398-08.2008","journal-title":"J Neurosci"},{"key":"ref2","doi-asserted-by":"publisher","DOI":"10.1007\/s00415-014-7408-6","article-title":"Outcome of limbic encephalitis with VGKC-complex antibodies: relation to antigenic specificity","volume":"261","author":"Malter MP","year":"2014","unstructured":"Malter MP, Frisch C, Schoene-Bake JC, et al.. Outcome of limbic encephalitis with VGKC-complex antibodies: relation to antigenic specificity. J Neurol. 2014, 261:1695-705. 10.1007\/s00415-014-7408-6","journal-title":"J Neurol"},{"key":"ref3","doi-asserted-by":"publisher","DOI":"10.1007\/s00415-019-09686-2","article-title":"Systematic review of the clinical spectrum of CASPR2 antibody syndrome","volume":"267","author":"Boyko M","year":"2020","unstructured":"Boyko M, Au KL, Casault C, de Robles P, Pfeffer G. Systematic review of the clinical spectrum of CASPR2 antibody syndrome. J Neurol. 2020, 267:1137-46. 10.1007\/s00415-019-09686-2","journal-title":"J Neurol"},{"key":"ref4","doi-asserted-by":"publisher","DOI":"10.1212\/NXI.0000000000000371","article-title":"Autoimmune episodic ataxia in patients with anti-CASPR2 antibody-associated encephalitis","volume":"4","author":"Joubert B","year":"2017","unstructured":"Joubert B, Gobert F, Thomas L, et al.. Autoimmune episodic ataxia in patients with anti-CASPR2 antibody-associated encephalitis. Neurol Neuroimmunol Neuroinflamm. 2017, 4:e371. 10.1212\/NXI.0000000000000371","journal-title":"Neurol Neuroimmunol Neuroinflamm"},{"key":"ref5","doi-asserted-by":"publisher","DOI":"10.1038\/nrneurol.2017.43","article-title":"The value of LGI1, Caspr2 and voltage-gated potassium channel antibodies in encephalitis","volume":"13","author":"van Sonderen A","year":"2017","unstructured":"van Sonderen A, Petit-Pedrol M, Dalmau J, Titulaer MJ. The value of LGI1, Caspr2 and voltage-gated potassium channel antibodies in encephalitis. Nat Rev Neurol. 2017, 13:290-301. 10.1038\/nrneurol.2017.43","journal-title":"Nat Rev Neurol"},{"key":"ref6","doi-asserted-by":"publisher","DOI":"10.1002\/ana.24979","article-title":"Expanded phenotypes and outcomes among 256 LGI1\/CASPR2-IgG-positive patients","volume":"82","author":"Gadoth A","year":"2017","unstructured":"Gadoth A, Pittock SJ, Dubey D, et al.. Expanded phenotypes and outcomes among 256 LGI1\/CASPR2-IgG-positive patients. Ann Neurol. 2017, 82:79-92. 10.1002\/ana.24979","journal-title":"Ann Neurol"},{"key":"ref7","doi-asserted-by":"publisher","DOI":"10.1038\/ng1094-136","article-title":"Episodic ataxia\/myokymia syndrome is associated with point mutations in the human potassium channel gene, KCNA1","volume":"8","author":"Browne DL","year":"1994","unstructured":"Browne DL, Gancher ST, Nutt JG, Brunt ER, Smith EA, Kramer P, Litt M. Episodic ataxia\/myokymia syndrome is associated with point mutations in the human potassium channel gene, KCNA1. Nat Genet. 1994, 8:136-40. 10.1038\/ng1094-136","journal-title":"Nat Genet"},{"key":"ref8","doi-asserted-by":"publisher","DOI":"10.1002\/ana.22297","article-title":"Investigations of caspr2, an autoantigen of encephalitis and neuromyotonia","volume":"69","author":"Lancaster E","year":"2011","unstructured":"Lancaster E, Huijbers MG, Bar V, et al.. Investigations of caspr2, an autoantigen of encephalitis and neuromyotonia. Ann Neurol. 2011, 69:303-11. 10.1002\/ana.22297","journal-title":"Ann Neurol"},{"key":"ref9","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/awac276","article-title":"Distinct movement disorders in contactin-associated-protein-like-2 antibody-associated autoimmune encephalitis","volume":"146","author":"G\u00f6vert F","year":"2023","unstructured":"G\u00f6vert F, Abrante L, Becktepe J, et al.. Distinct movement disorders in contactin-associated-protein-like-2 antibody-associated autoimmune encephalitis. Brain. 2023, 146:657-67. 10.1093\/brain\/awac276","journal-title":"Brain"},{"key":"ref10","doi-asserted-by":"publisher","DOI":"10.1212\/NXI.0000000000000536","article-title":"Episodic ataxia in CASPR2 autoimmunity","volume":"6","author":"L\u00f3pez Chiriboga AS","year":"2019","unstructured":"L\u00f3pez Chiriboga AS, Pittock S. Episodic ataxia in CASPR2 autoimmunity. Neurol Neuroimmunol Neuroinflamm. 2019, 6:e536. 10.1212\/NXI.0000000000000536","journal-title":"Neurol Neuroimmunol Neuroinflamm"},{"key":"ref11","doi-asserted-by":"publisher","DOI":"10.1212\/NXI.0000000000001088","article-title":"Rituximab treatment and long-term outcome of patients with autoimmune encephalitis: real-world evidence from the GENERATE registry","volume":"8","author":"Thaler FS","year":"2021","unstructured":"Thaler FS, Zimmermann L, Kammermeier S, et al.. Rituximab treatment and long-term outcome of patients with autoimmune encephalitis: real-world evidence from the GENERATE registry. Neurol Neuroimmunol Neuroinflamm. 2021, 8:1-17. 10.1212\/NXI.0000000000001088","journal-title":"Neurol Neuroimmunol Neuroinflamm"}],"container-title":["Cureus"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.cureus.com\/articles\/251810-anti-caspr2-antibody-associated-syndrome-presenting-with-episodic-ataxia","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,5,7]],"date-time":"2024-05-07T16:57:11Z","timestamp":1715101031000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.cureus.com\/articles\/251810-anti-caspr2-antibody-associated-syndrome-presenting-with-episodic-ataxia"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,5,7]]},"references-count":11,"URL":"https:\/\/doi.org\/10.7759\/cureus.59821","relation":{},"ISSN":["2168-8184"],"issn-type":[{"value":"2168-8184","type":"print"}],"subject":[],"published":{"date-parts":[[2024,5,7]]}}}