{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,7]],"date-time":"2026-02-07T09:04:04Z","timestamp":1770455044861,"version":"3.49.0"},"reference-count":16,"publisher":"Springer Science and Business Media LLC","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2025,8,14]]},"DOI":"10.7759\/cureus.90088","type":"journal-article","created":{"date-parts":[[2025,8,14]],"date-time":"2025-08-14T17:07:30Z","timestamp":1755191250000},"source":"Crossref","is-referenced-by-count":0,"title":["Incomplete Susac Syndrome With Recurrent Retinal Occlusions and Vertigo: A Case of Early Immunosuppressive Success"],"prefix":"10.7759","author":[{"given":"Arathi","family":"Kulkarni","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Amara","family":"Miller","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Chandana","family":"Keshavamurthy","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tamim","family":"Sultani","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ramin","family":"Schadlu","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Trent","family":"Smith","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","reference":[{"key":"ref1","doi-asserted-by":"publisher","DOI":"10.1016\/j.autrev.2022.103097","article-title":"Susac syndrome: a scoping review","volume":"21","author":"David C","year":"2022","unstructured":"David C, Sacr\u00e9 K, Henri-Feugeas MC, et al.. Susac syndrome: a scoping review. Autoimmun Rev. 2022, 21:103097. 10.1016\/j.autrev.2022.103097","journal-title":"Autoimmun Rev"},{"key":"ref2","doi-asserted-by":"publisher","DOI":"10.1080\/01658107.2020.1748062","article-title":"Susac's syndrome: an updated review","volume":"44","author":"Pereira S","year":"2020","unstructured":"Pereira S, Vieira B, Maio T, Moreira J, Sampaio F. Susac's syndrome: an updated review. Neuroophthalmology. 2020, 44:355-60. 10.1080\/01658107.2020.1748062","journal-title":"Neuroophthalmology"},{"key":"ref3","doi-asserted-by":"publisher","DOI":"10.1038\/s41467-019-13593-5","article-title":"CD8(+) T cell-mediated endotheliopathy is a targetable mechanism of neuro-inflammation in Susac syndrome","volume":"10","author":"Gross CC","year":"2019","unstructured":"Gross CC, Meyer C, Bhatia U, et al.. CD8(+) T cell-mediated endotheliopathy is a targetable mechanism of neuro-inflammation in Susac syndrome. Nat Commun. 2019, 10:5779. 10.1038\/s41467-019-13593-5","journal-title":"Nat Commun"},{"key":"ref4","doi-asserted-by":"publisher","DOI":"10.1016\/j.jns.2007.01.036","article-title":"Susac's syndrome: 1975-2005 microangiopathy\/autoimmune endotheliopathy","volume":"257","author":"Susac JO","year":"2007","unstructured":"Susac JO, Egan RA, Rennebohm RM, Lubow M. Susac's syndrome: 1975-2005 microangiopathy\/autoimmune endotheliopathy. J Neurol Sci. 2007, 257:270-2. 10.1016\/j.jns.2007.01.036","journal-title":"J Neurol Sci"},{"key":"ref5","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp-2016-314295","article-title":"Diagnostic criteria for Susac syndrome","volume":"87","author":"Kleffner I","year":"2016","unstructured":"Kleffner I, D\u00f6rr J, Ringelstein M, et al.. Diagnostic criteria for Susac syndrome. J Neurol Neurosurg Psychiatry. 2016, 87:1287-95. 10.1136\/jnnp-2016-314295","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"ref6","doi-asserted-by":"publisher","DOI":"10.1111\/ene.15317","article-title":"Diagnosis, differential diagnosis and misdiagnosis of Susac syndrome","volume":"29","author":"Triplett JD","year":"2022","unstructured":"Triplett JD, Qiu J, O'Brien B, et al.. Diagnosis, differential diagnosis and misdiagnosis of Susac syndrome. Eur J Neurol. 2022, 29:1771-81. 10.1111\/ene.15317","journal-title":"Eur J Neurol"},{"key":"ref7","doi-asserted-by":"publisher","DOI":"10.7759\/cureus.27903","article-title":"Incomplete Susac's syndrome: a case report and literature review","volume":"14","author":"Ahmad A","year":"2022","unstructured":"Ahmad A, Tariq F, Zaheer M. Incomplete Susac's syndrome: a case report and literature review. Cureus. 2022, 14:e27903. 10.7759\/cureus.27903","journal-title":"Cureus"},{"key":"ref8","doi-asserted-by":"publisher","DOI":"10.1097\/MAO.0b013e31822e9665","article-title":"Temporal bone findings in a case of Susac's syndrome","volume":"32","author":"Francis HW","year":"2011","unstructured":"Francis HW, Makary C, Halpin C, Crane BT, Merchant SN. Temporal bone findings in a case of Susac's syndrome. Otol Neurotol. 2011, 32:1198-204. 10.1097\/MAO.0b013e31822e9665","journal-title":"Otol Neurotol"},{"key":"ref9","doi-asserted-by":"publisher","DOI":"10.1097\/WNO.0000000000000677","article-title":"Diagnostic criteria and treatment algorithm for Susac syndrome","volume":"39","author":"Egan RA","year":"2019","unstructured":"Egan RA. Diagnostic criteria and treatment algorithm for Susac syndrome. J Neuroophthalmol. 2019, 39:60-7. 10.1097\/WNO.0000000000000677","journal-title":"J Neuroophthalmol"},{"key":"ref10","doi-asserted-by":"publisher","DOI":"10.1212\/NXI.0000000000200209","article-title":"Clinical characterization and ancillary tests in Susac syndrome: a systematic review","volume":"11","author":"Wilf-Yarkoni A","year":"2024","unstructured":"Wilf-Yarkoni A, Zmira O, Tolkovsky A, et al.. Clinical characterization and ancillary tests in Susac syndrome: a systematic review. Neurol Neuroimmunol Neuroinflamm. 2024, 11:e200209. 10.1212\/NXI.0000000000200209","journal-title":"Neurol Neuroimmunol Neuroinflamm"},{"key":"ref11","doi-asserted-by":"publisher","DOI":"10.1007\/s00415-020-10086-0","article-title":"The neuro-otology of Susac syndrome","volume":"267","author":"Hardy TA","year":"2020","unstructured":"Hardy TA, Taylor RL, Qiu J, et al.. The neuro-otology of Susac syndrome. J Neurol. 2020, 267:3711-22. 10.1007\/s00415-020-10086-0","journal-title":"J Neurol"},{"key":"ref12","doi-asserted-by":"publisher","DOI":"10.1007\/s00415-023-11891-z","article-title":"Susac syndrome: neurological update (clinical features, long-term observational follow-up and management of sixteen patients)","volume":"270","author":"Bose S","year":"2023","unstructured":"Bose S, Papathanasiou A, Karkhanis S, et al.. Susac syndrome: neurological update (clinical features, long-term observational follow-up and management of sixteen patients). J Neurol. 2023, 270:6193-206. 10.1007\/s00415-023-11891-z","journal-title":"J Neurol"},{"key":"ref13","doi-asserted-by":"publisher","DOI":"10.4103\/ijo.IJO_1705_22","article-title":"Posterior segment involvement in systemic lupus erythematosus - a series from South India","volume":"71","author":"Babu K","year":"2023","unstructured":"Babu K, Nanda S, Hegde P, Rao AP, Jois R. Posterior segment involvement in systemic lupus erythematosus - a series from South India. Indian J Ophthalmol. 2023, 71:1986-93. 10.4103\/ijo.IJO_1705_22","journal-title":"Indian J Ophthalmol"},{"key":"ref14","doi-asserted-by":"publisher","DOI":"10.1016\/j.ophtha.2019.09.028","article-title":"Retinal and ophthalmic artery occlusions preferred practice pattern","volume":"127","author":"Flaxel CJ","year":"2020","unstructured":"Flaxel CJ, Adelman RA, Bailey ST, Fawzi A, Lim JI, Vemulakonda GA, Ying GS. Retinal and ophthalmic artery occlusions preferred practice pattern. Ophthalmology. 2020, 127:P259-87. 10.1016\/j.ophtha.2019.09.028","journal-title":"Ophthalmology"},{"key":"ref15","doi-asserted-by":"publisher","DOI":"10.1177\/1120672120924545","article-title":"Rituximab in the treatment of Susac's syndrome: report of a case","volume":"31","author":"Monferrer-Adsuara C","year":"2021","unstructured":"Monferrer-Adsuara C, Remol\u00ed-Sargues L, Hern\u00e1ndez-Bel L, Gracia-Garc\u00eda A, Hern\u00e1ndez-Garfella ML, Cervera-Taulet E. Rituximab in the treatment of Susac's syndrome: report of a case. Eur J Ophthalmol. 2021, 31:NP48-52. 10.1177\/1120672120924545","journal-title":"Eur J Ophthalmol"},{"key":"ref16","doi-asserted-by":"publisher","DOI":"10.1111\/j.1468-1331.2011.03627.x","article-title":"Susac syndrome: clinical characteristics and treatment in 29 new cases","volume":"19","author":"Mateen FJ","year":"2012","unstructured":"Mateen FJ, Zubkov AY, Muralidharan R, Fugate JE, Rodriguez FJ, Winters JL, Petty GW. Susac syndrome: clinical characteristics and treatment in 29 new cases. Eur J Neurol. 2012, 19:800-11. 10.1111\/j.1468-1331.2011.03627.x","journal-title":"Eur J Neurol"}],"container-title":["Cureus"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.cureus.com\/articles\/379540-incomplete-susac-syndrome-with-recurrent-retinal-occlusions-and-vertigo-a-case-of-early-immunosuppressive-success","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,14]],"date-time":"2025-08-14T17:07:31Z","timestamp":1755191251000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.cureus.com\/articles\/379540-incomplete-susac-syndrome-with-recurrent-retinal-occlusions-and-vertigo-a-case-of-early-immunosuppressive-success"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,8,14]]},"references-count":16,"URL":"https:\/\/doi.org\/10.7759\/cureus.90088","relation":{},"ISSN":["2168-8184"],"issn-type":[{"value":"2168-8184","type":"print"}],"subject":[],"published":{"date-parts":[[2025,8,14]]}}}